EC: 2.3.1.16

acetyl-CoA C-acyltransferase (acyl-CoA:acetyl-CoA C-acyltransferase)

enzyme lambda metabolic reaction experiment
uniprot:Q3T0R7 [acetyl-CoA C-acyltransferase(Enzyme) wildtype]

Lauroyl_CoA + Acetyldithio_CoA -> Coenzyme_A + 3_Oxotetradecanoyldithio_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 85 mM Tris-HCl
PH: 8.5
Temperature: 25
uniprot:Q3T0R7 [acetyl-CoA C-acyltransferase(Enzyme) wildtype]

Octanoyl_CoA + Acetyldithio_CoA -> Coenzyme_A + 3_Oxodecanoyldithio_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 85 mM Tris-HCl
PH: 8.5
Temperature: 25
uniprot:Q3T0R7 [acetyl-CoA C-acyltransferase(Enzyme) wildtype]

Myristoyl_CoA + Acetyldithio_CoA -> 3_Oxopalmitoyldithio_CoA + Coenzyme_A
(( (Vmax * S) ) / (Km + S)) buffer: 85 mM Tris-HCl
PH: 8.5
Temperature: 25
uniprot:Q3T0R7 [acetyl-CoA C-acyltransferase(Enzyme) wildtype]

Decanoyl_CoA + Acetyldithio_CoA -> Coenzyme_A + 3_Oxododecanoyldithio_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 85 mM Tris-HCl
PH: 8.5
Temperature: 25
uniprot:Q9TUF6 [acetyl-CoA C-acyltransferase(Enzyme) wildtype]

Acetyldithio_CoA + Butanoyl_CoA -> 3_Oxohexanoyldithio_CoA + Coenzyme_A
(( (Vmax * S) ) / (Km + S)) buffer: 85 mM Tris-HCl
PH: 8.5
Temperature: 25
uniprot:Q9TUF6 [acetyl-CoA C-acyltransferase(Enzyme) wildtype]

Octanoyl_CoA + Acetyldithio_CoA -> Coenzyme_A + 3_Oxodecanoyldithio_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 85 mM Tris-HCl
PH: 8.5
Temperature: 25
uniprot:Q3T0R7 [acetyl-CoA C-acyltransferase(Enzyme) wildtype]

Acetyldithio_CoA + Butanoyl_CoA -> 3_Oxohexanoyldithio_CoA + Coenzyme_A
(( (Vmax * S) ) / (Km + S)) buffer: 85 mM Tris-HCl
PH: 8.5
Temperature: 25
uniprot:Q9TUF6 [acetyl-CoA C-acyltransferase(Enzyme) wildtype]

Acetyldithio_CoA + Decanoyl_CoA -> Coenzyme_A + 3_Oxododecanoyldithio_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 85 mM Tris-HCl
PH: 8.5
Temperature: 25
uniprot:Q9TUF6 [acetyl-CoA C-acyltransferase(Enzyme) wildtype]

Hexanoyl_CoA + Acetyldithio_CoA -> Coenzyme_A + 3_Oxooctanoyldithio_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 85 mM Tris-HCl
PH: 8.5
Temperature: 25
uniprot:Q9TUF6 [acetyl-CoA C-acyltransferase(Enzyme) wildtype]

Acetyl_CoA + Acetyldithio_CoA -> 3_Oxobutanoyldithio_CoA + Coenzyme_A
(( (Vmax * S) ) / (Km + S)) buffer: 85 mM Tris-HCl
PH: 8.5
Temperature: 25
uniprot:Q3T0R7 [acetyl-CoA C-acyltransferase(Enzyme) wildtype]

Acetyl_CoA + Acetyldithio_CoA -> 3_Oxobutanoyldithio_CoA + Coenzyme_A
(( (Vmax * S) ) / (Km + S)) buffer: 85 mM Tris-HCl
PH: 8.5
Temperature: 25
uniprot:Q3T0R7 [acetyl-CoA C-acyltransferase(Enzyme) wildtype]

Hexanoyl_CoA + Acetyldithio_CoA -> 3_Oxooctanoyldithio_CoA + Coenzyme_A
(( (Vmax * S) ) / (Km + S)) buffer: 85 mM Tris-HCl
PH: 8.5
Temperature: 25
uniprot:Q9TUF6 [acetyl-CoA C-acyltransferase(Enzyme) wildtype]

Lauroyl_CoA + Acetyldithio_CoA -> Coenzyme_A + 3_Oxotetradecanoyldithio_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 85 mM Tris-HCl
PH: 8.5
Temperature: 25
uniprot:Q9TUF6 [acetyl-CoA C-acyltransferase(Enzyme) wildtype]

Acetyldithio_CoA + Butanoyl_CoA -> 3_Oxohexanoyldithio_CoA + Coenzyme_A
(( (Vmax * S) ) / (Km + S)) buffer: 85 mM Tris-HCl
PH: 8.5
Temperature: 25
uniprot:Q9TUF6 [acetyl-CoA C-acyltransferase(Enzyme) wildtype]

Acetyldithio_CoA + Octanoyl_CoA -> Coenzyme_A + 3_Oxodecanoyldithio_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 85 mM Tris-HCl
PH: 8.5
Temperature: 25
uniprot:Q9TUF6 [acetyl-CoA C-acyltransferase(Enzyme) wildtype]

