EC: 1.1.1.35

3-hydroxyacyl-CoA dehydrogenase ((S)-3-hydroxyacyl-CoA:NAD+ oxidoreductase)

enzyme lambda metabolic reaction experiment
uniprot:Q16836 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype]

H+ + NADH + Acetoacetyl_CoA -> NAD+ + (S)_3_Hydroxybutanoyl_CoA
(( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 0.1 M Citrate/phosphate, 0.1 mM Dithiothreitol, 0.1 % Triton-X 100
PH: 5
Temperature: 36
uniprot:Q16836 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype]

H+ + NADH + Acetoacetyl_CoA -> (S)_3_Hydroxybutanoyl_CoA + NAD+
(( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 0.1 M Potassium phosphate, 0.1 mM Dithiothreitol, 0.1 % Triton-X 100
PH: 6
Temperature: 36
uniprot:Q16836 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype]

H+ + Acetoacetyl_CoA + NADH -> NAD+ + (S)_3_Hydroxybutanoyl_CoA
(( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 0.1 M Potassium phosphate, 0.1 mM Dithiothreitol, 0.1 % Triton-X 100
PH: 7
Temperature: 36
uniprot:Q16836 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype]

Acetoacetyl_CoA + H+ + NADH -> (S)_3_Hydroxybutanoyl_CoA + NAD+
(( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 0.1 M Potassium phosphate, 0.1 mM Dithiothreitol, 0.1 % Triton-X 100
PH: 8
Temperature: 36
uniprot:P00348 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype]

H+ + NADH + S_(3_Oxobutyl)_CoA -> NAD+ + 3_Hydroxybutyl_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 0.0125 M sodium pyrophosphate
PH: 7.3
Temperature: 25
uniprot:Q99714 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype]

Acetoacetyl_CoA + NADH + H+ -> (S)_3_Hydroxybutanoyl_CoA + NAD+
(( (( (kcat * E) ) * S2) ) / (Km + S2)) buffer: 0.1 M Potassium phosphate, 0.2 mg/ml BSA
PH: 7
Temperature: 25
uniprot:Q99714 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype]

H+ + Acetoacetyl_CoA + NADH -> NAD+ + (S)_3_Hydroxybutanoyl_CoA
(( (( (kcat * E) ) * S1) ) / (Km + S1)) buffer: 0.1 M Potassium phosphate, 0.2 mg/ml BSA
PH: 7
Temperature: 25
uniprot:Q99714 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype]

NADH + H+ + 3_Oxooctanoyl_CoA -> (S)_3_Hydroxyoctanoyl_CoA + NAD+
(( (( (kcat * E) ) * S1) ) / (Km + S1)) buffer: 0.1 M Potassium phosphate, 0.2 mg/ml BSA
PH: 7
Temperature: 25
uniprot:Q99714 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype]

3_Oxooctanoyl_CoA + H+ + NADH -> NAD+ + (S)_3_Hydroxyoctanoyl_CoA
(( (( (kcat * E) ) * S2) ) / (Km + S2)) buffer: 0.1 M Potassium phosphate, 0.2 mg/ml BSA
PH: 7
Temperature: 25
uniprot:Q99714 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype]

H+ + NADH + 3_Oxopalmitoyl_CoA -> NAD+ + (S)_3_Hydroxyhexadecanoyl_CoA
(( (( (kcat * E) ) * S1) ) / (Km + S1)) buffer: 0.1 M Potassium phosphate, 0.2 mg/ml BSA
PH: 7
Temperature: 25
uniprot:Q99714 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype]

3_Oxopalmitoyl_CoA + NADH + H+ -> NAD+ + (S)_3_Hydroxyhexadecanoyl_CoA
(( (( (kcat * E) ) * S2) ) / (Km + S2)) buffer: 0.1 M Potassium phosphate, 0.2 mg/ml BSA
PH: 7
Temperature: 25
uniprot:Q9WVK7 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype isoenzyme type I]

(S)_3_Hydroxybutanoyl_CoA + NAD+ -> NADH + H+ + Acetoacetyl_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 0.1 M Tris, 0.1 M KCl, 0.22 µg/ml Crotonase
PH: 10.2
Temperature: 30
uniprot:Q9WVK7 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype isoenzyme type I]

