EC: 6.3.2.3

glutathione synthase (gamma-L-glutamyl-L-cysteine:glycine ligase (ADP-forming))

enzyme lambda metabolic reaction experiment
uniprot:P48637 [glutathione synthase(Enzyme) wildtype His-tagged]

ATP + Glycine + L_gamma_Glutamyl_L_alpha_aminobutyrate -> ADP + gamma_L_Glutamyl_L_alpha_aminobutyryl_glycine + Phosphate		 (( (Vmax * A) ) / (Km + A)) buffer: 100 mM Tris/HCl, 50 mM KCl, 20 mM MgCl2, 5 mM sodium phosphoenolpyruvate, 10 units/ml lactic acid dehydrogenase (Type II rabbit muscle), 10 units/ml pyruvate kinase (Type III rabbit muscle), 0.2 mM NADH
PH: 8.2
Temperature: 37
uniprot:P48637 [glutathione synthase(Enzyme) mutant His-tagged L188P]

Glycine + L_gamma_Glutamyl_L_alpha_aminobutyrate + ATP -> ADP + Phosphate + gamma_L_Glutamyl_L_alpha_aminobutyryl_glycine		 (( (Vmax * A) ) / (Km + A)) buffer: 100 mM Tris/HCl, 50 mM KCl, 20 mM MgCl2, 5 mM sodium phosphoenolpyruvate, 10 units/ml lactic acid dehydrogenase (Type II rabbit muscle), 10 units/ml pyruvate kinase (Type III rabbit muscle), 0.2 mM NADH
PH: 8.2
Temperature: 37
uniprot:P48637 [glutathione synthase(Enzyme) mutant His-tagged D219A]

ATP + L_gamma_Glutamyl_L_alpha_aminobutyrate + Glycine -> Phosphate + ADP + gamma_L_Glutamyl_L_alpha_aminobutyryl_glycine		 (( (Vmax * A) ) / (Km + A)) buffer: 100 mM Tris/HCl, 50 mM KCl, 20 mM MgCl2, 5 mM sodium phosphoenolpyruvate, 10 units/ml lactic acid dehydrogenase (Type II rabbit muscle), 10 units/ml pyruvate kinase (Type III rabbit muscle), 0.2 mM NADH
PH: 8.2
Temperature: 37
uniprot:P48637 [glutathione synthase(Enzyme) mutant His-tagged Y270C]

Glycine + L_gamma_Glutamyl_L_alpha_aminobutyrate + ATP -> ADP + gamma_L_Glutamyl_L_alpha_aminobutyryl_glycine + Phosphate		 (( (Vmax * A) ) / (Km + A)) buffer: 100 mM Tris/HCl, 50 mM KCl, 20 mM MgCl2, 5 mM sodium phosphoenolpyruvate, 10 units/ml lactic acid dehydrogenase (Type II rabbit muscle), 10 units/ml pyruvate kinase (Type III rabbit muscle), 0.2 mM NADH
PH: 8.2
Temperature: 37
uniprot:P48637 [glutathione synthase(Enzyme) mutant His-tagged Y270H]

ATP + L_gamma_Glutamyl_L_alpha_aminobutyrate + Glycine -> ADP + Phosphate + gamma_L_Glutamyl_L_alpha_aminobutyryl_glycine		 (( (Vmax * A) ) / (Km + A)) buffer: 100 mM Tris/HCl, 50 mM KCl, 20 mM MgCl2, 5 mM sodium phosphoenolpyruvate, 10 units/ml lactic acid dehydrogenase (Type II rabbit muscle), 10 units/ml pyruvate kinase (Type III rabbit muscle), 0.2 mM NADH
PH: 8.2
Temperature: 37
uniprot:P48637 [glutathione synthase(Enzyme) mutant His-tagged R283C]

Glycine + L_gamma_Glutamyl_L_alpha_aminobutyrate + ATP -> ADP + gamma_L_Glutamyl_L_alpha_aminobutyryl_glycine + Phosphate		 (( (Vmax * A) ) / (Km + A)) buffer: 100 mM Tris/HCl, 50 mM KCl, 20 mM MgCl2, 5 mM sodium phosphoenolpyruvate, 10 units/ml lactic acid dehydrogenase (Type II rabbit muscle), 10 units/ml pyruvate kinase (Type III rabbit muscle), 0.2 mM NADH
PH: 8.2
Temperature: 37
uniprot:P48637 [glutathione synthase(Enzyme) mutant His-tagged D219G]