Acetyldithio_CoA + Myristoyl_CoA -> Coenzyme_A + 3_Oxopalmitoyldithio_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 85 mM Tris-HCl
PH: 8.5
Temperature: 25
uniprot:Q9TUF6 [acetyl-CoA C-acyltransferase(Enzyme) wildtype]

Hexanoyl_CoA + Acetyldithio_CoA -> Coenzyme_A + 3_Oxooctanoyldithio_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 85 mM Tris-HCl
PH: 8.5
Temperature: 25
uniprot:Q9TUF6 [acetyl-CoA C-acyltransferase(Enzyme) wildtype]

Acetyldithio_CoA + Acetyl_CoA -> 3_Oxobutanoyldithio_CoA + Coenzyme_A
(( (Vmax * S) ) / (Km + S)) buffer: 85 mM Tris-HCl
PH: 8.5
Temperature: 25
- [acetyl-CoA C-acyltransferase(Enzyme) wildtype]

Acetoacetyl_CoA + Coenzyme_A -> 2 Acetyl_CoA
(( (Vmax * B) ) / (Km + B)) buffer: 50 mM Tris/HCl
PH: 8
Temperature: 37
- [acetyl-CoA C-acyltransferase(Enzyme) wildtype]

Acetoacetyl_CoA + Coenzyme_A -> 2 Acetyl_CoA
(( (Vmax * A) ) / (Km + A)) buffer: 50 mM Tris/HCl
PH: 8
Temperature: 37
- [acetyl-CoA C-acyltransferase(Enzyme) wildtype]

2 Acetyl_CoA -> Acetoacetyl_CoA + Coenzyme_A
(( (Vmax * A) ) / (Km + A)) buffer: 50 mM Tris/HCl, 0.1 mM NADH, 0.5 U/ml 3-hydroxyacyl-CoA dehydrogenase
PH: 8.8
Temperature: 37
uniprot:P07871 [acetyl-CoA C-acyltransferase(Enzyme) wildtype isoenzyme thiolase B]

Acetoacetyl_CoA + Coenzyme_A -> 2 Acetyl_CoA
(( (Vmax * B) ) / (Km + B)) buffer: 50 mM Tris-HCl, 5 mM MgCl2
PH: 8
Temperature: 37
uniprot:P07871 [acetyl-CoA C-acyltransferase(Enzyme) wildtype isoenzyme thiolase B]

Coenzyme_A + 3_Oxopalmitoyl_CoA -> Myristoyl_CoA + Acetyl_CoA
(( (Vmax * B) ) / (Km + B)) buffer: 50 mM Tris-HCl, 5 mM MgCl2
PH: 8
Temperature: 37
uniprot:P07871 [acetyl-CoA C-acyltransferase(Enzyme) wildtype isoenzyme thiolase B]

3_Oxooctanoyl_CoA + Coenzyme_A -> Hexanoyl_CoA + Acetyl_CoA
(( (Vmax * B) ) / (Km + B)) buffer: 50 mM Tris-HCl, 5 mM MgCl2
PH: 8
Temperature: 37
uniprot:P07871 [acetyl-CoA C-acyltransferase(Enzyme) wildtype isoenzyme thiolase B]

Acetoacetyl_CoA + Coenzyme_A -> 2 Acetyl_CoA
(( (Vmax * B) ) / (Km + B)) buffer: 50 mM Tris-HCl, 5 mM MgCl2
PH: 8
Temperature: 37
uniprot:P07871 [acetyl-CoA C-acyltransferase(Enzyme) wildtype isoenzyme thiolase B]

Coenzyme_A + 3_Oxopalmitoyl_CoA -> Myristoyl_CoA + Acetyl_CoA
(( (Vmax * B) ) / (Km + B)) buffer: 50 mM Tris-HCl, 5 mM MgCl2
PH: 8
Temperature: 37
uniprot:P07871 [acetyl-CoA C-acyltransferase(Enzyme) wildtype isoenzyme thiolase B]

3_Oxooctanoyl_CoA + Coenzyme_A -> Acetyl_CoA + Hexanoyl_CoA
(( (Vmax * B) ) / (Km + B)) buffer: 50 mM Tris-HCl, 5 mM MgCl2
PH: 8
Temperature: 37
uniprot:P07871 [acetyl-CoA C-acyltransferase(Enzyme) wildtype isoenzyme thiolase B]

Coenzyme_A + 3_Oxohexadecandioyl_CoA -> Acetyl_CoA + Tetradecandioyl_CoA
(( (Vmax * B) ) / (Km + B)) buffer: 50 mM Tris-HCl, 5 mM MgCl2
PH: 8
Temperature: 37
uniprot:P07871 [acetyl-CoA C-acyltransferase(Enzyme) wildtype isoenzyme thiolase B]

3_Oxohexadecandioyl_CoA + Coenzyme_A -> Tetradecandioyl_CoA + Acetyl_CoA
(( (Vmax * B) ) / (Km + B)) buffer: 50 mM Tris-HCl, 5 mM MgCl2
PH: 8
Temperature: 37
uniprot:P21775 [acetyl-CoA C-acyltransferase(Enzyme) wildtype isoenzyme thiolase A]

Acetoacetyl_CoA + Coenzyme_A -> 2 Acetyl_CoA
(( (Vmax * A) ) / (Km + A)) buffer: 50 mM Tris-Cl, 5 mM MgCl2
PH: 8
Temperature: 25
uniprot:P21775 [acetyl-CoA C-acyltransferase(Enzyme) wildtype isoenzyme thiolase A]

