EC: 2.1.3.3

ornithine carbamoyltransferase (carbamoyl-phosphate:L-ornithine carbamoyltransferase)

enzyme lambda metabolic reaction experiment
uniprot:P00480 [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> Phosphate + L_Citrulline		 (( (Vmax * S) ) / (Km + S)) buffer: *
PH: 7
Temperature: 36
uniprot:P00480 [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> Phosphate + L_Citrulline		 (( (Vmax * S) ) / (Km + S)) buffer: *
PH: 7
Temperature: 36
uniprot:P00480 [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (( (Vmax * S) ) / (Km + S)) buffer: *
PH: 7
Temperature: 36
uniprot:P04391 [Guanidium chloride]

L_Ornithine + Carbamoyl_phosphate -> Phosphate + L_Citrulline		 (( (V * C) ) / (Kr + C)) buffer: 50 mM Tris-acetate
PH: 8.3
Temperature: 25
uniprot:P04391 [Methylguanidine]

Carbamoyl_phosphate + L_Ornithine -> Phosphate + L_Citrulline		 (( (V * C) ) / (Kr + C)) buffer: 50 mM Tris-acetate
PH: 8.3
Temperature: 25
uniprot:P04391 [ornithine carbamoyltransferase(Enzyme) mutant R57G]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (V * C) ) / (Kr + C)) buffer: 50 mM Tris-acetate
PH: 8.3
Temperature: 25
uniprot:P04391 [Guanidinoethanol]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (( (V * C) ) / (Kr + C)) buffer: 50 mM Tris-acetate
PH: 8.3
Temperature: 25
uniprot:P04391 [Butylguanidine]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (( (V * C) ) / (Kr + C)) buffer: 50 mM Tris-acetate
PH: 8.3
Temperature: 25
uniprot:P04391 [Ethylguanidine]

L_Ornithine + Carbamoyl_phosphate -> Phosphate + L_Citrulline		 (( (V * C) ) / (Kr + C)) buffer: 50 mM Tris-acetate
PH: 8.3
Temperature: 25
uniprot:P04391 [Nitroguanidine]

Carbamoyl_phosphate + L_Ornithine -> Phosphate + L_Citrulline		 (( (V * C) ) / (Kr + C)) buffer: 50 mM Tris-acetate
PH: 8.3
Temperature: 25
uniprot:P04391 [1,3-Diaminoguanidine]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (( (V * C) ) / (Kr + C)) buffer: 50 mM Tris-acetate
PH: 8.3
Temperature: 25
uniprot:P04391 [Aminoguanidine]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (V * C) ) / (Kr + C)) buffer: 50 mM Tris-acetate
PH: 8.3
Temperature: 25
uniprot:P04391 [Propylguanidine]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (( (V * C) ) / (Kr + C)) buffer: 50 mM Tris-acetate
PH: 8.3
Temperature: 25
uniprot:P04391 [Guanylurea]

Carbamoyl_phosphate + L_Ornithine -> Phosphate + L_Citrulline		 (( (V * C) ) / (Kr + C)) buffer: 50 mM Tris-acetate
PH: 8.3
Temperature: 25
uniprot:P04391 [Guanidinoethanol]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (( (kcat * E) ) * A) ) / (Km + A)) buffer: 50 mM Tris-acetate
PH: 8.3
Temperature: 25
uniprot:P04391 [Butylguanidine]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (( (( (kcat * E) ) * A) ) / (Km + A)) buffer: 50 mM Tris-acetate
PH: 8.3
Temperature: 25
uniprot:P04391 [Methylguanidine]

L_Ornithine + Carbamoyl_phosphate -> Phosphate + L_Citrulline		 (( (( (kcat * E) ) * A) ) / (Km + A)) buffer: 50 mM Tris-acetate
PH: 8.3
Temperature: 25
uniprot:P04391 [Guanidium chloride]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (( (kcat * E) ) * A) ) / (Km + A)) buffer: 50 mM Tris-acetate
PH: 8.3
Temperature: 25
uniprot:P04391 [Ethylguanidine]

L_Ornithine + Carbamoyl_phosphate -> Phosphate + L_Citrulline		 (( (( (kcat * E) ) * A) ) / (Km + A)) buffer: 50 mM Tris-acetate
PH: 8.3
Temperature: 25
uniprot:P04391 [Aminoguanidine]

Carbamoyl_phosphate + L_Ornithine -> Phosphate + L_Citrulline		 (( (( (kcat * E) ) * A) ) / (Km + A)) buffer: 50 mM Tris-acetate
PH: 8.3
Temperature: 25
uniprot:P04391 [Nitroguanidine]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (( (kcat * E) ) * A) ) / (Km + A)) buffer: 50 mM Tris-acetate
PH: 8.3
Temperature: 25
uniprot:P04391 [Propylguanidine]

Carbamoyl_phosphate + L_Ornithine -> Phosphate + L_Citrulline		 (( (( (kcat * E) ) * A) ) / (Km + A)) buffer: 50 mM Tris-acetate
PH: 8.3
Temperature: 25
uniprot:P04391 [ornithine carbamoyltransferase(Enzyme) mutant R57G]