Glycine + ATP + L_gamma_Glutamyl_L_alpha_aminobutyrate -> gamma_L_Glutamyl_L_alpha_aminobutyryl_glycine + Phosphate + ADP		 (( (Vmax * A) ) / (Km + A)) buffer: 100 mM Tris/HCl, 50 mM KCl, 20 mM MgCl2, 5 mM sodium phosphoenolpyruvate, 10 units/ml lactic acid dehydrogenase (Type II rabbit muscle), 10 units/ml pyruvate kinase (Type III rabbit muscle), 0.2 mM NADH
PH: 8.2
Temperature: 37
uniprot:P48637 [glutathione synthase(Enzyme) wildtype His-tagged]

L_gamma_Glutamyl_L_alpha_aminobutyrate + ATP + Glycine -> ADP + Phosphate + gamma_L_Glutamyl_L_alpha_aminobutyryl_glycine		 (( (Vmax * A) ) / (Km + A)) buffer: 100 mM Tris/HCl, 50 mM KCl, 20 mM MgCl2, 5 mM sodium phosphoenolpyruvate, 10 units/ml lactic acid dehydrogenase (Type II rabbit muscle), 10 units/ml pyruvate kinase (Type III rabbit muscle), 0.2 mM NADH
PH: 8.2
Temperature: 37
uniprot:P48637 [glutathione synthase(Enzyme) mutant His-tagged Y270H]

Glycine + L_gamma_Glutamyl_L_alpha_aminobutyrate + ATP -> ADP + gamma_L_Glutamyl_L_alpha_aminobutyryl_glycine + Phosphate		 (( (Vmax * A) ) / (Km + A)) buffer: 100 mM Tris/HCl, 50 mM KCl, 20 mM MgCl2, 5 mM sodium phosphoenolpyruvate, 10 units/ml lactic acid dehydrogenase (Type II rabbit muscle), 10 units/ml pyruvate kinase (Type III rabbit muscle), 0.2 mM NADH
PH: 8.2
Temperature: 37
uniprot:P48637 [glutathione synthase(Enzyme) mutant His-tagged L188P]

Glycine + L_gamma_Glutamyl_L_alpha_aminobutyrate + ATP -> gamma_L_Glutamyl_L_alpha_aminobutyryl_glycine + Phosphate + ADP		 (( (Vmax * A) ) / (Km + A)) buffer: 100 mM Tris/HCl, 50 mM KCl, 20 mM MgCl2, 5 mM sodium phosphoenolpyruvate, 10 units/ml lactic acid dehydrogenase (Type II rabbit muscle), 10 units/ml pyruvate kinase (Type III rabbit muscle), 0.2 mM NADH
PH: 8.2
Temperature: 37
uniprot:P48637 [glutathione synthase(Enzyme) mutant His-tagged D219G]

Glycine + ATP + L_gamma_Glutamyl_L_alpha_aminobutyrate -> gamma_L_Glutamyl_L_alpha_aminobutyryl_glycine + Phosphate + ADP		 (( (Vmax * A) ) / (Km + A)) buffer: 100 mM Tris/HCl, 50 mM KCl, 20 mM MgCl2, 5 mM sodium phosphoenolpyruvate, 10 units/ml lactic acid dehydrogenase (Type II rabbit muscle), 10 units/ml pyruvate kinase (Type III rabbit muscle), 0.2 mM NADH
PH: 8.2
Temperature: 37
uniprot:P48637 [glutathione synthase(Enzyme) mutant His-tagged P314L]

L_gamma_Glutamyl_L_alpha_aminobutyrate + ATP + Glycine -> Phosphate + gamma_L_Glutamyl_L_alpha_aminobutyryl_glycine + ADP		 (( (Vmax * A) ) / (Km + A)) buffer: 100 mM Tris/HCl, 50 mM KCl, 20 mM MgCl2, 5 mM sodium phosphoenolpyruvate, 10 units/ml lactic acid dehydrogenase (Type II rabbit muscle), 10 units/ml pyruvate kinase (Type III rabbit muscle), 0.2 mM NADH
PH: 8.2
Temperature: 37
uniprot:P48637 [glutathione synthase(Enzyme) mutant His-tagged D219A]