Coenzyme_A + Acetoacetyl_CoA -> 2 Acetyl_CoA
(( (Vmax * B) ) / (Km + B)) buffer: 50 mM Tris-Cl, 5 mM MgCl2
PH: 8
Temperature: 25
uniprot:P21775 [acetyl-CoA C-acyltransferase(Enzyme) wildtype isoenzyme thiolase A]

Coenzyme_A + 3_Oxooctanoyl_CoA -> Hexanoyl_CoA + Acetyl_CoA
(( (Vmax * A) ) / (Km + A)) buffer: 50 mM Tris-Cl, 5 mM MgCl2
PH: 8
Temperature: 25
uniprot:P11915 [acetyl-CoA C-acyltransferase(Enzyme) wildtype SCP-2]

Coenzyme_A + 3_Oxo_2_methylpalmitoyl_CoA -> Propanoyl_CoA + Myristoyl_CoA
(( (Vmax * A) ) / (( (Km + A) ) + (( (A ^ 2) ) / Ki))) buffer: 50 mM Tris-Cl, 5 mM MgCl2
PH: 8
Temperature: 25
uniprot:P21775 [acetyl-CoA C-acyltransferase(Enzyme) wildtype isoenzyme thiolase A]

3_Oxohexadecandioyl_CoA + Coenzyme_A -> Acetyl_CoA + Tetradecandioyl_CoA
(( (Vmax * A) ) / (Km + A)) buffer: 50 mM Tris-Cl, 5 mM MgCl2
PH: 8
Temperature: 25
uniprot:P11915 [acetyl-CoA C-acyltransferase(Enzyme) wildtype SCP-2]

Acetoacetyl_CoA + Coenzyme_A -> 2 Acetyl_CoA
(( (Vmax * A) ) / (Km + A)) buffer: 50 mM Tris-Cl, 5 mM MgCl2
PH: 8
Temperature: 25
uniprot:P11915 [acetyl-CoA C-acyltransferase(Enzyme) wildtype SCP-2]

3_Oxopalmitoyl_CoA + Coenzyme_A -> Acetyl_CoA + Myristoyl_CoA
(( (Vmax * A) ) / (Km + A)) buffer: 50 mM Tris-Cl, 5 mM MgCl2
PH: 8
Temperature: 25
uniprot:P21775 [acetyl-CoA C-acyltransferase(Enzyme) wildtype isoenzyme thiolase A]

3_Oxopalmitoyl_CoA + Coenzyme_A -> Acetyl_CoA + Myristoyl_CoA
(( (Vmax * B) ) / (Km + B)) buffer: 50 mM Tris-Cl, 5 mM MgCl2
PH: 8
Temperature: 25
uniprot:P11915 [acetyl-CoA C-acyltransferase(Enzyme) wildtype SCP-2]

Coenzyme_A + 3_Oxopalmitoyl_CoA -> Myristoyl_CoA + Acetyl_CoA
(( (Vmax * B) ) / (Km + B)) buffer: 50 mM Tris-Cl, 5 mM MgCl2
PH: 8
Temperature: 25
uniprot:P11915 [acetyl-CoA C-acyltransferase(Enzyme) wildtype SCP-2]

3_Oxooctanoyl_CoA + Coenzyme_A -> Hexanoyl_CoA + Acetyl_CoA
(( (Vmax * A) ) / (Km + A)) buffer: 50 mM Tris-Cl, 5 mM MgCl2
PH: 8
Temperature: 25
uniprot:P21775 [acetyl-CoA C-acyltransferase(Enzyme) wildtype isoenzyme thiolase A]

3_Oxooctanoyl_CoA + Coenzyme_A -> Acetyl_CoA + Hexanoyl_CoA
(( (Vmax * B) ) / (Km + B)) buffer: 50 mM Tris-Cl, 5 mM MgCl2
PH: 8
Temperature: 25
uniprot:P11915 [acetyl-CoA C-acyltransferase(Enzyme) wildtype SCP-2]

3_Oxooctanoyl_CoA + Coenzyme_A -> Acetyl_CoA + Hexanoyl_CoA
(( (Vmax * B) ) / (Km + B)) buffer: 50 mM Tris-Cl, 5 mM MgCl2
PH: 8
Temperature: 25
uniprot:P11915 [acetyl-CoA C-acyltransferase(Enzyme) wildtype SCP-2]

Coenzyme_A + 3_Oxohexadecandioyl_CoA -> Tetradecandioyl_CoA + Acetyl_CoA
(( (Vmax * A) ) / (Km + A)) buffer: 50 mM Tris-Cl, 5 mM MgCl2
PH: 8
Temperature: 25
uniprot:P21775 [acetyl-CoA C-acyltransferase(Enzyme) wildtype isoenzyme thiolase A]

Coenzyme_A + 3_Oxohexadecandioyl_CoA -> Tetradecandioyl_CoA + Acetyl_CoA
(( (Vmax * B) ) / (Km + B)) buffer: 50 mM Tris-Cl, 5 mM MgCl2
PH: 8
Temperature: 25
uniprot:P11915 [acetyl-CoA C-acyltransferase(Enzyme) wildtype SCP-2]

Coenzyme_A + 3alpha,7alpha,12alpha_Trihydroxy_5beta_24_oxocholestanoyl_CoA -> Propanoyl_CoA + Choloyl_CoA
(( (Vmax * A) ) / (( (Km + A) ) + (( (A ^ 2) ) / Ki))) buffer: 50 mM Tris-Cl, 5 mM MgCl2
PH: 8
Temperature: 25
uniprot:P21775 [acetyl-CoA C-acyltransferase(Enzyme) wildtype isoenzyme thiolase A]