L_Ornithine + Carbamoyl_phosphate -> Phosphate + L_Citrulline		 (( (( (kcat * E) ) * A) ) / (Km + A)) buffer: 50 mM Tris-acetate
PH: 8.3
Temperature: 25
uniprot:P04391 [ornithine carbamoyltransferase(Enzyme) mutant R57G]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (( (kcat * E) ) * A) ) / (Km + A)) buffer: 50 mM Tris-acetate
PH: 8.3
Temperature: 25
uniprot:P04391 [1,3-Diaminoguanidine]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (( (( (kcat * E) ) * A) ) / (Km + A)) buffer: 50 mM Tris-acetate
PH: 8.3
Temperature: 25
uniprot:P04391 [Guanylurea]

L_Ornithine + Carbamoyl_phosphate -> Phosphate + L_Citrulline		 (( (( (kcat * E) ) * A) ) / (Km + A)) buffer: 50 mM Tris-acetate
PH: 8.3
Temperature: 25
uniprot:P00481 [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> Phosphate + L_Citrulline		 (( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 0.1 M Hepes/NaOH
PH: 7.72
Temperature: 37
uniprot:P00481 [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 0.1 M Hepes/NaOH
PH: 8.28
Temperature: 37
uniprot:P00481 [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> Phosphate + L_Citrulline		 (( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 0.1 M Hepes/NaOH
PH: 7.14
Temperature: 37
uniprot:P00481 [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> Phosphate + L_Citrulline		 (( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 0.1 M Hepes/NaOH
PH: 7.72
Temperature: 37
uniprot:P00481 [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Lysine + Carbamoyl_phosphate -> L_Homocitrulline + Phosphate		 (( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 100 mM Triethanolamine/Acetate
PH: 7.65
Temperature: 37
uniprot:P00481 [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Lysine -> Phosphate + L_Homocitrulline		 (( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 100 mM Triethanolamine/Acetate
PH: 8.78
Temperature: 37
- [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (( (Vmax * A) ) / (Km + A)) buffer: 250 mM Tris/HCl
PH: 8.7
Temperature: 30
- [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (( (Vmax * A) ) / (Km + A)) buffer: 250 mM Tris/HCl
PH: 7.5
Temperature: 30
- [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> Phosphate + L_Citrulline		 (( (Vmax * A) ) / (Km + A)) buffer: 250 mM Tris/HCl
PH: 8
Temperature: 30
- [ornithine carbamoyltransferase(Enzyme) wildtype]

Phosphate + L_Citrulline -> Carbamoyl_phosphate + L_Ornithine		 (( (Vmax * A) ) / (Km + A)) buffer: 0.6 M imidazol/HCl, 20 mM KH2PO4/K2HPO4, 5 U/ml Carbamate kinase from streptococcus faecalis
PH: 6.8
Temperature: 30
- [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (Vmax * A) ) / (Km + A)) buffer: 250 mM Tris/HCl
PH: 8
Temperature: 30
- [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (( (Vmax * A) ) / (Km + A)) buffer: 250 mM Tris/HCl
PH: 8
Temperature: 30
- [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> Phosphate + L_Citrulline		 (( (Vmax * A) ) / (Km + A)) buffer: 250 mM Tris/HCl
PH: 8
Temperature: 30
- [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (( (( (Vmax * A) ) * B) ) / (( (( (( (Kia * Kb) ) + (Ka * B)) ) + (Kb * A)) ) + (A * B))) buffer: 50 mM TAPS/NaOH
PH: 8.5
Temperature: 37
- [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (( (( (Vmax * A) ) * B) ) / (( (( (( (Kia * Kb) ) + (Ka * B)) ) + (Kb * A)) ) + (A * B))) buffer: 50 mM TAPS/NaOH
PH: 8.5
Temperature: 37
- [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (1 / (( (( (( (( (( (( (( (( (Kia * Kb) ) / (( (V * A) ) * B)) ) + (Kb / (V * B))) ) + (Ka / (V * A))) ) + (( (( (Kia * Kb) ) * P) ) / (( (( (V * A) ) * B) ) * Kip))) ) + (( (( (Kia * Kb) ) * Q) ) / (( (( (V * A) ) * B) ) * Kiq))) ) + (( (( (( (Kia * Kb) ) / (( (V * A) ) * B)) ) * (P * Q)) ) / (Kiq * Kp))) ) + (( (( (Ka / (V * A)) ) * Q) ) / Kiq)) ) + (1 / V))) buffer: 100 mM Phosphate
PH: 6.8
Temperature: 37
uniprot:P11727 [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (1 / (( (( (( (( (( (( (( (( (Kia * Kb) ) / (( (V * A) ) * B)) ) + (Kb / (V * B))) ) + (Ka / (V * A))) ) + (( (( (Kia * Kb) ) * P) ) / (( (( (V * A) ) * B) ) * Kip))) ) + (( (( (Kia * Kb) ) * Q) ) / (( (( (V * A) ) * B) ) * Kiq))) ) + (( (( (( (Kia * Kb) ) / (( (V * A) ) * B)) ) * (P * Q)) ) / (Kiq * Kp))) ) + (( (( (Ka / (V * A)) ) * Q) ) / Kiq)) ) + (1 / V))) buffer: 50 mM Phosphate
PH: 6.8
Temperature: 30
uniprot:P11727 [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_arsenate -> L_Citrulline + Arsenate		 (1 / (( (( (( (( (( (( (( (( (Kia * Kb) ) / (( (V * A) ) * B)) ) + (Kb / (V * B))) ) + (Ka / (V * A))) ) + (( (( (Kia * Kb) ) * P) ) / (( (( (V * A) ) * B) ) * Kip))) ) + (( (( (Kia * Kb) ) * Q) ) / (( (( (V * A) ) * B) ) * Kiq))) ) + (( (( (( (Kia * Kb) ) / (( (V * A) ) * B)) ) * (P * Q)) ) / (Kiq * Kp))) ) + (( (( (Ka / (V * A)) ) * Q) ) / Kiq)) ) + (1 / V))) buffer: Arsenate
PH: 6.8
Temperature: 30
- [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_arsenate + L_Ornithine -> Arsenate + L_Citrulline		 (1 / (( (( (( (( (( (( (( (( (Kia * Kb) ) / (( (V * A) ) * B)) ) + (Kb / (V * B))) ) + (Ka / (V * A))) ) + (( (( (Kia * Kb) ) * P) ) / (( (( (V * A) ) * B) ) * Kip))) ) + (( (( (Kia * Kb) ) * Q) ) / (( (( (V * A) ) * B) ) * Kiq))) ) + (( (( (( (Kia * Kb) ) / (( (V * A) ) * B)) ) * (P * Q)) ) / (Kiq * Kp))) ) + (( (( (Ka / (V * A)) ) * Q) ) / Kiq)) ) + (1 / V))) buffer: Arsenate
PH: 6.8
Temperature: 37
- [Pyridoxal phosphate]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 0.051 M Diethanol amine, 0.1 M Mes, 0.051 N-Ethyl morpholine
PH: 7.8
Temperature: 37
- [Pyridoxal phosphate]