L_gamma_Glutamyl_L_alpha_aminobutyrate + ATP + Glycine -> ADP + Phosphate + gamma_L_Glutamyl_L_alpha_aminobutyryl_glycine		 (( (Vmax * A) ) / (Km + A)) buffer: 100 mM Tris/HCl, 50 mM KCl, 20 mM MgCl2, 5 mM sodium phosphoenolpyruvate, 10 units/ml lactic acid dehydrogenase (Type II rabbit muscle), 10 units/ml pyruvate kinase (Type III rabbit muscle), 0.2 mM NADH
PH: 8.2
Temperature: 37
uniprot:P48637 [glutathione synthase(Enzyme) mutant His-tagged P314L]

Glycine + L_gamma_Glutamyl_L_alpha_aminobutyrate + ATP -> gamma_L_Glutamyl_L_alpha_aminobutyryl_glycine + ADP + Phosphate		 (( (Vmax * A) ) / (Km + A)) buffer: 100 mM Tris/HCl, 50 mM KCl, 20 mM MgCl2, 5 mM sodium phosphoenolpyruvate, 10 units/ml lactic acid dehydrogenase (Type II rabbit muscle), 10 units/ml pyruvate kinase (Type III rabbit muscle), 0.2 mM NADH
PH: 8.2
Temperature: 37
uniprot:P48637 [glutathione synthase(Enzyme) mutant His-tagged R283C]

ATP + L_gamma_Glutamyl_L_alpha_aminobutyrate + Glycine -> ADP + Phosphate + gamma_L_Glutamyl_L_alpha_aminobutyryl_glycine		 (( (Vmax * A) ) / (Km + A)) buffer: 100 mM Tris/HCl, 50 mM KCl, 20 mM MgCl2, 5 mM sodium phosphoenolpyruvate, 10 units/ml lactic acid dehydrogenase (Type II rabbit muscle), 10 units/ml pyruvate kinase (Type III rabbit muscle), 0.2 mM NADH
PH: 8.2
Temperature: 37
uniprot:P48637 [glutathione synthase(Enzyme) mutant His-tagged Y270C]

Glycine + L_gamma_Glutamyl_L_alpha_aminobutyrate + ATP -> Phosphate + ADP + gamma_L_Glutamyl_L_alpha_aminobutyryl_glycine		 (( (Vmax * A) ) / (Km + A)) buffer: 100 mM Tris/HCl, 50 mM KCl, 20 mM MgCl2, 5 mM sodium phosphoenolpyruvate, 10 units/ml lactic acid dehydrogenase (Type II rabbit muscle), 10 units/ml pyruvate kinase (Type III rabbit muscle), 0.2 mM NADH
PH: 8.2
Temperature: 37
uniprot:P48637 [glutathione synthase(Enzyme) wildtype His-tagged]

ATP + Glycine + L_gamma_Glutamyl_L_alpha_aminobutyrate -> gamma_L_Glutamyl_L_alpha_aminobutyryl_glycine + Phosphate + ADP		 (( (Vmax * (( (S / Km1) ) + (( (S ^ 2) ) / (Km2 ^ 2)))) ) / (( (1 + (S / Km1)) ) + (( (S ^ 2) ) / (Km2 ^ 2)))) buffer: 100 mM Tris/HCl, 50 mM KCl, 20 mM MgCl2, 5 mM sodium phosphoenolpyruvate, 10 units/ml lactic acid dehydrogenase (Type II rabbit muscle), 10 units/ml pyruvate kinase (Type III rabbit muscle), 0.2 mM NADH
PH: 8.2
Temperature: 37
uniprot:P48637 [glutathione synthase(Enzyme) mutant His-tagged P314L]

L_gamma_Glutamyl_L_alpha_aminobutyrate + ATP + Glycine -> gamma_L_Glutamyl_L_alpha_aminobutyryl_glycine + ADP + Phosphate		 (( (Vmax * (( (S / Km1) ) + (( (S ^ 2) ) / (Km2 ^ 2)))) ) / (( (1 + (S / Km1)) ) + (( (S ^ 2) ) / (Km2 ^ 2)))) buffer: 100 mM Tris/HCl, 50 mM KCl, 20 mM MgCl2, 5 mM sodium phosphoenolpyruvate, 10 units/ml lactic acid dehydrogenase (Type II rabbit muscle), 10 units/ml pyruvate kinase (Type III rabbit muscle), 0.2 mM NADH
PH: 8.2
Temperature: 37
uniprot:P48637 [glutathione synthase(Enzyme) mutant His-tagged D219A]