NAD+ + (S)_3_Hydroxyhexanoyl_CoA -> NADH + 3_Oxohexanoyl_CoA + H+
(( (Vmax * S) ) / (Km + S)) buffer: 0.1 M Tris, 0.1 M KCl, 0.22 µg/ml Crotonase
PH: 10.2
Temperature: 30
uniprot:Q9WVK7 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype isoenzyme type I]

Acetoacetyl_CoA + NADH + H+ -> (S)_3_Hydroxybutanoyl_CoA + NAD+
(( (Vmax * A) ) / (Km + A)) buffer: 0.1 M Tris, 0.1 M KCl, 0.22 µg/ml Crotonase
PH: 10.2
Temperature: 30
uniprot:P07896 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype isoenzyme type II]

NAD+ + (S)_3_Hydroxybutanoyl_CoA -> NADH + H+ + Acetoacetyl_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 0.1 M Tris, 0.1 M KCl, 0.22 µg/ml Crotonase
PH: 10.2
Temperature: 30
uniprot:Q9WVK7 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype isoenzyme type I]

H+ + Acetoacetyl_CoA + NADH -> (S)_3_Hydroxybutanoyl_CoA + NAD+
(( (Vmax * S) ) / (Km + S)) buffer: 0.1 M Tris, 0.1 M KCl, 0.22 µg/ml Crotonase
PH: 10.2
Temperature: 30
uniprot:Q9WVK7 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype isoenzyme type I]

(S)_3_Hydroxybutanoyl_CoA + NAD+ -> H+ + NADH + Acetoacetyl_CoA
(( (Vmax * A) ) / (Km + A)) buffer: 0.1 M Tris, 0.1 M KCl, 0.22 µg/ml Crotonase
PH: 10.2
Temperature: 30
uniprot:Q9WVK7 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype isoenzyme type I]

(S)_3_Hydroxyoctanoyl_CoA + NAD+ -> H+ + NADH + 3_Oxooctanoyl_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 0.1 M Tris, 0.1 M KCl, 0.22 µg/ml Crotonase
PH: 10.2
Temperature: 30
uniprot:Q9WVK7 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype isoenzyme type I]

NAD+ + (S)_3_Hydroxydecanoyl_CoA -> 3_Oxodecanoyl_CoA + H+ + NADH
(( (Vmax * S) ) / (Km + S)) buffer: 0.1 M Tris, 0.1 M KCl, 0.22 µg/ml Crotonase
PH: 10.2
Temperature: 30
uniprot:Q9WVK7 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype isoenzyme type I]

Acetoacetyl_CoA + H+ + NADPH -> NADP+ + (S)_3_Hydroxybutanoyl_CoA
(( (Vmax * A) ) / (Km + A)) buffer: 0.1 M Tris, 0.1 M KCl, 0.22 µg/ml Crotonase
PH: 10.2
Temperature: 30
uniprot:Q9WVK7 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype isoenzyme type I]

NADP+ + (S)_3_Hydroxybutanoyl_CoA -> H+ + NADPH + Acetoacetyl_CoA
(( (Vmax * A) ) / (Km + A)) buffer: 0.1 M Tris, 0.1 M KCl, 0.22 µg/ml Crotonase
PH: 10.2
Temperature: 30
uniprot:Q9WVK7 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype isoenzyme type I]

H+ + Acetoacetyl_S_pantetheine + NADH -> (S)_3_Hydroxybutanoyl_S_pantetheine + NAD+
(( (Vmax * S) ) / (Km + S)) buffer: 0.1 M Tris, 0.1 M KCl, 0.22 µg/ml Crotonase
PH: 10.2
Temperature: 30
uniprot:P07896 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype isoenzyme type II]

NADH + Acetoacetyl_CoA + H+ -> NAD+ + (S)_3_Hydroxybutanoyl_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 0.1 M Tris, 0.1 M KCl, 0.22 µg/ml Crotonase
PH: 10.2
Temperature: 30
uniprot:P07896 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype isoenzyme type II]

H+ + NADH + Acetoacetyl_CoA -> NAD+ + (S)_3_Hydroxybutanoyl_CoA
(( (Vmax * A) ) / (Km + A)) buffer: 0.1 M Tris, 0.1 M KCl, 0.22 µg/ml Crotonase
PH: 10.2
Temperature: 30
uniprot:P07896 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype isoenzyme type II]