Coenzyme_A + 3_Oxopalmitoyl_CoA -> Myristoyl_CoA + Acetyl_CoA
(( (Vmax * A) ) / (Km + A)) buffer: 50 mM Tris-Cl, 5 mM MgCl2
PH: 8
Temperature: 25
uniprot:P11915 [acetyl-CoA C-acyltransferase(Enzyme) wildtype SCP-2]

3alpha,7alpha,12alpha_Trihydroxy_5beta_24_oxocholestanoyl_CoA + Coenzyme_A -> Propanoyl_CoA + Choloyl_CoA
(( (Vmax * B) ) / (Km + B)) buffer: 50 mM Tris-Cl, 5 mM MgCl2
PH: 8
Temperature: 25
uniprot:P11915 [acetyl-CoA C-acyltransferase(Enzyme) wildtype SCP-2]

3_Oxo_2_methylpalmitoyl_CoA + Coenzyme_A -> Propanoyl_CoA + Myristoyl_CoA
(( (Vmax * B) ) / (Km + B)) buffer: 50 mM Tris-Cl, 5 mM MgCl2
PH: 8
Temperature: 25
uniprot:P11915 [acetyl-CoA C-acyltransferase(Enzyme) wildtype SCP-2]

Coenzyme_A + 3_Oxohexadecandioyl_CoA -> Tetradecandioyl_CoA + Acetyl_CoA
(( (Vmax * B) ) / (Km + B)) buffer: 50 mM Tris-Cl, 5 mM MgCl2
PH: 8
Temperature: 25
uniprot:P13437 [acetyl-CoA C-acyltransferase(Enzyme) wildtype isoenzyme Acaa2]

Acetoacetyl_CoA + Coenzyme_A -> 2 Acetyl_CoA
(( (Vmax * S2) ) / (Km2 + S2)) buffer: 100 mM Tris-HCl, 25 mM MgCl2, 50 mM KCl
PH: 8.1
Temperature: 30
uniprot:P13437 [acetyl-CoA C-acyltransferase(Enzyme) wildtype isoenzyme Acaa2]

Acetoacetyl_CoA + Coenzyme_A -> 2 Acetyl_CoA
(( (Vmax * S1) ) / (Km1 + S1)) buffer: 100 mM Tris-HCl, 25 mM MgCl2, 50 mM KCl
PH: 8.1
Temperature: 30
uniprot:I6XHJ3 [Mg2+]

Acetoacetyl_CoA + Coenzyme_A -> 2 Acetyl_CoA
(( (( (kcat * E) ) * A) ) / (Km + A)) buffer: 25 mM HEPES
PH: 7.5
Temperature: 25

