Pathways Knowlegdes

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Pathway DOIs Note
Amino acid and derivative metabolism

Accession ID: Reactome:R-DME-71291
  • 10.1007/978-1-4757-0734-2_8
  • 10.1146/annurev.bi.44.070175.004441
  • 10.1177/014860719001400405
Häussinger D. Liver glutamine metabolism. JPEN J Parenter Enteral Nutr. 1990 Jul;14(4 Suppl):56S–62S. doi: 10.1177/014860719001400405. PMID: 2205732.; Owen OE, Reichard GA, Patel MS, Boden G. Energy metabolism in feasting and fasting. Adv Exp Med Biol. 1979;111():169–88. doi: 10.1007/978-1-4757-0734-2_8. PMID: 371355.; Felig P. Amino acid metabolism in man. Annu Rev Biochem. 1975;44():933–55. doi: 10.1146/annurev.bi.44.070175.004441. PMID: 1094924.
Carnitine synthesis

Accession ID: Reactome:R-DME-71262
  • 10.1016/0304-4165(80)90133-6
  • 10.1042/0264-6021:3610417
  • 10.1146/annurev.nutr.18.1.179
  • 10.1152/physrev.1983.63.4.1420
Vaz FM, Wanders RJ. Carnitine biosynthesis in mammals. Biochem J. 2002 Feb 01;361(Pt 3):417–29. PMID: 11802770; PMCID: PMC1222323.; Kerner J, Hoppel C. Genetic disorders of carnitine metabolism and their nutritional management. Annu Rev Nutr. 1998;18():179–206. doi: 10.1146/annurev.nutr.18.1.179. PMID: 9706223.; Bremer J. Carnitine--metabolism and functions. Physiol Rev. 1983 Oct;63(4):1420–80. doi: 10.1152/physrev.1983.63.4.1420. PMID: 6361812.; Rebouche CJ, Engel AG. Tissue distribution of carnitine biosynthetic enzymes in man. Biochimica et Biophysica Acta (BBA) - General Subjects. 1980 Jun;630(1):22–9. doi: 10.1016/0304-4165(80)90133-6.
Amino acid and derivative metabolism

Accession ID: Reactome:R-GGA-71291
  • 10.1007/978-1-4757-0734-2_8
  • 10.1146/annurev.bi.44.070175.004441
  • 10.1177/014860719001400405
Häussinger D. Liver glutamine metabolism. JPEN J Parenter Enteral Nutr. 1990 Jul;14(4 Suppl):56S–62S. doi: 10.1177/014860719001400405. PMID: 2205732.; Owen OE, Reichard GA, Patel MS, Boden G. Energy metabolism in feasting and fasting. Adv Exp Med Biol. 1979;111():169–88. doi: 10.1007/978-1-4757-0734-2_8. PMID: 371355.; Felig P. Amino acid metabolism in man. Annu Rev Biochem. 1975;44():933–55. doi: 10.1146/annurev.bi.44.070175.004441. PMID: 1094924.
Carnitine synthesis

Accession ID: Reactome:R-GGA-71262
  • 10.1016/0304-4165(80)90133-6
  • 10.1042/0264-6021:3610417
  • 10.1146/annurev.nutr.18.1.179
  • 10.1152/physrev.1983.63.4.1420
Vaz FM, Wanders RJ. Carnitine biosynthesis in mammals. Biochem J. 2002 Feb 01;361(Pt 3):417–29. PMID: 11802770; PMCID: PMC1222323.; Kerner J, Hoppel C. Genetic disorders of carnitine metabolism and their nutritional management. Annu Rev Nutr. 1998;18():179–206. doi: 10.1146/annurev.nutr.18.1.179. PMID: 9706223.; Bremer J. Carnitine--metabolism and functions. Physiol Rev. 1983 Oct;63(4):1420–80. doi: 10.1152/physrev.1983.63.4.1420. PMID: 6361812.; Rebouche CJ, Engel AG. Tissue distribution of carnitine biosynthetic enzymes in man. Biochimica et Biophysica Acta (BBA) - General Subjects. 1980 Jun;630(1):22–9. doi: 10.1016/0304-4165(80)90133-6.
Metabolism

