EC: 4.2.1.17

enoyl-CoA hydratase ((3S)-3-hydroxyacyl-CoA hydro-lyase)

enzyme lambda metabolic reaction experiment
uniprot:P96807 [enoyl-CoA hydratase(Enzyme) wildtype]

Crotonoyl_CoA + H2O -> 3_Hydroxybutanoyl_CoA
(( (( (E * kcat) ) * S) ) / (Km + S)) buffer: 50 mM Tris
PH: 8
Temperature: 30
uniprot:P96807 [enoyl-CoA hydratase(Enzyme) mutant D40N]

Crotonoyl_CoA + H2O -> 3_Hydroxybutanoyl_CoA
(( (( (E * kcat) ) * S) ) / (Km + S)) buffer: 50 mM Tris
PH: 8
Temperature: 30
uniprot:Q58DM8 [enoyl-CoA hydratase(Enzyme) wildtype]

trans_Hexadec_2_enoyl_CoA + H2O -> (S)_3_Hydroxyhexadecanoyl_CoA
(( (Vmax * A) ) / (Km + A)) buffer: 0.033 M Tris-HCl, 5E-7 M potassium EDTA, 5E-7 M egg albumin
PH: 7.5
Temperature: 25
uniprot:Q58DM8 [enoyl-CoA hydratase(Enzyme) wildtype]

H2O + trans_Dec_2_enoyl_CoA -> (S)_3_Hydroxydecanoyl_CoA
(( (Vmax * A) ) / (Km + A)) buffer: 0.033 M Tris-HCl, 5E-7 M potassium EDTA, 5E-7 M egg albumin
PH: 7.5
Temperature: 25
uniprot:Q58DM8 [enoyl-CoA hydratase(Enzyme) wildtype]

H2O + trans_Tetradec_2_enoyl_CoA -> (S)_3_Hydroxytetradecanoyl_CoA
(( (Vmax * A) ) / (Km + A)) buffer: 0.033 M Tris-HCl, 5E-7 M potassium EDTA, 5E-7 M egg albumin
PH: 7.5
Temperature: 25
uniprot:Q58DM8 [enoyl-CoA hydratase(Enzyme) wildtype]

H2O + 2_trans_Dodecenoyl_CoA -> (S)_3_Hydroxydodecanoyl_CoA
(( (Vmax * A) ) / (Km + A)) buffer: 0.033 M Tris-HCl, 5E-7 M potassium EDTA, 5E-7 M egg albumin
PH: 7.5
Temperature: 25
uniprot:Q08426 [enoyl-CoA hydratase(Enzyme) wildtype]

H2O + Crotonoyl_CoA -> (S)_3_Hydroxybutanoyl_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 50 mM Potassium phosphate, 2 mM Mercaptoethanol.
PH: 7.5
Temperature: 30
uniprot:P40939 [enoyl-CoA hydratase(Enzyme) wildtype]

trans_Hex_2_enoyl_CoA + H2O -> (S)_3_Hydroxyhexanoyl_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 50 mM Potassium phosphate, 2 mM Mercaptoethanol.
PH: 7.5
Temperature: 30
uniprot:P40939 [enoyl-CoA hydratase(Enzyme) wildtype]

H2O + trans_Oct_2_enoyl_CoA -> (S)_3_Hydroxyoctanoyl_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 50 mM Potassium phosphate, 2 mM Mercaptoethanol.
PH: 7.5
Temperature: 30
uniprot:Q08426 [enoyl-CoA hydratase(Enzyme) wildtype]

H2O + trans_Hex_2_enoyl_CoA -> (S)_3_Hydroxyhexanoyl_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 50 mM Potassium phosphate, 2 mM Mercaptoethanol.
PH: 7.5
Temperature: 30
uniprot:Q08426 [enoyl-CoA hydratase(Enzyme) wildtype]

H2O + trans_Oct_2_enoyl_CoA -> (S)_3_Hydroxyoctanoyl_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 50 mM Potassium phosphate, 2 mM Mercaptoethanol.
PH: 7.5
Temperature: 30
uniprot:Q58DM8 [enoyl-CoA hydratase(Enzyme) wildtype]