Glycine + L_gamma_Glutamyl_L_alpha_aminobutyrate + ATP -> Phosphate + ADP + gamma_L_Glutamyl_L_alpha_aminobutyryl_glycine		 (( (Vmax * (( (S / Km1) ) + (( (S ^ 2) ) / (Km2 ^ 2)))) ) / (( (1 + (S / Km1)) ) + (( (S ^ 2) ) / (Km2 ^ 2)))) buffer: 100 mM Tris/HCl, 50 mM KCl, 20 mM MgCl2, 5 mM sodium phosphoenolpyruvate, 10 units/ml lactic acid dehydrogenase (Type II rabbit muscle), 10 units/ml pyruvate kinase (Type III rabbit muscle), 0.2 mM NADH
PH: 8.2
Temperature: 37
uniprot:P48637 [glutathione synthase(Enzyme) mutant His-tagged D219G]

Glycine + L_gamma_Glutamyl_L_alpha_aminobutyrate + ATP -> gamma_L_Glutamyl_L_alpha_aminobutyryl_glycine + Phosphate + ADP		 (( (Vmax * (( (S / Km1) ) + (( (S ^ 2) ) / (Km2 ^ 2)))) ) / (( (1 + (S / Km1)) ) + (( (S ^ 2) ) / (Km2 ^ 2)))) buffer: 100 mM Tris/HCl, 50 mM KCl, 20 mM MgCl2, 5 mM sodium phosphoenolpyruvate, 10 units/ml lactic acid dehydrogenase (Type II rabbit muscle), 10 units/ml pyruvate kinase (Type III rabbit muscle), 0.2 mM NADH
PH: 8.2
Temperature: 37
uniprot:P48637 [glutathione synthase(Enzyme) mutant His-tagged Y270H]

Glycine + ATP + L_gamma_Glutamyl_L_alpha_aminobutyrate -> gamma_L_Glutamyl_L_alpha_aminobutyryl_glycine + ADP + Phosphate		 (( (Vmax * (( (S / Km1) ) + (( (S ^ 2) ) / (Km2 ^ 2)))) ) / (( (1 + (S / Km1)) ) + (( (S ^ 2) ) / (Km2 ^ 2)))) buffer: 100 mM Tris/HCl, 50 mM KCl, 20 mM MgCl2, 5 mM sodium phosphoenolpyruvate, 10 units/ml lactic acid dehydrogenase (Type II rabbit muscle), 10 units/ml pyruvate kinase (Type III rabbit muscle), 0.2 mM NADH
PH: 8.2
Temperature: 37
uniprot:P48637 [glutathione synthase(Enzyme) mutant His-tagged L188P]

L_gamma_Glutamyl_L_alpha_aminobutyrate + ATP + Glycine -> ADP + Phosphate + gamma_L_Glutamyl_L_alpha_aminobutyryl_glycine		 (( (Vmax * (( (S / Km1) ) + (( (S ^ 2) ) / (Km2 ^ 2)))) ) / (( (1 + (S / Km1)) ) + (( (S ^ 2) ) / (Km2 ^ 2)))) buffer: 100 mM Tris/HCl, 50 mM KCl, 20 mM MgCl2, 5 mM sodium phosphoenolpyruvate, 10 units/ml lactic acid dehydrogenase (Type II rabbit muscle), 10 units/ml pyruvate kinase (Type III rabbit muscle), 0.2 mM NADH
PH: 8.2
Temperature: 37
uniprot:P48637 [glutathione synthase(Enzyme) mutant His-tagged Y270C]

L_gamma_Glutamyl_L_alpha_aminobutyrate + Glycine + ATP -> gamma_L_Glutamyl_L_alpha_aminobutyryl_glycine + ADP + Phosphate		 (( (Vmax * (( (S / Km1) ) + (( (S ^ 2) ) / (Km2 ^ 2)))) ) / (( (1 + (S / Km1)) ) + (( (S ^ 2) ) / (Km2 ^ 2)))) buffer: 100 mM Tris/HCl, 50 mM KCl, 20 mM MgCl2, 5 mM sodium phosphoenolpyruvate, 10 units/ml lactic acid dehydrogenase (Type II rabbit muscle), 10 units/ml pyruvate kinase (Type III rabbit muscle), 0.2 mM NADH
PH: 8.2
Temperature: 37
uniprot:P48637 [glutathione synthase(Enzyme) mutant His-tagged R283C]