L_Ornithine + Carbamoyl_phosphate -> Phosphate + L_Citrulline		 (( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 0.051 M Diethanol amine, 0.1 M Mes, 0.051 N-Ethyl morpholine
PH: 7.8
Temperature: 37
- [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 0.051 M Diethanol amine, 0.1 M Mes, 0.051 N-Ethyl morpholine
PH: 7.8
Temperature: 37
- [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 0.051 M Diethanol amine, 0.1 M Mes, 0.051 N-Ethyl morpholine
PH: 7.8
Temperature: 37
uniprot:P00480 [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> Phosphate + L_Citrulline		 (( (Vmax * A) ) / (Km + A)) buffer: 200 mM Triethanolamine-HCl
PH: 7.7
Temperature: 37
uniprot:P00480 [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (( (Vmax * A) ) / (Km + A)) buffer: 200 mM Triethanolamine-HCl
PH: 7.7
Temperature: 37
uniprot:Q839Q5 [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> Phosphate + L_Citrulline		 (( (( (Vmax * A) ) * B) ) / (( (( (A * B) ) + (KmB * A)) ) + (KmA * B))) buffer: 0.01 M Maleate, 0.1 M NaCl
PH: 6
Temperature: 15
uniprot:Q839Q5 [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (( (Vmax * A) ) * B) ) / (( (( (A * B) ) + (KmB * A)) ) + (KmA * B))) buffer: 0.01 M Tris, 0.1 M NaCl
PH: 7
Temperature: 37
uniprot:Q839Q5 [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> Phosphate + L_Citrulline		 (( (( (Vmax * A) ) * B) ) / (( (( (A * B) ) + (KmB * A)) ) + (KmA * B))) buffer: 0.01 M Tris, 0.1 M NaCl
PH: 7
Temperature: 15
uniprot:Q839Q5 [2-Amino-5-hydroxyvaleric acid]