Crotonoyl_CoA + H2O -> (S)_3_Hydroxybutanoyl_CoA
(( (Vmax * A) ) / (Km + A)) buffer: 0.033 M Tris-HCl, 5E-7 M potassium EDTA, 5E-7 M egg albumin
PH: 7.5
Temperature: 25
uniprot:Q58DM8 [enoyl-CoA hydratase(Enzyme) wildtype]

trans_Hex_2_enoyl_CoA + H2O -> (S)_3_Hydroxyhexanoyl_CoA
(( (Vmax * A) ) / (Km + A)) buffer: 0.033 M Tris-HCl, 5E-7 M potassium EDTA, 5E-7 M egg albumin
PH: 7.5
Temperature: 25
uniprot:Q58DM8 [enoyl-CoA hydratase(Enzyme) wildtype]

trans_Oct_2_enoyl_CoA + H2O -> (S)_3_Hydroxyoctanoyl_CoA
(( (Vmax * A) ) / (Km + A)) buffer: 0.033 M Tris-HCl, 5E-7 M potassium EDTA, 5E-7 M egg albumin
PH: 7.5
Temperature: 25
uniprot:P30084 [enoyl-CoA hydratase(Enzyme) wildtype]

H2O + Crotonoyl_CoA -> (S)_3_Hydroxybutanoyl_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 100 mM Potassium phosphate, 1 mg/ml BSA.
PH: 7.5
Temperature: 30
uniprot:P30084 [enoyl-CoA hydratase(Enzyme) wildtype]

trans_Dec_2_enoyl_CoA + H2O -> (S)_3_Hydroxydecanoyl_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 100 mM Potassium phosphate, 1 mg/ml BSA.
PH: 7.5
Temperature: 30
uniprot:P30084 [enoyl-CoA hydratase(Enzyme) wildtype]

trans_Tetradec_2_enoyl_CoA + H2O -> (S)_3_Hydroxytetradecanoyl_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 100 mM Potassium phosphate, 1 mg/ml BSA.
PH: 7.5
Temperature: 30
uniprot:P30084 [enoyl-CoA hydratase(Enzyme) wildtype]

H2O + trans_Hex_2_enoyl_CoA -> (S)_3_Hydroxyhexanoyl_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 100 mM Potassium phosphate, 1 mg/ml BSA.
PH: 7.5
Temperature: 30
uniprot:P30084 [enoyl-CoA hydratase(Enzyme) wildtype]

trans_Oct_2_enoyl_CoA + H2O -> (S)_3_Hydroxyoctanoyl_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 100 mM Potassium phosphate, 1 mg/ml BSA.
PH: 7.5
Temperature: 30
uniprot:P30084 [enoyl-CoA hydratase(Enzyme) wildtype]

2_trans_Dodecenoyl_CoA + H2O -> (S)_3_Hydroxydodecanoyl_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 100 mM Potassium phosphate, 1 mg/ml BSA.
PH: 7.5
Temperature: 30
uniprot:P30084 [enoyl-CoA hydratase(Enzyme) wildtype]

H2O + Crotonoyl_CoA -> 3_Hydroxybutanoyl_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 100 mM potassium phosphate, 0.1 mg/ml bovine serum albumin
PH: 8
Temperature: 25
uniprot:P30084 [enoyl-CoA hydratase(Enzyme) wildtype]

H2O + 2_Methylbut_2_enoyl_CoA -> (2S,3S)_3_Hydroxy_2_methylbutanoyl_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 100 mM potassium phosphate, 0.1 mg/ml bovine serum albumin
PH: 8
Temperature: 25
uniprot:P30084 [enoyl-CoA hydratase(Enzyme) wildtype]

H2O + Acryloyl_CoA -> 3_Hydroxypropanoyl_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 100 mM potassium phosphate, 0.1 mg/ml bovine serum albumin
PH: 8
Temperature: 25
uniprot:P30084 [enoyl-CoA hydratase(Enzyme) wildtype]

H2O + 2_Methylprop_2_enoyl_CoA -> (S)_3_Hydroxyisobutyryl_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 0.1 M Tris-HCl, 1 mM EDTA, 0.1% Triton X-100, 0.1 mM DTNB, 5 U/ml 3-Hydroxyisobutyryl-CoA hydrolase
PH: 8
Temperature: 30
uniprot:P30084 [enoyl-CoA hydratase(Enzyme) wildtype]

3_Methylcrotonyl_CoA + H2O -> 3_Hydroxyisovaleryl_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 100 mM potassium phosphate, 0.1 mg/ml bovine serum albumin
PH: 8
Temperature: 25
uniprot:P23965 [enoyl-CoA hydratase(Enzyme) mutant K242T (His-tagged)]

H2O + trans_Hex_2_enoyl_CoA -> (S)_3_Hydroxyhexanoyl_CoA
(( (( (E * kcat) ) * S) ) / (Km + S)) buffer: 200 mM Potassium phosphate, 0.2 mg/ml BSA
PH: 8
Temperature: 25
uniprot:P23965 [enoyl-CoA hydratase(Enzyme) mutant K242D (His-tagged)]

