phhA, PAH

K00500 phhA, PAH; phenylalanine-4-hydroxylase [EC:1.14.16.1]

Protein Function: phenylalanine-4-hydroxylase [EC:1.14.16.1]

DBLinks
Proteins
protein id name function taxonomy source
Reactions
reaction id name note
KEGG:R01795 L-phenylalanine,tetrahydrobiopterin:oxygen oxidoreductase (4-hydroxylating) two-step reaction (see R07211+R04734)
KEGG:R07211 L-phenylalanine,tetrahydrobiopterin:oxygen oxidoreductase(4-hydroxylating) L-Phenylalanine + Tetrahydrobiopterin + Oxygen <=> L-Tyrosine + 4a-Hydroxytetrahydrobiopterin
KEGG:R12540 L-phenylalanine,tetrahydropteridine:oxygen oxidoreductase (4-hydroxylating) L-Phenylalanine + Tetrahydropteridine + Oxygen <=> L-Tyrosine + 4a-Hydroxy-5,6,7,8-tetrahydropteridine
Rhea:RHEA:20274 (6R)-L-erythro-5,6,7,8-tetrahydrobiopterin + L-phenylalanine + O2 => (4aS,6R)-4a-hydroxy-L-erythro-5,6,7,8-tetrahydrobiopterin + L-tyrosine
Rhea:RHEA:20275 (4aS,6R)-4a-hydroxy-L-erythro-5,6,7,8-tetrahydrobiopterin + L-tyrosine => (6R)-L-erythro-5,6,7,8-tetrahydrobiopterin + L-phenylalanine + O2
Rhea:RHEA:20276 (6R)-L-erythro-5,6,7,8-tetrahydrobiopterin + L-phenylalanine + O2 <=> (4aS,6R)-4a-hydroxy-L-erythro-5,6,7,8-tetrahydrobiopterin + L-tyrosine
BioCyc:RXN66-569 PHE + OXYGEN-MOLECULE + 5678-TETRAHYDROPTERIDINE --> TYR + 4a-Hydroxytetrahydroopteridines
BioCyc:RXN-13907 PHE + FORMYL-THF-GLU-N + OXYGEN-MOLECULE --> CPD-14931 + TYR