L_Ornithine + Carbamoyl_phosphate -> Phosphate + L_Citrulline		 (( (( (Vmax * A) ) * B) ) / (( (( (A * B) ) + (( (A * KmB) ) * (1 + (I / Ki)))) ) + (KmA * B))) buffer: 0.01 M Tris, 0.1 M NaCl
PH: 8
Temperature: 37
uniprot:Q839Q5 [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (( (Vmax * A) ) * B) ) / (( (( (A * B) ) + (KmB * A)) ) + (KmA * B))) buffer: 0.01 M Tris, 0.1 M NaCl
PH: 8.4
Temperature: 15
uniprot:Q839Q5 [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> Phosphate + L_Citrulline		 (( (( (Vmax * A) ) * B) ) / (( (( (A * B) ) + (KmB * A)) ) + (KmA * B))) buffer: 0.01 M Tris, 0.1 M NaCl
PH: 7.5
Temperature: 15
uniprot:Q839Q5 [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (( (Vmax * A) ) * B) ) / (( (( (A * B) ) + (KmB * A)) ) + (KmA * B))) buffer: 0.01 M Tris, 0.1 M NaCl
PH: 8
Temperature: 15
uniprot:Q839Q5 [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (( (Vmax * A) ) * B) ) / (( (( (A * B) ) + (KmB * A)) ) + (KmA * B))) buffer: 0.01 M Tris, 0.1 M NaCl
PH: 8
Temperature: 37
uniprot:P96134 [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (( (Vmax * A) ) / (Km_app + A)) buffer: 200 mM Tris/HCl
PH: 7
Temperature: 55
uniprot:P96134 [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> Phosphate + L_Citrulline		 (( (Vmax * A) ) / (Km_app + A)) buffer: 200 mM Tris/HCl
PH: 7
Temperature: 55
- [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> Phosphate + L_Citrulline		 (( (kcat * E) ) / (( (( (1 + (Km_A / A)) ) + (Km_B / B)) ) + (( (Kia * Km_B) ) / (A * B)))) buffer: 0.1 M tetramethylammonium chloride, 20 mM triethanolamine-HCl
PH: 7.12
Temperature: 25
- [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (( (kcat * E) ) / (( (( (1 + (Km_A / A)) ) + (Km_B / B)) ) + (( (Kia * Km_B) ) / (A * B)))) buffer: 0.1 M tetramethylammonium chloride, 20 mM diethanolamine-HCl
PH: 8.41
Temperature: 25
- [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> Phosphate + L_Citrulline		 (( (kcat * E) ) / (( (( (1 + (Km_A / A)) ) + (Km_B / B)) ) + (( (Kia * Km_B) ) / (A * B)))) buffer: 0.1 M tetramethylammonium chloride, 20 mM tetramethylammonium cacodylate
PH: 6.56
Temperature: 25
- [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (( (kcat * E) ) / (( (( (1 + (Km_A / A)) ) + (Km_B / B)) ) + (( (Kia * Km_B) ) / (A * B)))) buffer: 0.1 M tetramethylammonium chloride, 20 mM triethanolamine-HCl
PH: 7.9
Temperature: 25
- [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> Phosphate + L_Citrulline		 (( (kcat * E) ) / (( (( (1 + (Km_A / A)) ) + (Km_B / B)) ) + (( (Kia * Km_B) ) / (A * B)))) buffer: 0.1 M tetramethylammonium chloride, 20 mM triethanolamine-HCl
PH: 7.37
Temperature: 25
- [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (kcat * E) ) / (( (( (1 + (Km_A / A)) ) + (Km_B / B)) ) + (( (Kia * Km_B) ) / (A * B)))) buffer: 0.1 M tetramethylammonium chloride, 20 mM diethanolamine-HCl
PH: 8.8
Temperature: 25
- [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Citrulline + Phosphate -> Carbamoyl_phosphate + L_Ornithine		 (( (kcat * E) ) / (( (( (1 + (Km_A / A)) ) + (Km_B / B)) ) + (( (Kia * Km_B) ) / (A * B)))) buffer: 0.1 M tetramethylammonium chloride, 20 mM triethanolamine-HCl
PH: 7.12
Temperature: 25
- [ornithine carbamoyltransferase(Enzyme) wildtype]

Phosphate + L_Citrulline -> L_Ornithine + Carbamoyl_phosphate		 (( (kcat * E) ) / (( (( (1 + (Km_A / A)) ) + (Km_B / B)) ) + (( (Kia * Km_B) ) / (A * B)))) buffer: 0.1 M tetramethylammonium chloride, 20 mM tetramethylammonium cacodylate
PH: 6.56
Temperature: 25
- [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Citrulline + Phosphate -> Carbamoyl_phosphate + L_Ornithine		 (( (kcat * E) ) / (( (( (1 + (Km_A / A)) ) + (Km_B / B)) ) + (( (Kia * Km_B) ) / (A * B)))) buffer: 0.1 M tetramethylammonium chloride, 20 mM diethanolamine-HCl
PH: 8.8
Temperature: 25
- [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Citrulline + Phosphate -> Carbamoyl_phosphate + L_Ornithine		 (( (kcat * E) ) / (( (( (1 + (Km_A / A)) ) + (Km_B / B)) ) + (( (Kia * Km_B) ) / (A * B)))) buffer: 0.1 M tetramethylammonium chloride, 20 mM triethanolamine-HCl
PH: 7.66
Temperature: 25
- [ornithine carbamoyltransferase(Enzyme) wildtype]

Phosphate + L_Citrulline -> L_Ornithine + Carbamoyl_phosphate		 (( (kcat * E) ) / (( (( (1 + (Km_A / A)) ) + (Km_B / B)) ) + (( (Kia * Km_B) ) / (A * B)))) buffer: 0.1 M tetramethylammonium chloride, 20 mM diethanolamine-HCl
PH: 8.41
Temperature: 25
- [ornithine carbamoyltransferase(Enzyme) wildtype]