NAD+ + (S)_3_Hydroxybutanoyl_CoA -> Acetoacetyl_CoA + NADH + H+
(( (Vmax * A) ) / (Km + A)) buffer: 0.1 M Tris, 0.1 M KCl, 0.22 µg/ml Crotonase
PH: 10.2
Temperature: 30
uniprot:P07896 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype isoenzyme type II]

NAD+ + (S)_3_Hydroxyoctanoyl_CoA -> 3_Oxooctanoyl_CoA + NADH + H+
(( (Vmax * S) ) / (Km + S)) buffer: 0.1 M Tris, 0.1 M KCl, 0.22 µg/ml Crotonase
PH: 10.2
Temperature: 30
uniprot:P07896 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype isoenzyme type II]

NAD+ + (S)_3_Hydroxyhexanoyl_CoA -> NADH + H+ + 3_Oxohexanoyl_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 0.1 M Tris, 0.1 M KCl, 0.22 µg/ml Crotonase
PH: 10.2
Temperature: 30
uniprot:P07896 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype isoenzyme type II]

NAD+ + (S)_3_Hydroxydecanoyl_CoA -> 3_Oxodecanoyl_CoA + NADH + H+
(( (Vmax * S) ) / (Km + S)) buffer: 0.1 M Tris, 0.1 M KCl, 0.22 µg/ml Crotonase
PH: 10.2
Temperature: 30
uniprot:P21177 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype]

NADH + Acetoacetyl_CoA + H+ -> (S)_3_Hydroxybutanoyl_CoA + NAD+
(( (( (kcat * E) ) * S) ) / (Km + S)) buffer: 0.1 M potassium phosphate, 0.2 mg/ml bovine serum albumin
PH: 7
Temperature: 25
uniprot:P21177 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) mutant G116F]

H+ + NADH + Acetoacetyl_CoA -> (S)_3_Hydroxybutanoyl_CoA + NAD+
(( (( (kcat * E) ) * S) ) / (Km + S)) buffer: 0.1 M potassium phosphate, 0.2 mg/ml bovine serum albumin
PH: 7
Temperature: 25
uniprot:P21177 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) wildtype]

H+ + NADH + Acetoacetyl_CoA -> (S)_3_Hydroxybutanoyl_CoA + NAD+
(( (( (kcat * E) ) * S) ) / (Km + S)) buffer: 0.1 M potassium phosphate, 0.2 mg/ml bovine serum albumin
PH: 7
Temperature: 25
uniprot:P21177 [3-hydroxyacyl-CoA dehydrogenase(Enzyme) mutant G116F]

H+ + NADH + Acetoacetyl_CoA -> NAD+ + (S)_3_Hydroxybutanoyl_CoA
(( (( (kcat * E) ) * S) ) / (Km + S)) buffer: 0.1 M potassium phosphate, 0.2 mg/ml bovine serum albumin
PH: 7
Temperature: 25

