gamma-Glutamyltranspeptidase Deficiency

Metabolites

(-)-Pyroglutamate

Formula: C5H7NO3 (129.0425912)

CAS ID: 98-79-3

ADP

Formula: C10H15N5O10P2 (427.02941500000003)

CAS ID: 58-64-0

ATP

Formula: C10H16N5O13P3 (506.9957476)

CAS ID: 56-65-5

Cys-Gly

Formula: C5H10N2O3S (178.041211)

CAS ID: 19246-18-5

Glutathione

Formula: C10H17N3O6S (307.08380220000004)

CAS ID: 70-18-8

H2O

Formula: H2O (18.0105642)

CAS ID: 7732-18-5

Hydrogen peroxide

Formula: H2O2 (34.0054792)

CAS ID: 7722-84-1

L-Alanine

Formula: C3H7NO2 (89.0476762)

CAS ID: 56-41-7

L-Cysteine

Formula: C3H7NO2S (121.0197482)

CAS ID: 52-90-4

L-Glutamate

Formula: C5H9NO4 (147.0531554)

CAS ID: 56-86-0

Methyl bromide

Formula: CH3Br (93.9418098)

CAS ID: 74-83-9

NADP+

Formula: C21H29N7O17P3 (744.0832754)

CAS ID: 53-59-8

Orthophosphate

Formula: H3PO4 (97.9768968)

CAS ID: 7664-38-2

S-Methyl GSH

Formula: C11H19N3O6S (321.0994514)

CAS ID: 2922-56-7



Enzyme

EC Number name full name note
1.11.1.12 phospholipid-hydroperoxide glutathione peroxidase glutathione:lipid-hydroperoxide oxidoreductase
1.11.1.9 glutathione peroxidase glutathione:hydrogen-peroxide oxidoreductase
1.20.4.2 methylarsonate reductase glutathione:methylarsonate oxidoreductase
1.8.5.1 glutathione dehydrogenase (ascorbate) glutathione:dehydroascorbate oxidoreductase
2.3.2.2 gamma-glutamyltransferase (5-L-glutamyl)-peptide:amino-acid 5-glutamyltransferase
2.5.1.18 glutathione transferase RX:glutathione R-transferase
3.4.11.2 membrane alanyl aminopeptidase
3.4.19.13 glutathione gamma-glutamate hydrolase
3.4.22.60 caspase-7
3.5.2.9 5-oxoprolinase (ATP-hydrolysing) 5-oxo-L-proline amidohydrolase (ATP-hydrolysing)
4.3.2.9 gamma-glutamylcyclotransferase alpha-(gamma-L-glutamyl)-L-amino-acid gamma-glutamyl cyclotransferase (5-oxo-L-proline producing)
6.3.2.2 glutamate-cysteine ligase L-glutamate:L-cysteine gamma-ligase (ADP-forming)
6.3.2.3 glutathione synthase gamma-L-glutamyl-L-cysteine:glycine ligase (ADP-forming)


Proteins

Protein ID name full name