Pathways Knowlegdes
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| Pathway | DOIs | Note |
|---|---|---|
| Valine, leucine and isoleucine degradation Accession ID: WikiPathways:WP1451 |
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| 3-Methylcrotonyl-CoA Carboxylase Deficiency Type I Accession ID: PathBank:SMP0120662 |
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| 3-Hydroxyisobutyric Aciduria Accession ID: PathBank:SMP0120806 |
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| 3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency Accession ID: PathBank:SMP0120440 |
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| 3-Methylglutaconic Aciduria Type IV Accession ID: PathBank:SMP0120444 |
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| Maple Syrup Urine Disease Accession ID: PathBank:SMP0120516 |
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| Isovaleric Acidemia Accession ID: PathBank:SMP0120589 |
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| Valine, Leucine, and Isoleucine Degradation Accession ID: PathBank:SMP0000032 |
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| beta-Ketothiolase Deficiency Accession ID: PathBank:SMP0000173 |
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| Maple Syrup Urine Disease Accession ID: PathBank:SMP0000199 |
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| Methylmalonate Semialdehyde Dehydrogenase Deficiency Accession ID: PathBank:SMP0000384 |
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| 3-Methylglutaconic Aciduria Type IV Accession ID: PathBank:SMP0000141 |
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| Isovaleric Acidemia Accession ID: PathBank:SMP0000524 |
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| Valine, Leucine, and Isoleucine Degradation Accession ID: PathBank:SMP0087234 |
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| 3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency Accession ID: PathBank:SMP0120661 |
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| 3-Methylglutaconic Aciduria Type IV Accession ID: PathBank:SMP0120665 |
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| Methylmalonic Aciduria Accession ID: PathBank:SMP0120745 |
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| Propionic Acidemia Accession ID: PathBank:SMP0120757 |
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| 3-Hydroxyisobutyric Acid Dehydrogenase Deficiency Accession ID: PathBank:SMP0120805 |
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| 2-Methyl-3-hydroxybutryl-CoA Dehydrogenase Deficiency Accession ID: PathBank:SMP0120439 |
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