Pathways

pathway id name
BioCyc:HUMAN_ILEUDEG-PWY isoleucine degradation
BioCyc:META_FAO-PWY fatty acid β-oxidation I
BioCyc:META_PWY-5137 fatty acid β-oxidation III (unsaturated, odd number)
BioCyc:META_ILEUDEG-PWY L-isoleucine degradation I
BioCyc:ECO_FAO-PWY fatty acid β-oxidation I
BioCyc:ECO_PWY0-1337 oleate β-oxidation
BioCyc:ARA_LYSINE-DEG2-PWY lysine degradation II
BioCyc:ECOO157_VALDEG-PWY valine degradation I
BioCyc:ECOL199310_PWY-5137 fatty acid β-oxidation III (unsaturated, odd number)
BioCyc:MOUSE_PWY-5137 fatty acid β-oxidation III (unsaturated, odd number)
BioCyc:MOUSE_PWY-5138 fatty acid β-oxidation IV (unsaturated, even number)
BioCyc:BSUB_FAO-PWY fatty acid β-oxidation I
BioCyc:ECOL316407_FAO-PWY fatty acid β-oxidation I
BioCyc:META_PWY-7726 (4Z,7Z,10Z,13Z,16Z)-docosapentaenoate biosynthesis (6-desaturase)
BioCyc:META_PWY-5138 unsaturated, even numbered fatty acid β-oxidation
BioCyc:ARA_PWY-5138 unsaturated, even numbered fatty acid β-oxidation
BioCyc:VCHO_FAO-PWY fatty acid β-oxidation I
BioCyc:VCHO_PWY-5137 fatty acid β-oxidation III (unsaturated, odd number)
BioCyc:ECOO157_PWY-5137 fatty acid β-oxidation III (unsaturated, odd number)
BioCyc:MOUSE_PWY3DJ-0 isoleucine degradation
BioCyc:BSUB_VALDEG-PWY L-valine degradation I
BioCyc:HUMAN_PWY-5137 fatty acid β-oxidation (unsaturated, odd number)
BioCyc:META_PWY-7007 methyl ketone biosynthesis (engineered)
BioCyc:META_PWY-7948 4-oxopentanoate degradation
BioCyc:META_PWY-735 jasmonic acid biosynthesis
BioCyc:ARA_PWY-5136 fatty acid β-oxidation II (peroxisome)
BioCyc:VCHO_VALDEG-PWY L-valine degradation I
BioCyc:ECOO157_GLUCONEO-PWY gluconeogenesis I
BioCyc:ECOO157_FAO-PWY fatty acid β-oxidation I
BioCyc:ECOL199310_FAO-PWY fatty acid β-oxidation I
BioCyc:MOUSE_PWY-5109 2-methylbutyrate biosynthesis
BioCyc:MOUSE_VALDEG-PWY valine degradation I
BioCyc:BSUB_ILEUDEG-PWY L-isoleucine degradation I
BioCyc:HUMAN_FAO-PWY fatty acid β-oxidation
BioCyc:HUMAN_PWY66-391 fatty acid β-oxidation (peroxisome)
BioCyc:META_PWY-561 superpathway of glyoxylate cycle and fatty acid degradation
BioCyc:META_PWY-5136 fatty acid β-oxidation II (peroxisome)
BioCyc:META_PWY66-391 fatty acid β-oxidation VI (peroxisome)
BioCyc:META_PWY0-1337 oleate β-oxidation
BioCyc:META_PWY-7606 docosahexaenoate biosynthesis III (6-desaturase, mammals)
BioCyc:MOUSE_FAO-PWY fatty acid β-oxidation I
BioCyc:MOUSE_PWY-5136 fatty acid β-oxidation II (core pathway)
BioCyc:MOUSE_PWY3DJ-86 valine degradation
WikiPathways:WP2472 Escherichia coli K-12 peripherome
PathBank:SMP0000781 Fatty Acid Oxidation
PathBank:SMP0001033 fatty acid oxidation (Butanoate)
PathBank:SMP0001034 fatty acid oxidation (Decanoate)
PathBank:SMP0001035 fatty acid oxidation (hexanoate)
PathBank:SMP0001036 Fatty Acid Oxidation (Laurate)
PathBank:SMP0001037 fatty acid oxidation (myristate)
PathBank:SMP0001038 fatty acid oxidation (octanoate)
PathBank:SMP0001039 fatty acid oxidation (palmitate)
PathBank:SMP0001040 fatty acid oxidation (steareate)
PathBank:SMP0002039 Oleic Acid Oxidation
Plant Reactome:R-OSA-2744345 Metabolism and regulation
Plant Reactome:R-OSA-2744343 Amino acid metabolism
Plant Reactome:R-OSA-5655122 Amino acid biosynthesis
Plant Reactome:R-OSA-1119445 Beta-alanine biosynthesis II
PlantCyc:ARA_LYSINE-DEG2-PWY lysine degradation II
PlantCyc:PLANT_PWY-5136 fatty acid β-oxidation II (peroxisome)
PlantCyc:PLANT_PWY-5138 unsaturated, even numbered fatty acid β-oxidation
PlantCyc:ARA_PWY-5138 unsaturated, even numbered fatty acid β-oxidation