Pathways

pathway id name
BioCyc:META_PWY-6863 pyruvate fermentation to hexanol (engineered)
BioCyc:META_FAO-PWY fatty acid β-oxidation I
BioCyc:META_PWY-7339 10-trans-heptadecenoyl-CoA degradation (MFE-dependent, yeast)
BioCyc:META_PWY-7338 10-trans-heptadecenoyl-CoA degradation (reductase-dependent, yeast)
BioCyc:ECO_FAO-PWY fatty acid β-oxidation I
BioCyc:YEAST_PWY-7288 fatty acid β-oxidation (peroxisome)
BioCyc:MTBH37RV_PWY-6946 cholesterol degradation to androstenedione II (cholesterol dehydrogenase)
BioCyc:ECOO157_PWY-7003 glycerol degradation to butanol
BioCyc:ECOO157_PWY-5177 glutaryl-CoA degradation
BioCyc:ECOO157_PWY-5676 acetyl-CoA fermentation to butyrate II
BioCyc:ECOO157_PWY-6590 superpathway of Clostridium acetobutylicum acidogenic fermentation
BioCyc:MOUSE_PWY-5138 fatty acid β-oxidation IV (unsaturated, even number)
BioCyc:MOUSE_PWY-6061 bile acid biosynthesis, neutral pathway
BioCyc:BSUB_FAO-PWY fatty acid β-oxidation I
BioCyc:ECOL316407_FAO-PWY fatty acid β-oxidation I
BioCyc:META_PWY-7340 9-cis, 11-trans-octadecadienoyl-CoA degradation (isomerase-dependent, yeast)
BioCyc:META_PWY-7337 10-cis-heptadecenoyl-CoA degradation (yeast)
BioCyc:META_PWY-6946 cholesterol degradation to androstenedione II (cholesterol dehydrogenase)
BioCyc:YEAST_PWY-7338 10-trans-heptadecenoyl-CoA degradation (reductase-dependent)
BioCyc:YEAST_PWY-7339 10-trans-heptadecenoyl-CoA degradation (MFE-dependent)
BioCyc:VCHO_FAO-PWY fatty acid β-oxidation I
BioCyc:ECOO157_CENTFERM-PWY pyruvate fermentation to butanoate
BioCyc:META_PWY1-3 polyhydroxybutanoate biosynthesis
BioCyc:META_PWY-7216 (R)- and (S)-3-hydroxybutanoate biosynthesis (engineered)
BioCyc:META_PWY-7218 photosynthetic 3-hydroxybutanoate biosynthesis (engineered)
BioCyc:META_PWY-7948 4-oxopentanoate degradation
BioCyc:META_PWY-7288 fatty acid β-oxidation (peroxisome, yeast)
BioCyc:META_PWY-735 jasmonic acid biosynthesis
BioCyc:META_PWY-6944 androstenedione degradation
BioCyc:YEAST_PWY-7337 10-cis-heptadecenoyl-CoA degradation
BioCyc:ARA_PWY-5136 fatty acid β-oxidation II (peroxisome)
BioCyc:MTBH37RV_PWY-6947 superpathway of cholesterol degradation II (cholesterol dehydrogenase)
BioCyc:MTBH37RV_PWY-6945 cholesterol degradation to androstenedione I (cholesterol oxidase)
BioCyc:ECOO157_GLUDEG-II-PWY glutamate degradation VII (to butanoate)
BioCyc:ECOL199310_ILEUDEG-PWY isoleucine degradation I
BioCyc:ECOL199310_FAO-PWY fatty acid β-oxidation I
BioCyc:HUMAN_FAO-PWY fatty acid β-oxidation
BioCyc:HUMAN_PWY66-391 fatty acid β-oxidation (peroxisome)
BioCyc:META_PWY-561 superpathway of glyoxylate cycle and fatty acid degradation
BioCyc:META_PWY-5136 fatty acid β-oxidation II (peroxisome)
BioCyc:META_PWY66-391 fatty acid β-oxidation VI (peroxisome)
BioCyc:META_PWY-6947 superpathway of cholesterol degradation II (cholesterol dehydrogenase)
BioCyc:META_PWY-6945 cholesterol degradation to androstenedione I (cholesterol oxidase)
BioCyc:YEAST_YEAST-FAO-PWY fatty acid oxidation (non-cyclic)
BioCyc:YEAST_PWY-7340 9-cis, 11-trans-octadecadienoyl-CoA degradation (isomerase-dependent)
BioCyc:MTBH37RV_PWY-6944 androstenedione degradation
BioCyc:ECOO157_PWY-7401 crotonate fermentation (to acetate and cyclohexane carboxylate)
BioCyc:ECOO157_ACETOACETATE-DEG-PWY acetoacetate degradation (to acetyl CoA)
BioCyc:MOUSE_FAO-PWY fatty acid β-oxidation I
BioCyc:MOUSE_PWY-2361 3-oxoadipate degradation
BioCyc:MOUSE_PWY-5136 fatty acid β-oxidation II (core pathway)
WikiPathways:WP2472 Escherichia coli K-12 peripherome
PathBank:SMP0000781 Fatty Acid Oxidation
PathBank:SMP0001033 fatty acid oxidation (Butanoate)
PathBank:SMP0001034 fatty acid oxidation (Decanoate)
PathBank:SMP0001035 fatty acid oxidation (hexanoate)
PathBank:SMP0001036 Fatty Acid Oxidation (Laurate)
PathBank:SMP0001037 fatty acid oxidation (myristate)
PathBank:SMP0001038 fatty acid oxidation (octanoate)
PathBank:SMP0001039 fatty acid oxidation (palmitate)
PathBank:SMP0001040 fatty acid oxidation (steareate)
Reactome:R-BTA-1430728 Metabolism
Reactome:R-BTA-556833 Metabolism of lipids
Reactome:R-BTA-77286 mitochondrial fatty acid beta-oxidation of saturated fatty acids
Reactome:R-BTA-77346 Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA
Reactome:R-CEL-77286 mitochondrial fatty acid beta-oxidation of saturated fatty acids
Reactome:R-CEL-77346 Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA
Reactome:R-HSA-2046106 alpha-linolenic acid (ALA) metabolism