Phosphate + L_Citrulline -> L_Ornithine + Carbamoyl_phosphate		 (( (kcat * E) ) / (( (( (1 + (Km_A / A)) ) + (Km_B / B)) ) + (( (Kia * Km_B) ) / (A * B)))) buffer: 0.1 M tetramethylammonium chloride, 20 mM triethanolamine-HCl
PH: 7.9
Temperature: 25
uniprot:Q9N1U7 [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 0.1 M tetramethylammonium methylsulfonate, 20 mM imidazole methylsulfonate
PH: 6.75
Temperature: 25
uniprot:Q9N1U7 [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> Phosphate + L_Citrulline		 (( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 0.1 M tetramethylammonium methylsulfonate, 20 mM tetramethylammonium morpholinoethanesulfonic acid
PH: 6.14
Temperature: 25
uniprot:Q9N1U7 [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> Phosphate + L_Citrulline		 (( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 0.1 M tetramethylammonium methylsulfonate, 20 mM diethanolamine methylsulfonate
PH: 8.47
Temperature: 25
uniprot:Q9N1U7 [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 0.1 M tetramethylammonium methylsulfonate, 20 mM triethanolamine methylsulfonate
PH: 7.88
Temperature: 25
uniprot:Q9N1U7 [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> Phosphate + L_Citrulline		 (( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 0.1 M tetramethylammonium methylsulfonate, 20 mM diethanolamine methylsulfonate
PH: 8.9
Temperature: 25
uniprot:Q9N1U7 [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 0.1 M tetramethylammonium methylsulfonate, 20 mM imidazole methylsulfonate
PH: 7.1
Temperature: 25
- [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> Phosphate + L_Citrulline		 (( (kcat * E) ) / (( (( (( (1 + (B / Kib)) ) + (Km_A / A)) ) + (Km_B / B)) ) + (( (Kia * Km_B) ) / (A * B)))) buffer: 0.1 M tetramethylammonium chloride, 20 mM triethanolamine-HCl
PH: 7.13
Temperature: 25
- [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (kcat * E) ) / (( (( (( (1 + (B / Kib)) ) + (Km_A / A)) ) + (Km_B / B)) ) + (( (Kia * Km_B) ) / (A * B)))) buffer: 0.1 M tetramethylammonium chloride, 20 mM triethanolamine-HCl
PH: 7.9
Temperature: 25
- [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (( (kcat * E) ) / (( (( (( (1 + (B / Kib)) ) + (Km_A / A)) ) + (Km_B / B)) ) + (( (Kia * Km_B) ) / (A * B)))) buffer: 0.1 M tetramethylammonium chloride, 20 mM triethanolamine-HCl
PH: 7.37
Temperature: 25
- [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (( (kcat * E) ) / (( (( (( (1 + (B / Kib)) ) + (Km_A / A)) ) + (Km_B / B)) ) + (( (Kia * Km_B) ) / (A * B)))) buffer: 0.1 M tetramethylammonium chloride, 20 mM triethanolamine-HCl
PH: 7.9
Temperature: 25
- [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (kcat * E) ) / (( (( (( (1 + (B / Kib)) ) + (Km_A / A)) ) + (Km_B / B)) ) + (( (Kia * Km_B) ) / (A * B)))) buffer: 0.1 M tetramethylammonium chloride, 20 mM diethanolamine-HCl
PH: 8.98
Temperature: 25
- [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (kcat * E) ) / (( (( (( (1 + (B / Kib)) ) + (Km_A / A)) ) + (Km_B / B)) ) + (( (Kia * Km_B) ) / (A * B)))) buffer: 0.1 M tetramethylammonium chloride, 20 mM diethanolamine-HCl
PH: 8.5
Temperature: 25
- [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (kcat * E) ) / (( (( (( (1 + (B / Kib)) ) + (Km_A / A)) ) + (Km_B / B)) ) + (( (Kia * Km_B) ) / (A * B)))) buffer: 0.1 M tetramethylammonium chloride, 20 mM diethanolamine-HCl
PH: 8.5
Temperature: 25
- [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> Phosphate + L_Citrulline		 (( (kcat * E) ) / (( (( (( (1 + (B / Kib)) ) + (Km_A / A)) ) + (Km_B / B)) ) + (( (Kia * Km_B) ) / (A * B)))) buffer: 0.1 M tetramethylammonium chloride, 20 mM diethanolamine-HCl