Glycine + ATP + L_gamma_Glutamyl_L_alpha_aminobutyrate -> Phosphate + gamma_L_Glutamyl_L_alpha_aminobutyryl_glycine + ADP		 (( (Vmax * (( (S / Km1) ) + (( (S ^ 2) ) / (Km2 ^ 2)))) ) / (( (1 + (S / Km1)) ) + (( (S ^ 2) ) / (Km2 ^ 2)))) buffer: 100 mM Tris/HCl, 50 mM KCl, 20 mM MgCl2, 5 mM sodium phosphoenolpyruvate, 10 units/ml lactic acid dehydrogenase (Type II rabbit muscle), 10 units/ml pyruvate kinase (Type III rabbit muscle), 0.2 mM NADH
PH: 8.2
Temperature: 37

Pathways

pathway id name
BioCyc:ARA_GLUTATHIONESYN-PWY glutathione biosynthesis
BioCyc:ECOO157_PWY-4041 γ-glutamyl cycle
BioCyc:AGRO_GLUTATHIONESYN-PWY glutathione biosynthesis
BioCyc:HUMAN_PWY-4041 γ-glutamyl cycle
BioCyc:HUMAN_GLUTATHIONESYN-PWY glutathione biosynthesis
BioCyc:META_PWY-4041 γ-glutamyl cycle
BioCyc:YEAST_GLUTATHIONESYN-PWY glutathione biosynthesis
BioCyc:ARA_PWY-4041 γ-glutamyl cycle
BioCyc:CAULO_PWY-4041 γ-glutamyl cycle
BioCyc:MOUSE_PWY-4041 γ-glutamyl cycle
BioCyc:SYNEL_GLUTATHIONESYN-PWY glutathione biosynthesis
BioCyc:ECO_GLUTATHIONESYN-PWY glutathione biosynthesis
BioCyc:ARA_PWYQT-4470 γ-glutamyl cycle (plant pathway)
BioCyc:ECOO157_GLUTATHIONESYN-PWY glutathione biosynthesis
BioCyc:ECOL199310_GLUTATHIONESYN-PWY glutathione biosynthesis
BioCyc:CAULO_GLUTATHIONESYN-PWY glutathione biosynthesis
BioCyc:MOUSE_GLUTATHIONESYN-PWY glutathione biosynthesis
BioCyc:META_GLUTATHIONESYN-PWY glutathione biosynthesis
BioCyc:YEAST_PWY-4041 γ-glutamyl cycle
BioCyc:YEAST_PWY3O-114 superpathway of glutathione metabolism (truncated γ-glutamyl cycle)
BioCyc:VCHO_GLUTATHIONESYN-PWY glutathione biosynthesis
BioCyc:ECOL316407_GLUTATHIONESYN-PWY glutathione biosynthesis
PathBank:SMP0000853 Glutathione Metabolism
PathBank:SMP0001941 Glutathione Metabolism II
PathBank:SMP0002032 Glutathione Metabolism III
PlantCyc:ARA_PWYQT-4470 γ-glutamyl cycle (plant pathway)
PlantCyc:ARA_PWY-4041 γ-glutamyl cycle
PlantCyc:ARA_GLUTATHIONESYN-PWY glutathione biosynthesis
PlantCyc:PLANT_PWY-4041 γ-glutamyl cycle
PlantCyc:PLANT_PWYQT-4470 γ-glutamyl cycle (plant pathway)
PlantCyc:PLANT_GLUTATHIONESYN-PWY glutathione biosynthesis
Reactome:R-DDI-211859 Biological oxidations
Reactome:R-HSA-211859 Biological oxidations
Reactome:R-MMU-1430728 Metabolism
Reactome:R-MMU-211859 Biological oxidations
Reactome:R-RNO-156590 Glutathione conjugation
Reactome:R-SPO-1430728 Metabolism
Reactome:R-DDI-174403 Glutathione synthesis and recycling
Reactome:R-HSA-156580 Phase II - Conjugation of compounds
Reactome:R-MMU-156580 Phase II - Conjugation of compounds
Reactome:R-RNO-211859 Biological oxidations
Reactome:R-SCE-1430728 Metabolism
Reactome:R-SCE-174403 Glutathione synthesis and recycling
Reactome:R-SPO-211859 Biological oxidations
Reactome:R-SPO-174403 Glutathione synthesis and recycling
Reactome:R-DDI-156580 Phase II - Conjugation of compounds
Reactome:R-HSA-156590 Glutathione conjugation