Reactome:R-HSA-77286 mitochondrial fatty acid beta-oxidation of saturated fatty acids
Reactome:R-HSA-77346 Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA
Reactome:R-HSA-77288 mitochondrial fatty acid beta-oxidation of unsaturated fatty acids
Reactome:R-HSA-9033500 TYSND1 cleaves peroxisomal proteins
Reactome:R-MMU-1430728 Metabolism
Reactome:R-MMU-556833 Metabolism of lipids
Reactome:R-MMU-2046106 alpha-linolenic acid (ALA) metabolism
Reactome:R-MMU-77286 mitochondrial fatty acid beta-oxidation of saturated fatty acids
Reactome:R-MMU-77346 Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA
Reactome:R-MMU-389887 Beta-oxidation of pristanoyl-CoA
Reactome:R-MMU-8957322 Metabolism of steroids
Reactome:R-RNO-8978868 Fatty acid metabolism
Reactome:R-RNO-2046104 alpha-linolenic (omega3) and linoleic (omega6) acid metabolism
Reactome:R-RNO-77289 Mitochondrial Fatty Acid Beta-Oxidation
Reactome:R-RNO-77310 Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA
Reactome:R-RNO-1482798 Acyl chain remodeling of CL
Reactome:R-RNO-193368 Synthesis of bile acids and bile salts via 7alpha-hydroxycholesterol
Reactome:R-SCE-2046106 alpha-linolenic acid (ALA) metabolism
Reactome:R-BTA-8978868 Fatty acid metabolism
Reactome:R-BTA-77289 Mitochondrial Fatty Acid Beta-Oxidation
Reactome:R-BTA-77310 Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA
Reactome:R-CEL-556833 Metabolism of lipids
Reactome:R-CEL-77289 Mitochondrial Fatty Acid Beta-Oxidation
Reactome:R-CEL-77310 Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA
Reactome:R-HSA-556833 Metabolism of lipids
Reactome:R-HSA-8978868 Fatty acid metabolism
Reactome:R-HSA-2046104 alpha-linolenic (omega3) and linoleic (omega6) acid metabolism
Reactome:R-HSA-77289 Mitochondrial Fatty Acid Beta-Oxidation
Reactome:R-HSA-77310 Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA
Reactome:R-HSA-1482798 Acyl chain remodeling of CL
Reactome:R-HSA-9033241 Peroxisomal protein import
Reactome:R-MMU-8978868 Fatty acid metabolism
Reactome:R-MMU-2046104 alpha-linolenic (omega3) and linoleic (omega6) acid metabolism
Reactome:R-MMU-77289 Mitochondrial Fatty Acid Beta-Oxidation
Reactome:R-MMU-77310 Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA
Reactome:R-MMU-1482798 Acyl chain remodeling of CL
Reactome:R-MMU-193368 Synthesis of bile acids and bile salts via 7alpha-hydroxycholesterol
Reactome:R-RNO-77285 Beta oxidation of myristoyl-CoA to lauroyl-CoA
Reactome:R-RNO-77350 Beta oxidation of hexanoyl-CoA to butanoyl-CoA
Reactome:R-RNO-390918 Peroxisomal lipid metabolism
Reactome:R-RNO-1483206 Glycerophospholipid biosynthesis
Reactome:R-RNO-192105 Synthesis of bile acids and bile salts
Reactome:R-SCE-1430728 Metabolism
Reactome:R-SCE-8978868 Fatty acid metabolism
Reactome:R-SCE-2046104 alpha-linolenic (omega3) and linoleic (omega6) acid metabolism
Reactome:R-SCE-390918 Peroxisomal lipid metabolism
Reactome:R-BTA-77305 Beta oxidation of palmitoyl-CoA to myristoyl-CoA
Reactome:R-BTA-77348 Beta oxidation of octanoyl-CoA to hexanoyl-CoA
Reactome:R-BTA-1483257 Phospholipid metabolism
Reactome:R-CEL-8978868 Fatty acid metabolism
Reactome:R-CEL-77305 Beta oxidation of palmitoyl-CoA to myristoyl-CoA
Reactome:R-CEL-77348 Beta oxidation of octanoyl-CoA to hexanoyl-CoA
Reactome:R-CEL-1483257 Phospholipid metabolism
Reactome:R-HSA-77305 Beta oxidation of palmitoyl-CoA to myristoyl-CoA
Reactome:R-HSA-77348 Beta oxidation of octanoyl-CoA to hexanoyl-CoA
Reactome:R-HSA-390247 Beta-oxidation of very long chain fatty acids
Reactome:R-HSA-1483257 Phospholipid metabolism
Reactome:R-HSA-9609507 Protein localization
Reactome:R-MMU-77305 Beta oxidation of palmitoyl-CoA to myristoyl-CoA
Reactome:R-MMU-77348 Beta oxidation of octanoyl-CoA to hexanoyl-CoA
Reactome:R-MMU-390247 Beta-oxidation of very long chain fatty acids
Reactome:R-MMU-1483257 Phospholipid metabolism
Reactome:R-MMU-194068 Bile acid and bile salt metabolism
Reactome:R-RNO-1430728 Metabolism
Reactome:R-RNO-556833 Metabolism of lipids
Reactome:R-RNO-2046106 alpha-linolenic acid (ALA) metabolism
Reactome:R-RNO-77286 mitochondrial fatty acid beta-oxidation of saturated fatty acids
Reactome:R-RNO-77346 Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA
Reactome:R-RNO-389887 Beta-oxidation of pristanoyl-CoA
Reactome:R-RNO-8957322 Metabolism of steroids
Reactome:R-SCE-556833 Metabolism of lipids
Reactome:R-BTA-77285 Beta oxidation of myristoyl-CoA to lauroyl-CoA
