Peroxisomal lipid metabolism
Wanders RJ, Waterham HR. Biochemistry of mammalian peroxisomes revisited. Annu Rev Biochem. 2006;75():295–332. doi: 10.1146/annurev.biochem.74.082803.133329. PMID: 16756494.
Metabolites
Enzyme
| EC Number | name | full name | note |
|---|---|---|---|
| 1.2.1.3 | aldehyde dehydrogenase (NAD+) | aldehyde:NAD+ oxidoreductase | |
| 1.2.1.64 | 4-hydroxybenzaldehyde dehydrogenase (NAD+) | 4-hydroxybenzaldehyde:NAD+ oxidoreductase | |
| 1.3.1.124 | 2,4-dienoyl-CoA reductase [(3E)-enoyl-CoA-producing] | (3E)-3-enoyl-CoA:NADP+ 4-oxidoreductase | |
| 1.3.3.6 | acyl-CoA oxidase | acyl-CoA:oxygen 2-oxidoreductase | |
| 2.3.1.16 | acetyl-CoA C-acyltransferase | acyl-CoA:acetyl-CoA C-acyltransferase | |
| 2.3.1.7 | carnitine O-acetyltransferase | acetyl-CoA:carnitine O-acetyltransferase | |
| 3.1.2.2 | palmitoyl-CoA hydrolase | palmitoyl-CoA hydrolase | |
| 4.1.2.63 | 2-hydroxyacyl-CoA lyase | 2-hydroxy-3-methyl fatty-CoA formyl-CoA lyase (2-methyl branched fatty aldehyde-forming) | |
| 5.3.3.8 | DELTA3-DELTA2-enoyl-CoA isomerase | (3Z/3E)-alk-3-enoyl-CoA (2E)-isomerase |
Proteins
| Protein ID | name | full name |
|---|---|---|
| P13711 | POX1 | Acyl-coenzyme A oxidase |
| P27796 | POT1 | 3-ketoacyl-CoA thiolase, peroxisomal |
| P32573 | SPS19 | Peroxisomal 2,4-dienoyl-CoA reductase SPS19 [(3E)-enoyl-CoA-producing] |
| P32796 | CAT2 | Carnitine O-acetyltransferase, mitochondrial |
| P39994 | PXP1 | 2-hydroxyacyl-CoA lyase |
| P41903 | TES1 | Peroxisomal acyl-coenzyme A thioester hydrolase 1 |
| Q04458 | HFD1 | Fatty aldehyde dehydrogenase HFD1 |
| Q05871 | ECI1 | 3,2-trans-enoyl-CoA isomerase |