Reactome:R-MMU-156590 Glutathione conjugation
Reactome:R-RNO-1430728 Metabolism
Reactome:R-RNO-174403 Glutathione synthesis and recycling
Reactome:R-SCE-156580 Phase II - Conjugation of compounds
Reactome:R-SPO-156580 Phase II - Conjugation of compounds
Reactome:R-DDI-1430728 Metabolism
Reactome:R-DDI-156590 Glutathione conjugation
Reactome:R-HSA-1430728 Metabolism
Reactome:R-HSA-174403 Glutathione synthesis and recycling
Reactome:R-MMU-174403 Glutathione synthesis and recycling
Reactome:R-RNO-156580 Phase II - Conjugation of compounds
Reactome:R-SCE-211859 Biological oxidations
Reactome:R-SCE-156590 Glutathione conjugation
Reactome:R-SPO-156590 Glutathione conjugation
WikiPathways:WP4518 Gamma-glutamyl cycle for the biosynthesis and degradation of glutathione, including diseases
WikiPathways:WP4504 Cysteine and methionine catabolism
PathBank:SMP0120666 4-Hydroxybutyric Aciduria/Succinic Semialdehyde Dehydrogenase Deficiency
PathBank:SMP0120714 Homocarnosinosis
PathBank:SMP0120850 Succinic Semialdehyde Dehydrogenase Deficiency
PathBank:SMP0120480 gamma-Glutamyltransferase Deficiency
PathBank:SMP0120496 Hyperinsulinism-Hyperammonemia Syndrome
PathBank:SMP0120565 5-Oxoprolinase Deficiency
PathBank:SMP0000015 Glutathione Metabolism
PathBank:SMP0000339 Hyperinsulinism-Hyperammonemia Syndrome
PathBank:SMP0000500 5-Oxoprolinase Deficiency
PathBank:SMP0087278 Glutamate Metabolism
PathBank:SMP0120705 Glutathione Synthetase Deficiency
PathBank:SMP0120785 gamma-Glutamyltranspeptidase Deficiency
PathBank:SMP0000385 Homocarnosinosis
PathBank:SMP0000136 2-Hydroxyglutric Aciduria (D and L Form)
PathBank:SMP0000567 Succinic Semialdehyde Dehydrogenase Deficiency
PathBank:SMP0002317 Glutathione Metabolism
PathBank:SMP0087277 Glutathione Metabolism
PathBank:SMP0120700 gamma-Glutamyltransferase Deficiency
PathBank:SMP0120716 Hyperinsulinism-Hyperammonemia Syndrome
PathBank:SMP0120784 5-Oxoprolinase Deficiency
PathBank:SMP0120445 4-Hydroxybutyric Aciduria/Succinic Semialdehyde Dehydrogenase Deficiency
PathBank:SMP0120485 Glutathione Synthetase Deficiency
PathBank:SMP0120566 gamma-Glutamyltranspeptidase Deficiency
PathBank:SMP0000337 Glutathione Synthetase Deficiency
PathBank:SMP0000501 gamma-Glutamyltranspeptidase Deficiency
PathBank:SMP0063590 Glutamate Metabolism
PathBank:SMP0120659 2-Hydroxyglutric Aciduria (D and L Form)
PathBank:SMP0120667 5-Oxoprolinuria
PathBank:SMP0120438 2-Hydroxyglutric Aciduria (D and L Form)
PathBank:SMP0120446 5-Oxoprolinuria
PathBank:SMP0120494 Homocarnosinosis
PathBank:SMP0120631 Succinic Semialdehyde Dehydrogenase Deficiency
PathBank:SMP0000072 Glutamate Metabolism
PathBank:SMP0000243 4-Hydroxybutyric Aciduria/Succinic Semialdehyde Dehydrogenase Deficiency
PathBank:SMP0000143 5-Oxoprolinuria
PathBank:SMP0000183 gamma-Glutamyltransferase Deficiency
PathBank:SMP0063622 Glutathione Metabolism