Hydantoin-5-propionate
Hydantoin-5-propionic acid is a metabolite of histidine, urinary hydantoin-5-propionic acid occur in patients with disorders of folate/ vitamin B12 metabolism (PMID: 3760095). Folic acid non-dependent excessive formiminoglutamic aciduria (Figlu-uria) is an extremely rare disorder; treatment with oral folate supplements (15 mg/day) for 3 weeks failed to reduce urinary hydantoin-5-propionic acid (PMID: 8487495).
| ID | EC Number | Name |
|---|---|---|
| KEGG:R00069 | 1.14.13.- | 4-imidazolone-5-propanoate:oxygen oxidoreductase |
| KEGG:R04875 | C05565 + C00001<=>C05829 |