Accession ID: Reactome:R-SCE-1430728
-
Amino acid and derivative metabolism

Accession ID: Reactome:R-SPO-71291
  • 10.1007/978-1-4757-0734-2_8
  • 10.1146/annurev.bi.44.070175.004441
  • 10.1177/014860719001400405
Häussinger D. Liver glutamine metabolism. JPEN J Parenter Enteral Nutr. 1990 Jul;14(4 Suppl):56S–62S. doi: 10.1177/014860719001400405. PMID: 2205732.; Owen OE, Reichard GA, Patel MS, Boden G. Energy metabolism in feasting and fasting. Adv Exp Med Biol. 1979;111():169–88. doi: 10.1007/978-1-4757-0734-2_8. PMID: 371355.; Felig P. Amino acid metabolism in man. Annu Rev Biochem. 1975;44():933–55. doi: 10.1146/annurev.bi.44.070175.004441. PMID: 1094924.
Carnitine synthesis

Accession ID: Reactome:R-SPO-71262
  • 10.1016/0304-4165(80)90133-6
  • 10.1042/0264-6021:3610417
  • 10.1146/annurev.nutr.18.1.179
  • 10.1152/physrev.1983.63.4.1420
Vaz FM, Wanders RJ. Carnitine biosynthesis in mammals. Biochem J. 2002 Feb 01;361(Pt 3):417–29. PMID: 11802770; PMCID: PMC1222323.; Kerner J, Hoppel C. Genetic disorders of carnitine metabolism and their nutritional management. Annu Rev Nutr. 1998;18():179–206. doi: 10.1146/annurev.nutr.18.1.179. PMID: 9706223.; Bremer J. Carnitine--metabolism and functions. Physiol Rev. 1983 Oct;63(4):1420–80. doi: 10.1152/physrev.1983.63.4.1420. PMID: 6361812.; Rebouche CJ, Engel AG. Tissue distribution of carnitine biosynthetic enzymes in man. Biochimica et Biophysica Acta (BBA) - General Subjects. 1980 Jun;630(1):22–9. doi: 10.1016/0304-4165(80)90133-6.
Metabolism

Accession ID: Reactome:R-SSC-1430728
-
Amino acid and derivative metabolism

Accession ID: Reactome:R-XTR-71291
  • 10.1007/978-1-4757-0734-2_8
  • 10.1146/annurev.bi.44.070175.004441
  • 10.1177/014860719001400405
Häussinger D. Liver glutamine metabolism. JPEN J Parenter Enteral Nutr. 1990 Jul;14(4 Suppl):56S–62S. doi: 10.1177/014860719001400405. PMID: 2205732.; Owen OE, Reichard GA, Patel MS, Boden G. Energy metabolism in feasting and fasting. Adv Exp Med Biol. 1979;111():169–88. doi: 10.1007/978-1-4757-0734-2_8. PMID: 371355.; Felig P. Amino acid metabolism in man. Annu Rev Biochem. 1975;44():933–55. doi: 10.1146/annurev.bi.44.070175.004441. PMID: 1094924.
Carnitine synthesis