Reactome:R-BTA-77350 Beta oxidation of hexanoyl-CoA to butanoyl-CoA
Reactome:R-BTA-1483206 Glycerophospholipid biosynthesis
Reactome:R-BTA-1482798 Acyl chain remodeling of CL
Reactome:R-CEL-1430728 Metabolism
Reactome:R-CEL-77285 Beta oxidation of myristoyl-CoA to lauroyl-CoA
Reactome:R-CEL-77350 Beta oxidation of hexanoyl-CoA to butanoyl-CoA
Reactome:R-CEL-1483206 Glycerophospholipid biosynthesis
Reactome:R-CEL-1482798 Acyl chain remodeling of CL
Reactome:R-HSA-1430728 Metabolism
Reactome:R-HSA-77285 Beta oxidation of myristoyl-CoA to lauroyl-CoA
Reactome:R-HSA-77350 Beta oxidation of hexanoyl-CoA to butanoyl-CoA
Reactome:R-HSA-390918 Peroxisomal lipid metabolism
Reactome:R-HSA-1483206 Glycerophospholipid biosynthesis
Reactome:R-MMU-77285 Beta oxidation of myristoyl-CoA to lauroyl-CoA
Reactome:R-MMU-77350 Beta oxidation of hexanoyl-CoA to butanoyl-CoA
Reactome:R-MMU-390918 Peroxisomal lipid metabolism
Reactome:R-MMU-1483206 Glycerophospholipid biosynthesis
Reactome:R-MMU-192105 Synthesis of bile acids and bile salts
Reactome:R-RNO-77305 Beta oxidation of palmitoyl-CoA to myristoyl-CoA
Reactome:R-RNO-77348 Beta oxidation of octanoyl-CoA to hexanoyl-CoA
Reactome:R-RNO-390247 Beta-oxidation of very long chain fatty acids
Reactome:R-RNO-1483257 Phospholipid metabolism
Reactome:R-RNO-194068 Bile acid and bile salt metabolism
Reactome:R-SCE-390247 Beta-oxidation of very long chain fatty acids
WikiPathways:WP5123 Mitochondrial fatty acid oxidation disorders
WikiPathways:WP1941 Peroxisomal beta-oxidation of tetracosanoyl-CoA
WikiPathways:WP2318 Fatty acid oxidation
PathBank:SMP0120662 3-Methylcrotonyl-CoA Carboxylase Deficiency Type I
PathBank:SMP0120806 3-Hydroxyisobutyric Aciduria
PathBank:SMP0120822 Carnitine Palmitoyl Transferase Deficiency I
PathBank:SMP0120826 Medium Chain Acyl-CoA Dehydrogenase Deficiency (MCAD)
PathBank:SMP0120440 3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency
PathBank:SMP0120444 3-Methylglutaconic Aciduria Type IV
PathBank:SMP0120468 Congenital Bile Acid Synthesis Defect Type III
PathBank:SMP0120516 Maple Syrup Urine Disease
PathBank:SMP0120589 Isovaleric Acidemia
PathBank:SMP0121348 Fatty Acid Oxidation (Hexanoate)
PathBank:SMP0121352 Fatty Acid Oxidation (Palmitate)
PathBank:SMP0000032 Valine, Leucine, and Isoleucine Degradation
PathBank:SMP0000051 Fatty Acid Metabolism
PathBank:SMP0000173 beta-Ketothiolase Deficiency
PathBank:SMP0000199 Maple Syrup Urine Disease
PathBank:SMP0000384 Methylmalonate Semialdehyde Dehydrogenase Deficiency
PathBank:SMP0000235 Short-Chain Acyl-CoA Dehydrogenase Deficiency (SCAD Deficiency)
PathBank:SMP0000482 Mitochondrial Beta-Oxidation of Long Chain Saturated Fatty Acids
PathBank:SMP0000318 Congenital Bile Acid Synthesis Defect Type III
PathBank:SMP0000141 3-Methylglutaconic Aciduria Type IV
PathBank:SMP0000524 Isovaleric Acidemia
PathBank:SMP0000540 Very-Long-Chain Acyl-CoA Dehydrogenase Deficiency (VLCAD)
PathBank:SMP0000544 Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase Deficiency (LCHAD)
PathBank:SMP0000568 Short-Chain 3-Hydroxyacyl-CoA Dehydrogenase Deficiency (SCHAD)
PathBank:SMP0087294 Fatty Acid Elongation in Mitochondria
PathBank:SMP0087358 Mitochondrial Beta-Oxidation of Short Chain Saturated Fatty Acids
PathBank:SMP0087430 Fatty Acid Metabolism
PathBank:SMP0120661 3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency
PathBank:SMP0120665 3-Methylglutaconic Aciduria Type IV
PathBank:SMP0120745 Methylmalonic Aciduria
PathBank:SMP0120757 Propionic Acidemia
PathBank:SMP0120805 3-Hydroxyisobutyric Acid Dehydrogenase Deficiency
PathBank:SMP0120825 Carnitine Palmitoyl Transferase Deficiency II
PathBank:SMP0120439 2-Methyl-3-hydroxybutryl-CoA Dehydrogenase Deficiency
PathBank:SMP0120443 3-Methylglutaconic Aciduria Type III
PathBank:SMP0120459 beta-Ketothiolase Deficiency
PathBank:SMP0120463 Cerebrotendinous Xanthomatosis (CTX)
PathBank:SMP0120467 Congenital Bile Acid Synthesis Defect Type II
PathBank:SMP0120495 Zellweger Syndrome
PathBank:SMP0120503 Isovaleric Aciduria
PathBank:SMP0120523 Methylmalonate Semialdehyde Dehydrogenase Deficiency
PathBank:SMP0120588 Isobutyryl-CoA Dehydrogenase Deficiency
PathBank:SMP0120632 Short-Chain 3-Hydroxyacyl-CoA Dehydrogenase Deficiency (SCHAD)
PathBank:SMP0121206 Jasmonic Acid Biosynthesis
PathBank:SMP0121347 Fatty Acid Oxidation (Decanoate)
PathBank:SMP0121351 Fatty Acid Oxidation (Octanoate)
PathBank:SMP0000054 Fatty Acid Elongation in Mitochondria