PH: 8.98
Temperature: 25
uniprot:Q9N1U7 [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> Phosphate + L_Citrulline		 (( (( (E * kcat) ) * B) ) / (Km + B)) buffer: 0.1 M tetramethylammonium methylsulfonate, 20 mM triethanolamine methylsulfonate
PH: 7.9
Temperature: 25
uniprot:Q9N1U7 [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> Phosphate + L_Citrulline		 (( (( (E * kcat) ) * B) ) / (Km + B)) buffer: 0.1 M tetramethylammonium methylsulfonate, 20 mM diethanolamine methylsulfonate
PH: 8.47
Temperature: 25
uniprot:Q9N1U7 [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> Phosphate + L_Citrulline		 (( (( (E * kcat) ) * B) ) / (Km + B)) buffer: 0.1 M tetramethylammonium methylsulfonate, 20 mM triethanolamine methylsulfonate
PH: 7.9
Temperature: 25
uniprot:Q9N1U7 [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (( (( (E * kcat) ) * B) ) / (Km + B)) buffer: 0.1 M tetramethylammonium methylsulfonate, 20 mM diethanolamine methylsulfonate
PH: 8.95
Temperature: 25
uniprot:Q9N1U7 [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> Phosphate + L_Citrulline		 (( (( (E * kcat) ) * B) ) / (Km + B)) buffer: 0.1 M tetramethylammonium methylsulfonate, 20 mM diethanolamine methylsulfonate
PH: 8.95
Temperature: 25
uniprot:Q9N1U7 [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (( (E * kcat) ) * B) ) / (Km + B)) buffer: 0.1 M tetramethylammonium methylsulfonate, 20 mM diethanolamine methylsulfonate
PH: 8.47
Temperature: 25
uniprot:Q9N1U7 [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 0.1 M tetramethylammonium methylsulfonate, 20 mM imidazole methylsulfonate
PH: 6.75
Temperature: 25
uniprot:Q9N1U7 [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (( (E * kcat) ) * B) ) / (Km + B)) buffer: 0.1 M tetramethylammonium methylsulfonate, 20 mM tetramethylammonium morpholinoethanesulfonic acid
PH: 6.18
Temperature: 25
uniprot:Q9N1U7 [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> Phosphate + L_Citrulline		 (( (( (E * kcat) ) * B) ) / (Km + B)) buffer: 0.1 M tetramethylammonium methylsulfonate, 20 mM imidazole methylsulfonate
PH: 7.1
Temperature: 25
uniprot:P00480 [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> Phosphate + L_Citrulline		 (( (Vmax * S) ) / (Km + S)) buffer: 50 mM triethanolamine
PH: 8
Temperature: 37
uniprot:P00480 [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> Phosphate + L_Citrulline		 (( (Vmax * S) ) / (Km + S)) buffer: 50 mM triethanolamine
PH: 8
Temperature: 37
uniprot:P00480 [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (( (Vmax * S) ) / (Km + S)) buffer: 50 mM triethanolamine
PH: 8
Temperature: 37
uniprot:P00480 [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (Vmax * S) ) / (Km + S)) buffer: 50 mM triethanolamine
PH: 8
Temperature: 37
uniprot:P00480 [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> Phosphate + L_Citrulline		 (( (Vmax * S) ) / (Km + S)) buffer: 50 mM triethanolamine
PH: 8
Temperature: 37
uniprot:P00480 [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (Vmax * S) ) / (Km + S)) buffer: 50 mM triethanolamine
PH: 8
Temperature: 37
uniprot:P00480 [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (( (Vmax * S) ) / (Km + S)) buffer: 50 mM triethanolamine
PH: 8
Temperature: 37
uniprot:P00480 [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (Vmax * S) ) / (Km + S)) buffer: 50 mM triethanolamine
PH: 8
Temperature: 37
uniprot:Q837U7 [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (( (Vmax * A) ) / (Km + A)) buffer: 50 mM Tris/HCl
PH: 7
Temperature: 37
uniprot:Q837U7 [ornithine carbamoyltransferase(Enzyme) wildtype]