H2O + trans_Hex_2_enoyl_CoA -> (S)_3_Hydroxyhexanoyl_CoA
(( (( (E * kcat) ) * S) ) / (Km + S)) buffer: 200 mM Potassium phosphate, 0.2 mg/ml BSA
PH: 8
Temperature: 25
uniprot:Q58DM8 [enoyl-CoA hydratase(Enzyme) wildtype (His-tagged)]

H2O + trans_Hex_2_enoyl_CoA -> (S)_3_Hydroxyhexanoyl_CoA
(( (( (E * kcat) ) * S) ) / (Km + S)) buffer: 200 mM Potassium phosphate, 0.2 mg/ml BSA
PH: 8
Temperature: 25
uniprot:P23965 [enoyl-CoA hydratase(Enzyme) mutant K242C (His-tagged)]

H2O + trans_Hex_2_enoyl_CoA -> (S)_3_Hydroxyhexanoyl_CoA
(( (( (E * kcat) ) * S) ) / (Km + S)) buffer: 200 mM Potassium phosphate, 0.2 mg/ml BSA
PH: 8
Temperature: 25
uniprot:Q58DM8 [enoyl-CoA hydratase(Enzyme) wildtype GST-His fused]

Crotonoyl_CoA + H2O -> 3_Hydroxybutanoyl_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 50 mM potassium phosphate, 3 mM EDTA
PH: 7.5
Temperature: 30
uniprot:Q9Y232 [enoyl-CoA hydratase(Enzyme) wildtype GST-His fused]

Crotonoyl_CoA + H2O -> 3_Hydroxybutanoyl_CoA
(( (Vmax * S) ) / (Km + S)) buffer: 50 mM potassium phosphate, 3 mM EDTA
PH: 7.5
Temperature: 30