PlantCyc:ARA_PWY-561 superpathway of glyoxylate cycle and fatty acid degradation
PlantCyc:ARA_PWY-5136 fatty acid β-oxidation II (peroxisome)
PlantCyc:PLANT_LYSINE-DEG2-PWY lysine degradation II
PlantCyc:PLANT_PWY-561 superpathway of glyoxylate cycle and fatty acid degradation
Reactome:R-BTA-1430728 Metabolism
Reactome:R-BTA-71291 Amino acid and derivative metabolism
Reactome:R-CEL-77286 mitochondrial fatty acid beta-oxidation of saturated fatty acids
Reactome:R-CEL-77346 Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA
Reactome:R-DRE-8978868 Fatty acid metabolism
Reactome:R-HSA-77286 mitochondrial fatty acid beta-oxidation of saturated fatty acids
Reactome:R-HSA-77346 Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA
Reactome:R-HSA-70895 Branched-chain amino acid catabolism
Reactome:R-HSA-72306 tRNA processing
Reactome:R-HSA-6785470 tRNA processing in the mitochondrion
Reactome:R-MMU-1430728 Metabolism
Reactome:R-MMU-556833 Metabolism of lipids
Reactome:R-MMU-77286 mitochondrial fatty acid beta-oxidation of saturated fatty acids
Reactome:R-MMU-77346 Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA
Reactome:R-MMU-70895 Branched-chain amino acid catabolism
Reactome:R-RNO-8978868 Fatty acid metabolism
Reactome:R-RNO-77289 Mitochondrial Fatty Acid Beta-Oxidation
Reactome:R-RNO-77310 Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA
Reactome:R-RNO-77352 Beta oxidation of butanoyl-CoA to acetyl-CoA
Reactome:R-RNO-70895 Branched-chain amino acid catabolism
Reactome:R-SSC-77350 Beta oxidation of hexanoyl-CoA to butanoyl-CoA
Reactome:R-BTA-70895 Branched-chain amino acid catabolism
Reactome:R-CEL-556833 Metabolism of lipids
Reactome:R-CEL-77289 Mitochondrial Fatty Acid Beta-Oxidation
Reactome:R-CEL-77310 Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA
Reactome:R-CEL-77352 Beta oxidation of butanoyl-CoA to acetyl-CoA
Reactome:R-DRE-390918 Peroxisomal lipid metabolism
Reactome:R-DME-1430728 Metabolism
Reactome:R-DME-71291 Amino acid and derivative metabolism
Reactome:R-HSA-556833 Metabolism of lipids
Reactome:R-HSA-8978868 Fatty acid metabolism
Reactome:R-HSA-77289 Mitochondrial Fatty Acid Beta-Oxidation
Reactome:R-HSA-77310 Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA
Reactome:R-HSA-77352 Beta oxidation of butanoyl-CoA to acetyl-CoA
Reactome:R-MMU-8978868 Fatty acid metabolism
Reactome:R-MMU-77289 Mitochondrial Fatty Acid Beta-Oxidation
Reactome:R-MMU-77310 Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA
Reactome:R-MMU-77352 Beta oxidation of butanoyl-CoA to acetyl-CoA
Reactome:R-RNO-77350 Beta oxidation of hexanoyl-CoA to butanoyl-CoA
Reactome:R-RNO-390918 Peroxisomal lipid metabolism
Reactome:R-SSC-1430728 Metabolism
Reactome:R-SSC-556833 Metabolism of lipids
Reactome:R-SSC-77348 Beta oxidation of octanoyl-CoA to hexanoyl-CoA
Reactome:R-CEL-8978868 Fatty acid metabolism
Reactome:R-CEL-77348 Beta oxidation of octanoyl-CoA to hexanoyl-CoA
Reactome:R-DRE-1430728 Metabolism
Reactome:R-DRE-556833 Metabolism of lipids
Reactome:R-HSA-77348 Beta oxidation of octanoyl-CoA to hexanoyl-CoA
Reactome:R-HSA-390247 Beta-oxidation of very long chain fatty acids
Reactome:R-HSA-71291 Amino acid and derivative metabolism
Reactome:R-HSA-8953854 Metabolism of RNA
Reactome:R-HSA-6787450 tRNA modification in the mitochondrion
Reactome:R-MMU-77348 Beta oxidation of octanoyl-CoA to hexanoyl-CoA
Reactome:R-MMU-390247 Beta-oxidation of very long chain fatty acids
Reactome:R-MMU-71291 Amino acid and derivative metabolism