Carbamoyl_phosphate + L_Ornithine -> L_Citrulline + Phosphate		 (V / (( (( (( (( (( (KiA * KB) ) / A) ) * B) ) + (KA / A)) ) + (KB / B)) ) + 1)) buffer: 50 mM Tris/HCl
PH: 7
Temperature: 37
uniprot:Q837U7 [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (V / (( (( (( (( (( (KiB * KB) ) / A) ) * B) ) + (KA / A)) ) + (KB / B)) ) + 1)) buffer: 50 mM Tris/HCl
PH: 7
Temperature: 37
- [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> L_Citrulline + Phosphate		 (Vmax / (( (1 + (Kb / B)) ) + (( (( (Ka * Kb) ) / A) ) * B))) buffer: 7.4 mM Tris
PH: 7.7
Temperature: 37
- [ornithine carbamoyltransferase(Enzyme) wildtype]

L_Ornithine + Carbamoyl_phosphate -> Phosphate + L_Citrulline		 (Vmax / (( (1 + (KmA / A)) ) + (KmB / B))) buffer: 7.4 mM Triethanolamine
PH: 7.7
Temperature: 37

Pathways

pathway id name
BioCyc:HUMAN_PWY-4984 urea cycle
BioCyc:META_PWY-5004 superpathway of L-citrulline metabolism
BioCyc:YEAST_CITRULBIO-PWY citrulline biosynthesis
BioCyc:VCHO_PWY-4984 urea cycle
BioCyc:VCHO_ARGSYN-PWY L-arginine biosynthesis I (via L-ornithine)
BioCyc:MTBCDC1551_PWY-7400 L-arginine biosynthesis IV (archaebacteria)
BioCyc:ANTHRA_ARGSYN-PWY L-arginine biosynthesis I (via L-ornithine)
BioCyc:ANTHRA_PWY-4984 urea cycle
BioCyc:MOUSE_PWY-4984 urea cycle
BioCyc:ECOL316407_ARG+POLYAMINE-SYN superpathway of arginine and polyamine biosynthesis
BioCyc:META_PWY-4984 urea cycle
BioCyc:ECO_ARG+POLYAMINE-SYN superpathway of arginine and polyamine biosynthesis
BioCyc:ECO_ARGSYN-PWY L-arginine biosynthesis I (via L-ornithine)
BioCyc:VCHO_ARGDEGRAD-PWY L-arginine degradation V (arginine deiminase pathway)
BioCyc:VCHO_CITRULLINE-DEG-PWY L-citrulline degradation
BioCyc:MTBH37RV_ARGSYNBSUB-PWY L-arginine biosynthesis II (acetyl cycle)
BioCyc:MTBH37RV_CITRULLINE-DEG-PWY L-citrulline degradation
BioCyc:MTBCDC1551_ARGSYN-PWY L-arginine biosynthesis I (via L-ornithine)
BioCyc:MTBCDC1551_CITRULLINE-DEG-PWY L-citrulline degradation
BioCyc:ECOO157_CITRULLINE-DEG-PWY citrulline degradation
BioCyc:ECOO157_PWY-7400 arginine biosynthesis IV (archaebacteria)
BioCyc:ECOL199310_CITRULLINE-DEG-PWY citrulline degradation
BioCyc:ECOL199310_ARGDEGRAD-PWY arginine degradation V (arginine deiminase pathway)
BioCyc:ECOL199310_PWY-7400 arginine biosynthesis IV (archaebacteria)
BioCyc:ECOL199310_ARGSYN-PWY arginine biosynthesis I (via L-ornithine)
BioCyc:CAULO_CITRULLINE-DEG-PWY citrulline degradation
BioCyc:ANTHRA_ARGSYNBSUB-PWY L-arginine biosynthesis II (acetyl cycle)
BioCyc:ANTHRA_CITRULLINE-DEG-PWY L-citrulline degradation
BioCyc:AGRO_ARGSYN-PWY L-arginine biosynthesis I (via L-ornithine)
BioCyc:MOUSE_PWY-4981 proline biosynthesis II (from arginine)
BioCyc:MOUSE_PWY-5004 superpathway of citrulline metabolism
BioCyc:BSUB_CITRULLINE-DEG-PWY L-citrulline degradation
BioCyc:SYNEL_CITRULLINE-DEG-PWY L-citrulline degradation
BioCyc:CORYNE_ARGSYNBSUB-PWY L-arginine biosynthesis II (acetyl cycle)
BioCyc:CORYNE_CITRULLINE-DEG-PWY L-citrulline degradation
BioCyc:META_ARGSYN-PWY L-arginine biosynthesis I (via L-ornithine)
BioCyc:META_PWY-7400 L-arginine biosynthesis IV (archaebacteria)
BioCyc:META_CITRULBIO-PWY L-citrulline biosynthesis
BioCyc:META_CITRULLINE-DEG-PWY L-citrulline degradation
BioCyc:META_ARGDEGRAD-PWY L-arginine degradation V (arginine deiminase pathway)
BioCyc:YEAST_PWY-4984 urea cycle
BioCyc:MTBH37RV_ARGDEGRAD-PWY L-arginine degradation V (arginine deiminase pathway)
BioCyc:MTBCDC1551_ARGDEGRAD-PWY L-arginine degradation V (arginine deiminase pathway)
BioCyc:ECOL199310_ARGSYNBSUB-PWY arginine biosynthesis II (acetyl cycle)
BioCyc:CAULO_ARGSYNBSUB-PWY arginine biosynthesis II (acetyl cycle)
BioCyc:ANTHRA_ARGORNPROST-PWY arginine, ornithine and proline interconversion
BioCyc:AGRO_CITRULLINE-DEG-PWY L-citrulline degradation
BioCyc:MOUSE_ARGININE-SYN4-PWY arginine biosynthesis IV
BioCyc:ECOL316407_ARGSYN-PWY arginine biosynthesis I (via L-ornithine)
BioCyc:CORYNE_ARGSYN-PWY L-arginine biosynthesis I (via L-ornithine)
BioCyc:META_ARG+POLYAMINE-SYN superpathway of arginine and polyamine biosynthesis