PathBank:SMP0000035 Bile Acid Biosynthesis
PathBank:SMP0000138 3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency
PathBank:SMP0000140 3-Methylglutaconic Aciduria Type III
PathBank:SMP0000238 Isovaleric Aciduria
PathBank:SMP0000185 Glutaric Aciduria Type I
PathBank:SMP0000481 Mitochondrial Beta-Oxidation of Medium Chain Saturated Fatty Acids
PathBank:SMP0000314 Congenital Bile Acid Synthesis Defect Type II
PathBank:SMP0000315 Cerebrotendinous Xanthomatosis (CTX)
PathBank:SMP0000523 Isobutyryl-CoA Dehydrogenase Deficiency
PathBank:SMP0000539 Long Chain Acyl-CoA Dehydrogenase Deficiency (LCAD)
PathBank:SMP0002361 Fatty Acid Metabolism
PathBank:SMP0002368 Fatty Acid Elongation In Mitochondria
PathBank:SMP0002381 Steroid Biosynthesis
PathBank:SMP0087521 Mitochondrial Beta-Oxidation of Medium Chain Saturated Fatty Acids
PathBank:SMP0063641 Mitochondrial Beta-Oxidation of Short Chain Saturated Fatty Acids
PathBank:SMP0063689 Valine, Leucine, and Isoleucine Degradation
PathBank:SMP0120652 27-Hydroxylase Deficiency
PathBank:SMP0120660 2-Methyl-3-hydroxybutryl-CoA Dehydrogenase Deficiency
PathBank:SMP0120664 3-Methylglutaconic Aciduria Type III
PathBank:SMP0120696 Ethylmalonic Encephalopathy
PathBank:SMP0120736 Maple Syrup Urine Disease
PathBank:SMP0120740 Short-Chain Acyl-CoA Dehydrogenase Deficiency (SCAD Deficiency)
PathBank:SMP0120808 Isovaleric Acidemia
PathBank:SMP0120824 Very-Long-Chain Acyl-CoA Dehydrogenase Deficiency (VLCAD)
PathBank:SMP0120828 Trifunctional Protein Deficiency
PathBank:SMP0120441 3-Methylcrotonyl-CoA Carboxylase Deficiency Type I
PathBank:SMP0120477 Familial Hypercholanemia (FHCA)
PathBank:SMP0120525 Methylmalonic Aciduria
PathBank:SMP0120537 Propionic Acidemia
PathBank:SMP0120586 3-Hydroxyisobutyric Acid Dehydrogenase Deficiency
PathBank:SMP0121261 Fatty Acid Oxidation
PathBank:SMP0121349 Fatty Acid Oxidation (Laurate)
PathBank:SMP0121353 Fatty Acid Oxidation (Steareate)
PathBank:SMP0000137 2-Methyl-3-hydroxybutyryl-CoA Dehydrogenase Deficiency
PathBank:SMP0000237 3-Methylcrotonyl-CoA Carboxylase Deficiency Type I
PathBank:SMP0000200 Methylmalonic Aciduria
PathBank:SMP0000317 Familial Hypercholanemia (FHCA)
PathBank:SMP0000521 3-Hydroxyisobutyric Acid Dehydrogenase Deficiency
PathBank:SMP0000541 Carnitine Palmitoyl Transferase Deficiency II
PathBank:SMP0000545 Trifunctional Protein Deficiency
PathBank:SMP0002383 Ketone Body Metabolism
PathBank:SMP0087280 Fatty Acid Metabolism
PathBank:SMP0087360 Mitochondrial Beta-Oxidation of Long Chain Saturated Fatty Acids
PathBank:SMP0012062 Fatty Acid Beta-Oxidation I
PathBank:SMP0063640 Mitochondrial Beta-Oxidation of Medium Chain Saturated Fatty Acids
PathBank:SMP0120663 3-Methylglutaconic Aciduria Type I
PathBank:SMP0120679 beta-Ketothiolase Deficiency
PathBank:SMP0120723 Isovaleric Aciduria
PathBank:SMP0120743 Methylmalonate Semialdehyde Dehydrogenase Deficiency
PathBank:SMP0120807 Isobutyryl-CoA Dehydrogenase Deficiency
PathBank:SMP0120823 Long Chain Acyl-CoA Dehydrogenase Deficiency (LCAD)
PathBank:SMP0120827 Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase Deficiency (LCHAD)
PathBank:SMP0120851 Short-Chain 3-Hydroxyacyl-CoA Dehydrogenase Deficiency (SCHAD)
PathBank:SMP0120442 3-Methylglutaconic Aciduria Type I
PathBank:SMP0120587 3-Hydroxyisobutyric Aciduria
PathBank:SMP0121346 Fatty Acid Oxidation (Butanoate)
PathBank:SMP0121350 Fatty Acid Oxidation (Myristate)
PathBank:SMP0122254 Acetate Metabolism
PathBank:SMP0000236 Propionic Acidemia
PathBank:SMP0000139 3-Methylglutaconic Aciduria Type I
PathBank:SMP0000181 Ethylmalonic Encephalopathy
PathBank:SMP0000480 Mitochondrial Beta-Oxidation of Short Chain Saturated Fatty Acids
PathBank:SMP0000316 Zellweger Syndrome
PathBank:SMP0000522 3-Hydroxyisobutyric Aciduria
PathBank:SMP0000538 Carnitine Palmitoyl Transferase Deficiency I
PathBank:SMP0000542 Medium Chain Acyl-CoA Dehydrogenase Deficiency (MCAD)
PathBank:SMP0000635 Valproic Acid Metabolism Pathway
PathBank:SMP0000720 27-Hydroxylase Deficiency
PathBank:SMP0002384 Terpenoid Backbone Biosynthesis
PathBank:SMP0087327 Valine, Leucine, and Isoleucine Degradation
PathBank:SMP0087359 Mitochondrial Beta-Oxidation of Medium Chain Saturated Fatty Acids
PathBank:SMP0087523 Mitochondrial Beta-Oxidation of Long Chain Saturated Fatty Acids
PathBank:SMP0063601 Bile Acid Biosynthesis
PathBank:SMP0063639 Mitochondrial Beta-Oxidation of Long Chain Saturated Fatty Acids