Reactome:R-RNO-1430728 Metabolism
Reactome:R-RNO-556833 Metabolism of lipids
Reactome:R-RNO-77286 mitochondrial fatty acid beta-oxidation of saturated fatty acids
Reactome:R-RNO-77346 Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA
Reactome:R-RNO-71291 Amino acid and derivative metabolism
Reactome:R-SSC-77289 Mitochondrial Fatty Acid Beta-Oxidation
Reactome:R-SSC-77310 Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA
Reactome:R-SSC-77352 Beta oxidation of butanoyl-CoA to acetyl-CoA
Reactome:R-CEL-1430728 Metabolism
Reactome:R-CEL-77350 Beta oxidation of hexanoyl-CoA to butanoyl-CoA
Reactome:R-DRE-390247 Beta-oxidation of very long chain fatty acids
Reactome:R-DME-70895 Branched-chain amino acid catabolism
Reactome:R-HSA-1430728 Metabolism
Reactome:R-HSA-77350 Beta oxidation of hexanoyl-CoA to butanoyl-CoA
Reactome:R-HSA-390918 Peroxisomal lipid metabolism
Reactome:R-HSA-72312 rRNA processing
Reactome:R-HSA-8868766 rRNA processing in the mitochondrion
Reactome:R-MMU-77350 Beta oxidation of hexanoyl-CoA to butanoyl-CoA
Reactome:R-MMU-390918 Peroxisomal lipid metabolism
Reactome:R-RNO-77348 Beta oxidation of octanoyl-CoA to hexanoyl-CoA
Reactome:R-RNO-390247 Beta-oxidation of very long chain fatty acids
Reactome:R-SSC-8978868 Fatty acid metabolism
Reactome:R-SSC-77286 mitochondrial fatty acid beta-oxidation of saturated fatty acids
Reactome:R-SSC-77346 Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA
WikiPathways:WP465 Tryptophan metabolism
WikiPathways:WP5355 Metabolic Epileptic Disorders
WikiPathways:WP4686 Leucine, isoleucine and valine metabolism
WikiPathways:WP2318 Fatty acid oxidation
PathBank:SMP0120746 Saccharopinuria/Hyperlysinemia II
PathBank:SMP0120854 Pyridoxine Dependency with Seizures
PathBank:SMP0120870 2-Aminoadipic 2-Oxoadipic Aciduria
PathBank:SMP0120440 3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency
PathBank:SMP0120444 3-Methylglutaconic Aciduria Type IV
PathBank:SMP0120484 Glutaric Aciduria Type I
PathBank:SMP0120516 Maple Syrup Urine Disease
PathBank:SMP0120589 Isovaleric Acidemia
PathBank:SMP0120593 Hyperlysinemia II or Saccharopinuria
PathBank:SMP0121348 Fatty Acid Oxidation (Hexanoate)
PathBank:SMP0121352 Fatty Acid Oxidation (Palmitate)
PathBank:SMP0122220 Oleic Acid Oxidation
PathBank:SMP0000032 Valine, Leucine, and Isoleucine Degradation
PathBank:SMP0000173 beta-Ketothiolase Deficiency
PathBank:SMP0000199 Maple Syrup Urine Disease
PathBank:SMP0000384 Methylmalonate Semialdehyde Dehydrogenase Deficiency
PathBank:SMP0000239 Saccharopinuria/Hyperlysinemia II
PathBank:SMP0000482 Mitochondrial Beta-Oxidation of Long Chain Saturated Fatty Acids
PathBank:SMP0000141 3-Methylglutaconic Aciduria Type IV
PathBank:SMP0000524 Isovaleric Acidemia
PathBank:SMP0000528 Hyperlysinemia II or Saccharopinuria
PathBank:SMP0000544 Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase Deficiency (LCHAD)
PathBank:SMP0000568 Short-Chain 3-Hydroxyacyl-CoA Dehydrogenase Deficiency (SCHAD)
PathBank:SMP0087358 Mitochondrial Beta-Oxidation of Short Chain Saturated Fatty Acids
PathBank:SMP0063612 Fatty Acid Elongation In Mitochondria
PathBank:SMP0120439 2-Methyl-3-hydroxybutryl-CoA Dehydrogenase Deficiency
PathBank:SMP0120443 3-Methylglutaconic Aciduria Type III
PathBank:SMP0120459 beta-Ketothiolase Deficiency
PathBank:SMP0120503 Isovaleric Aciduria
PathBank:SMP0120523 Methylmalonate Semialdehyde Dehydrogenase Deficiency
PathBank:SMP0120588 Isobutyryl-CoA Dehydrogenase Deficiency
PathBank:SMP0120592 Hyperlysinemia I, Familial