Accession ID: Reactome:R-XTR-71262
  • 10.1016/0304-4165(80)90133-6
  • 10.1042/0264-6021:3610417
  • 10.1146/annurev.nutr.18.1.179
  • 10.1152/physrev.1983.63.4.1420
Vaz FM, Wanders RJ. Carnitine biosynthesis in mammals. Biochem J. 2002 Feb 01;361(Pt 3):417–29. PMID: 11802770; PMCID: PMC1222323.; Kerner J, Hoppel C. Genetic disorders of carnitine metabolism and their nutritional management. Annu Rev Nutr. 1998;18():179–206. doi: 10.1146/annurev.nutr.18.1.179. PMID: 9706223.; Bremer J. Carnitine--metabolism and functions. Physiol Rev. 1983 Oct;63(4):1420–80. doi: 10.1152/physrev.1983.63.4.1420. PMID: 6361812.; Rebouche CJ, Engel AG. Tissue distribution of carnitine biosynthetic enzymes in man. Biochimica et Biophysica Acta (BBA) - General Subjects. 1980 Jun;630(1):22–9. doi: 10.1016/0304-4165(80)90133-6.
Amino acid and derivative metabolism

Accession ID: Reactome:R-CEL-71291
  • 10.1007/978-1-4757-0734-2_8
  • 10.1146/annurev.bi.44.070175.004441
  • 10.1177/014860719001400405
Häussinger D. Liver glutamine metabolism. JPEN J Parenter Enteral Nutr. 1990 Jul;14(4 Suppl):56S–62S. doi: 10.1177/014860719001400405. PMID: 2205732.; Owen OE, Reichard GA, Patel MS, Boden G. Energy metabolism in feasting and fasting. Adv Exp Med Biol. 1979;111():169–88. doi: 10.1007/978-1-4757-0734-2_8. PMID: 371355.; Felig P. Amino acid metabolism in man. Annu Rev Biochem. 1975;44():933–55. doi: 10.1146/annurev.bi.44.070175.004441. PMID: 1094924.
Carnitine synthesis

Accession ID: Reactome:R-CEL-71262
  • 10.1016/0304-4165(80)90133-6
  • 10.1042/0264-6021:3610417
  • 10.1146/annurev.nutr.18.1.179
  • 10.1152/physrev.1983.63.4.1420
Vaz FM, Wanders RJ. Carnitine biosynthesis in mammals. Biochem J. 2002 Feb 01;361(Pt 3):417–29. PMID: 11802770; PMCID: PMC1222323.; Kerner J, Hoppel C. Genetic disorders of carnitine metabolism and their nutritional management. Annu Rev Nutr. 1998;18():179–206. doi: 10.1146/annurev.nutr.18.1.179. PMID: 9706223.; Bremer J. Carnitine--metabolism and functions. Physiol Rev. 1983 Oct;63(4):1420–80. doi: 10.1152/physrev.1983.63.4.1420. PMID: 6361812.; Rebouche CJ, Engel AG. Tissue distribution of carnitine biosynthetic enzymes in man. Biochimica et Biophysica Acta (BBA) - General Subjects. 1980 Jun;630(1):22–9. doi: 10.1016/0304-4165(80)90133-6.
Metabolism

Accession ID: Reactome:R-DRE-1430728
-
Metabolism

Accession ID: Reactome:R-GGA-1430728
-
Amino acid and derivative metabolism

Accession ID: Reactome:R-HSA-71291
  • 10.1007/978-1-4757-0734-2_8
  • 10.1146/annurev.bi.44.070175.004441
  • 10.1177/014860719001400405
Häussinger D. Liver glutamine metabolism. JPEN J Parenter Enteral Nutr. 1990 Jul;14(4 Suppl):56S–62S. doi: 10.1177/014860719001400405. PMID: 2205732.; Owen OE, Reichard GA, Patel MS, Boden G. Energy metabolism in feasting and fasting. Adv Exp Med Biol. 1979;111():169–88. doi: 10.1007/978-1-4757-0734-2_8. PMID: 371355.; Felig P. Amino acid metabolism in man. Annu Rev Biochem. 1975;44():933–55. doi: 10.1146/annurev.bi.44.070175.004441. PMID: 1094924.
Carnitine synthesis

