Familial Lipoprotein Lipase Deficiency

Metabolites

ADP

Formula: C10H15N5O10P2 (427.02941500000003)

CAS ID: 58-64-0

ATP

Formula: C10H16N5O13P3 (506.9957476)

CAS ID: 56-65-5

D-Glycerate

Formula: C3H6O4 (106.0266076)

CAS ID: 473-81-4

Glyceraldehyde

Formula: C3H6O3 (90.0316926)

CAS ID: 367-47-5

Glycerate 3-phosphate

Formula: C3H7O7P (185.9929402)

CAS ID: 820-11-1

Glycerol

Formula: C3H8O3 (92.0473418)

CAS ID: 56-81-5

Glycerone phosphate

Formula: C3H7O6P (169.9980252)

CAS ID: 57-04-5

H2O

Formula: H2O (18.0105642)

CAS ID: 7732-18-5

Hexadecanoic acid

Formula: C16H32O2 (256.2402172)

CAS ID: 57-10-3

Hydroquinone

Formula: C6H6O2 (110.0367776)

CAS ID: 123-31-9

NAD+

Formula: C21H28N7O14P2 (664.1169428000001)

CAS ID: 53-84-9

NADH

Formula: C21H29N7O14P2 (665.1247674)

CAS ID: 58-68-4

NADP+

Formula: C21H29N7O17P3 (744.0832754)

CAS ID: 53-59-8

p-Benzoquinone

Formula: C6H4O2 (108.0211284)

CAS ID: 106-51-4

sn-Glycerol 3-phosphate

Formula: C3H9O6P (172.01367439999999)

CAS ID: 17989-41-2

PA(16:0/16:0)

Formula: C35H69O8P (648.4729804)

CAS ID: 7091-44-3

TG(16:0/16:0/16:0)

Formula: C51H98O6 (806.7363008)

CAS ID: 555-44-2

DG(16:0/16:0/0:0)

Formula: C35H68O5 (568.5066478)

CAS ID: 30334-71-5

MG(0:0/16:0/0:0)

Formula: C19H38O4 (330.2769948)

CAS ID: 23470-00-0

PA(16:0/0:0)

Formula: C19H39O7P (410.2433274)

CAS ID: 7220-34-0

phosphate(3-)

Formula: O4P (94.953423)

CAS ID: 14265-44-2



Enzyme

EC Number name full name note
3.1.3.-
1.1.1.21 aldose reductase alditol:NAD(P)+ 1-oxidoreductase
1.1.1.300 NADP-retinol dehydrogenase retinol:NADP+ oxidoreductase
1.1.1.372 D/L-glyceraldehyde reductase glycerol:NADP+ oxidoreductase (D/L-glyceraldehyde-forming)
1.1.1.54 allyl-alcohol dehydrogenase allyl-alcohol:NADP+ oxidoreductase
1.1.5.3 glycerol-3-phosphate dehydrogenase sn-glycerol 3-phosphate:quinone oxidoreductase
1.2.1.5 aldehyde dehydrogenase [NAD(P)+] aldehyde:NAD(P)+ oxidoreductase
2.3.1.15 glycerol-3-phosphate 1-O-acyltransferase acyl-CoA:sn-glycerol-3-phosphate 1-O-acyltransferase
2.3.1.51 1-acylglycerol-3-phosphate O-acyltransferase acyl-CoA:1-acyl-sn-glycerol-3-phosphate 2-O-acyltransferase
2.7.1.107 diacylglycerol kinase (ATP) ATP:1,2-diacyl-sn-glycerol 3-phosphotransferase
2.7.1.30 glycerol kinase ATP:glycerol 3-phosphotransferase
2.7.1.31 glycerate 3-kinase ATP:D-glycerate 3-phosphotransferase
2.7.1.93 alkylglycerol kinase ATP:1-O-alkyl-sn-glycerol 3-phosphotransferase
3.1.1.3 triacylglycerol lipase triacylglycerol acylhydrolase
3.1.1.32 phospholipase A1 phosphatidylcholine 1-acylhydrolase
3.1.1.34 lipoprotein lipase triacylglycero-protein acylhydrolase
3.1.1.5 lysophospholipase 2-lysophosphatidylcholine acylhydrolase
3.1.3.4 phosphatidate phosphatase diacylglycerol-3-phosphate phosphohydrolase


Proteins

Protein ID name full name