PathBank:SMP0120608 Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase Deficiency (LCHAD)
PathBank:SMP0120632 Short-Chain 3-Hydroxyacyl-CoA Dehydrogenase Deficiency (SCHAD)
PathBank:SMP0121206 Jasmonic Acid Biosynthesis
PathBank:SMP0121347 Fatty Acid Oxidation (Decanoate)
PathBank:SMP0121351 Fatty Acid Oxidation (Octanoate)
PathBank:SMP0000073 Butyrate Metabolism
PathBank:SMP0000054 Fatty Acid Elongation in Mitochondria
PathBank:SMP0000138 3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency
PathBank:SMP0000140 3-Methylglutaconic Aciduria Type III
PathBank:SMP0000238 Isovaleric Aciduria
PathBank:SMP0000186 Glutaric Aciduria Type I
PathBank:SMP0000481 Mitochondrial Beta-Oxidation of Medium Chain Saturated Fatty Acids
PathBank:SMP0000523 Isobutyryl-CoA Dehydrogenase Deficiency
PathBank:SMP0000527 Hyperlysinemia I, Familial
PathBank:SMP0000571 Pyridoxine Dependency with Seizures
PathBank:SMP0087521 Mitochondrial Beta-Oxidation of Medium Chain Saturated Fatty Acids
PathBank:SMP0063603 Butyrate Metabolism
PathBank:SMP0063641 Mitochondrial Beta-Oxidation of Short Chain Saturated Fatty Acids
PathBank:SMP0063689 Valine, Leucine, and Isoleucine Degradation
PathBank:SMP0120704 Glutaric Aciduria Type I
PathBank:SMP0120812 Hyperlysinemia II or Saccharopinuria
PathBank:SMP0120441 3-Methylcrotonyl-CoA Carboxylase Deficiency Type I
PathBank:SMP0120525 Methylmalonic Aciduria
PathBank:SMP0120537 Propionic Acidemia
PathBank:SMP0120586 3-Hydroxyisobutyric Acid Dehydrogenase Deficiency
PathBank:SMP0121261 Fatty Acid Oxidation
PathBank:SMP0121349 Fatty Acid Oxidation (Laurate)
PathBank:SMP0121353 Fatty Acid Oxidation (Steareate)
PathBank:SMP0000137 2-Methyl-3-hydroxybutyryl-CoA Dehydrogenase Deficiency
PathBank:SMP0000237 3-Methylcrotonyl-CoA Carboxylase Deficiency Type I
PathBank:SMP0000200 Methylmalonic Aciduria
PathBank:SMP0000521 3-Hydroxyisobutyric Acid Dehydrogenase Deficiency
PathBank:SMP0000719 2-Aminoadipic 2-Oxoadipic Aciduria
PathBank:SMP0002434 Lysine Metabolism
PathBank:SMP0087300 Lysine Degradation
PathBank:SMP0087360 Mitochondrial Beta-Oxidation of Long Chain Saturated Fatty Acids
PathBank:SMP0012062 Fatty Acid Beta-Oxidation I
PathBank:SMP0063640 Mitochondrial Beta-Oxidation of Medium Chain Saturated Fatty Acids
PathBank:SMP0120651 2-Aminoadipic 2-Oxoadipic Aciduria
PathBank:SMP0120811 Hyperlysinemia I, Familial
PathBank:SMP0120851 Short-Chain 3-Hydroxyacyl-CoA Dehydrogenase Deficiency (SCHAD)
PathBank:SMP0120442 3-Methylglutaconic Aciduria Type I
PathBank:SMP0120526 Saccharopinuria/Hyperlysinemia II
PathBank:SMP0120587 3-Hydroxyisobutyric Aciduria
PathBank:SMP0120635 Pyridoxine Dependency with Seizures
PathBank:SMP0121350 Fatty Acid Oxidation (Myristate)
PathBank:SMP0122226 L-Carnitine Degradation I
PathBank:SMP0000037 Lysine Degradation
PathBank:SMP0000236 Propionic Acidemia
PathBank:SMP0000139 3-Methylglutaconic Aciduria Type I
PathBank:SMP0000480 Mitochondrial Beta-Oxidation of Short Chain Saturated Fatty Acids
PathBank:SMP0000522 3-Hydroxyisobutyric Aciduria
PathBank:SMP0000635 Valproic Acid Metabolism Pathway
PathBank:SMP0087287 Butyrate Metabolism
PathBank:SMP0087359 Mitochondrial Beta-Oxidation of Medium Chain Saturated Fatty Acids
PathBank:SMP0087519 Mitochondrial Beta-Oxidation of Short Chain Saturated Fatty Acids
PathBank:SMP0087523 Mitochondrial Beta-Oxidation of Long Chain Saturated Fatty Acids
PathBank:SMP0063635 Lysine Degradation
PathBank:SMP0063639 Mitochondrial Beta-Oxidation of Long Chain Saturated Fatty Acids