Accession ID: Reactome:R-HSA-71262
  • 10.1016/0304-4165(80)90133-6
  • 10.1042/0264-6021:3610417
  • 10.1146/annurev.nutr.18.1.179
  • 10.1152/physrev.1983.63.4.1420
Vaz FM, Wanders RJ. Carnitine biosynthesis in mammals. Biochem J. 2002 Feb 01;361(Pt 3):417–29. PMID: 11802770; PMCID: PMC1222323.; Kerner J, Hoppel C. Genetic disorders of carnitine metabolism and their nutritional management. Annu Rev Nutr. 1998;18():179–206. doi: 10.1146/annurev.nutr.18.1.179. PMID: 9706223.; Bremer J. Carnitine--metabolism and functions. Physiol Rev. 1983 Oct;63(4):1420–80. doi: 10.1152/physrev.1983.63.4.1420. PMID: 6361812.; Rebouche CJ, Engel AG. Tissue distribution of carnitine biosynthetic enzymes in man. Biochimica et Biophysica Acta (BBA) - General Subjects. 1980 Jun;630(1):22–9. doi: 10.1016/0304-4165(80)90133-6.
Amino acid and derivative metabolism

Accession ID: Reactome:R-MMU-71291
  • 10.1007/978-1-4757-0734-2_8
  • 10.1146/annurev.bi.44.070175.004441
  • 10.1177/014860719001400405
Häussinger D. Liver glutamine metabolism. JPEN J Parenter Enteral Nutr. 1990 Jul;14(4 Suppl):56S–62S. doi: 10.1177/014860719001400405. PMID: 2205732.; Owen OE, Reichard GA, Patel MS, Boden G. Energy metabolism in feasting and fasting. Adv Exp Med Biol. 1979;111():169–88. doi: 10.1007/978-1-4757-0734-2_8. PMID: 371355.; Felig P. Amino acid metabolism in man. Annu Rev Biochem. 1975;44():933–55. doi: 10.1146/annurev.bi.44.070175.004441. PMID: 1094924.
Carnitine synthesis

Accession ID: Reactome:R-MMU-71262
  • 10.1016/0304-4165(80)90133-6
  • 10.1042/0264-6021:3610417
  • 10.1146/annurev.nutr.18.1.179
  • 10.1152/physrev.1983.63.4.1420
Vaz FM, Wanders RJ. Carnitine biosynthesis in mammals. Biochem J. 2002 Feb 01;361(Pt 3):417–29. PMID: 11802770; PMCID: PMC1222323.; Kerner J, Hoppel C. Genetic disorders of carnitine metabolism and their nutritional management. Annu Rev Nutr. 1998;18():179–206. doi: 10.1146/annurev.nutr.18.1.179. PMID: 9706223.; Bremer J. Carnitine--metabolism and functions. Physiol Rev. 1983 Oct;63(4):1420–80. doi: 10.1152/physrev.1983.63.4.1420. PMID: 6361812.; Rebouche CJ, Engel AG. Tissue distribution of carnitine biosynthetic enzymes in man. Biochimica et Biophysica Acta (BBA) - General Subjects. 1980 Jun;630(1):22–9. doi: 10.1016/0304-4165(80)90133-6.
Metabolism

Accession ID: Reactome:R-RNO-1430728
-
Amino acid and derivative metabolism

Accession ID: Reactome:R-RNO-71291
  • 10.1007/978-1-4757-0734-2_8
  • 10.1146/annurev.bi.44.070175.004441
  • 10.1177/014860719001400405
Häussinger D. Liver glutamine metabolism. JPEN J Parenter Enteral Nutr. 1990 Jul;14(4 Suppl):56S–62S. doi: 10.1177/014860719001400405. PMID: 2205732.; Owen OE, Reichard GA, Patel MS, Boden G. Energy metabolism in feasting and fasting. Adv Exp Med Biol. 1979;111():169–88. doi: 10.1007/978-1-4757-0734-2_8. PMID: 371355.; Felig P. Amino acid metabolism in man. Annu Rev Biochem. 1975;44():933–55. doi: 10.1146/annurev.bi.44.070175.004441. PMID: 1094924.