BioCyc:YEAST_ARGSYNBSUB-PWY arginine biosynthesis
BioCyc:VCHO_ARGSYNBSUB-PWY L-arginine biosynthesis II (acetyl cycle)
BioCyc:MTBH37RV_ARGSYN-PWY L-arginine biosynthesis I (via L-ornithine)
BioCyc:MTBCDC1551_ARGSYNBSUB-PWY L-arginine biosynthesis II (acetyl cycle)
BioCyc:ECOO157_ARGSYN-PWY arginine biosynthesis I (via L-ornithine)
BioCyc:CAULO_ARGSYN-PWY arginine biosynthesis I
BioCyc:AGRO_PWY-4984 urea cycle
BioCyc:MOUSE_CITRULBIO-PWY citrulline biosynthesis
BioCyc:MOUSE_CITRULLINE-DEG-PWY citrulline degradation
BioCyc:BSUB_ARGSYNBSUB-PWY L-arginine biosynthesis II (acetyl cycle)
BioCyc:SYNEL_PWY-4984 urea cycle
BioCyc:SYNEL_ARGSYNBSUB-PWY L-arginine biosynthesis II (acetyl cycle)
PathBank:SMP0000812 Arginine Metabolism
Reactome:R-GGA-1660598 Metabolism
Reactome:R-MMU-1430728 Metabolism
Reactome:R-SCE-71291 Amino acid and derivative metabolism
Reactome:R-SPO-1430728 Metabolism
Reactome:R-SCE-1430728 Metabolism
Reactome:R-SPO-71291 Amino acid and derivative metabolism
Reactome:R-SPO-70635 Urea cycle
Reactome:R-GGA-372568 Amino acid metabolism
Reactome:R-HSA-71291 Amino acid and derivative metabolism
Reactome:R-MMU-71291 Amino acid and derivative metabolism
Reactome:R-RNO-1430728 Metabolism
Reactome:R-RNO-71291 Amino acid and derivative metabolism
Reactome:R-GGA-187630 Arginine metabolism
Reactome:R-HSA-1430728 Metabolism
Reactome:R-HSA-70635 Urea cycle
Reactome:R-MMU-70635 Urea cycle
Reactome:R-RNO-70635 Urea cycle
Reactome:R-SCE-70635 Urea cycle
WikiPathways:WP4595 Urea cycle and associated pathways
WikiPathways:WP4225 Pyrimidine metabolism and related diseases
WikiPathways:WP497 Urea cycle and metabolism of amino groups
WikiPathways:WP4583 Biomarkers for urea cycle disorders
PathBank:SMP0120456 Argininosuccinic Aciduria
PathBank:SMP0120569 Creatine Deficiency, Guanidinoacetate Methyltransferase Deficiency
PathBank:SMP0000059 Urea Cycle
PathBank:SMP0000020 Arginine and Proline Metabolism
PathBank:SMP0000362 Arginine: Glycine Amidinotransferase Deficiency (AGAT Deficiency)
PathBank:SMP0000188 Guanidinoacetate Methyltransferase Deficiency (GAMT Deficiency)
PathBank:SMP0000001 Citrullinemia Type I
PathBank:SMP0000504 Creatine Deficiency, Guanidinoacetate Methyltransferase Deficiency
PathBank:SMP0002420 Proline Metabolism
PathBank:SMP0063596 Arginine and Proline Metabolism
PathBank:SMP0120455 Argininemia
PathBank:SMP0120499 Hyperprolinemia Type I
PathBank:SMP0120539 Prolinemia Type II
PathBank:SMP0120572 L-Arginine:Glycine Amidinotransferase Deficiency
PathBank:SMP0000207 Prolidase Deficiency (PD)
PathBank:SMP0000208 Prolinemia Type II
PathBank:SMP0000003 Argininosuccinic Aciduria
PathBank:SMP0000507 L-Arginine:Glycine Amidinotransferase Deficiency
PathBank:SMP0002416 Arginine Metabolism
PathBank:SMP0087224 Urea Cycle
PathBank:SMP0120501 Hyperprolinemia Type II
PathBank:SMP0120541 Prolidase Deficiency (PD)
PathBank:SMP0120570 Hyperornithinemia with Gyrate Atrophy (HOGA)
PathBank:SMP0000360 Hyperprolinemia Type II
PathBank:SMP0000363 Ornithine Aminotransferase Deficiency (OAT Deficiency)
PathBank:SMP0000205 Ornithine Transcarbamylase Deficiency (OTC Deficiency)
PathBank:SMP0000505 Hyperornithinemia with Gyrate Atrophy (HOGA)
PathBank:SMP0120454 Arginine: Glycine Amidinotransferase Deficiency (AGAT Deficiency)
PathBank:SMP0120462 Carbamoyl Phosphate Synthetase Deficiency
PathBank:SMP0120466 Citrullinemia Type I
PathBank:SMP0120490 Guanidinoacetate Methyltransferase Deficiency (GAMT Deficiency)
PathBank:SMP0120538 Ornithine Aminotransferase Deficiency (OAT Deficiency)
PathBank:SMP0120542 Ornithine Transcarbamylase Deficiency (OTC Deficiency)
PathBank:SMP0120571 Hyperornithinemia-Hyperammonemia-Homocitrullinuria [HHH-syndrome]
PathBank:SMP0000361 Hyperprolinemia Type I
PathBank:SMP0000357 Argininemia
PathBank:SMP0000002 Carbamoyl Phosphate Synthetase Deficiency
PathBank:SMP0000506 Hyperornithinemia-Hyperammonemia-Homocitrullinuria [HHH-syndrome]
PathBank:SMP0087178 Arginine and Proline Metabolism
PathBank:SMP0063686 Urea Cycle