Pathways

pathway id name
BioCyc:HUMAN_PWY-5177 glutaryl-CoA degradation
BioCyc:HUMAN_ILEUDEG-PWY isoleucine degradation
BioCyc:HUMAN_TRYPTOPHAN-DEGRADATION-1 tryptophan degradation
BioCyc:HUMAN_PWY66-401 superpathway of tryptophan utilization
BioCyc:META_FAO-PWY fatty acid β-oxidation I
BioCyc:META_PWY-5137 fatty acid β-oxidation III (unsaturated, odd number)
BioCyc:META_ILEUDEG-PWY L-isoleucine degradation I
BioCyc:ECO_FAO-PWY fatty acid β-oxidation I
BioCyc:ECO_PWY0-1337 oleate β-oxidation
BioCyc:ECO_PWY0-321 phenylacetate degradation I (aerobic)
BioCyc:ARA_LYSINE-DEG2-PWY lysine degradation II
BioCyc:MTBCDC1551_ILEUDEG-PWY L-isoleucine degradation I
BioCyc:ECOO157_VALDEG-PWY valine degradation I
BioCyc:ECOL199310_PWY-5137 fatty acid β-oxidation III (unsaturated, odd number)
BioCyc:MOUSE_PWY-5137 fatty acid β-oxidation III (unsaturated, odd number)
BioCyc:MOUSE_PWY-5138 fatty acid β-oxidation IV (unsaturated, even number)
BioCyc:BSUB_FAO-PWY fatty acid β-oxidation I
BioCyc:ECOL316407_PWY0-321 phenylacetate degradation I (aerobic)
BioCyc:ECOL316407_FAO-PWY fatty acid β-oxidation I
BioCyc:META_PWY-7726 (4Z,7Z,10Z,13Z,16Z)-docosapentaenoate biosynthesis (6-desaturase)
BioCyc:META_PWY-5138 unsaturated, even numbered fatty acid β-oxidation
BioCyc:META_VALDEG-PWY L-valine degradation I
BioCyc:ARA_PWY-5138 unsaturated, even numbered fatty acid β-oxidation
BioCyc:VCHO_FAO-PWY fatty acid β-oxidation I
BioCyc:VCHO_PWY-5137 fatty acid β-oxidation III (unsaturated, odd number)
BioCyc:MTBH37RV_FAO-PWY fatty acid β-oxidation I
BioCyc:MTBCDC1551_PWY0-321 phenylacetate degradation I (aerobic)
BioCyc:ECOO157_PWY-5137 fatty acid β-oxidation III (unsaturated, odd number)
BioCyc:MOUSE_PWY3DJ-0 isoleucine degradation
BioCyc:BSUB_VALDEG-PWY L-valine degradation I
BioCyc:HUMAN_VALDEG-PWY valine degradation
BioCyc:HUMAN_PWY-5137 fatty acid β-oxidation (unsaturated, odd number)
BioCyc:META_PWY-7007 methyl ketone biosynthesis (engineered)
BioCyc:META_PWY-7948 4-oxopentanoate degradation
BioCyc:META_PWY-7571 ferrichrome A biosynthesis
BioCyc:META_PWY-735 jasmonic acid biosynthesis
BioCyc:ECO_PWY-6071 superpathway of phenylethylamine degradation
BioCyc:ARA_PWY-5136 fatty acid β-oxidation II (peroxisome)
BioCyc:VCHO_VALDEG-PWY L-valine degradation I
BioCyc:MTBH37RV_PWY-6947 superpathway of cholesterol degradation II (cholesterol dehydrogenase)
BioCyc:MTBCDC1551_VALDEG-PWY L-valine degradation I
BioCyc:ECOO157_GLUCONEO-PWY gluconeogenesis I
BioCyc:ECOO157_FAO-PWY fatty acid β-oxidation I
BioCyc:ECOL199310_FAO-PWY fatty acid β-oxidation I
BioCyc:MOUSE_PWY-5109 2-methylbutyrate biosynthesis
BioCyc:MOUSE_VALDEG-PWY valine degradation I
BioCyc:BSUB_ILEUDEG-PWY L-isoleucine degradation I
BioCyc:HUMAN_FAO-PWY fatty acid β-oxidation
BioCyc:HUMAN_PWY66-391 fatty acid β-oxidation (peroxisome)
BioCyc:META_PWY-561 superpathway of glyoxylate cycle and fatty acid degradation
BioCyc:META_PWY-5136 fatty acid β-oxidation II (peroxisome)
BioCyc:META_PWY66-391 fatty acid β-oxidation VI (peroxisome)
BioCyc:META_PWY0-1337 oleate β-oxidation
BioCyc:META_PWY-7606 docosahexaenoate biosynthesis III (6-desaturase, mammals)
BioCyc:MTBH37RV_VALDEG-PWY L-valine degradation I
BioCyc:MTBH37RV_PWY-6944 androstenedione degradation
BioCyc:MTBCDC1551_FAO-PWY fatty acid β-oxidation I
BioCyc:MOUSE_FAO-PWY fatty acid β-oxidation I
BioCyc:MOUSE_PWY-2361 3-oxoadipate degradation
BioCyc:MOUSE_PWY-5136 fatty acid β-oxidation II (core pathway)
BioCyc:MOUSE_PWY3DJ-86 valine degradation
BioCyc:ECOL316407_PWY-6071 superpathway of phenylethylamine degradation
WikiPathways:WP2472 Escherichia coli K-12 peripherome
PathBank:SMP0000781 Fatty Acid Oxidation
PathBank:SMP0001033 fatty acid oxidation (Butanoate)
PathBank:SMP0001034 fatty acid oxidation (Decanoate)
PathBank:SMP0001035 fatty acid oxidation (hexanoate)
PathBank:SMP0001036 Fatty Acid Oxidation (Laurate)
PathBank:SMP0001037 fatty acid oxidation (myristate)
PathBank:SMP0001038 fatty acid oxidation (octanoate)
PathBank:SMP0001039 fatty acid oxidation (palmitate)
PathBank:SMP0001040 fatty acid oxidation (steareate)
PathBank:SMP0002039 Oleic Acid Oxidation
PathBank:SMP0002041 Phenylethylamine Metabolism
Plant Reactome:R-OSA-2744345 Metabolism and regulation
Plant Reactome:R-OSA-2744343 Amino acid metabolism
Plant Reactome:R-OSA-5655122 Amino acid biosynthesis
Plant Reactome:R-OSA-1119445 Beta-alanine biosynthesis II
PlantCyc:ARA_LYSINE-DEG2-PWY lysine degradation II
PlantCyc:PLANT_PWY-5136 fatty acid β-oxidation II (peroxisome)
PlantCyc:PLANT_PWY-5138 unsaturated, even numbered fatty acid β-oxidation
PlantCyc:ARA_PWY-5138 unsaturated, even numbered fatty acid β-oxidation
PlantCyc:ARA_PWY-561 superpathway of glyoxylate cycle and fatty acid degradation
PlantCyc:ARA_PWY-5136 fatty acid β-oxidation II (peroxisome)
PlantCyc:PLANT_LYSINE-DEG2-PWY lysine degradation II
PlantCyc:PLANT_PWY-561 superpathway of glyoxylate cycle and fatty acid degradation
Reactome:R-BTA-1430728 Metabolism
Reactome:R-BTA-556833 Metabolism of lipids
Reactome:R-BTA-77286 mitochondrial fatty acid beta-oxidation of saturated fatty acids
Reactome:R-BTA-77346 Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA
Reactome:R-BTA-71291 Amino acid and derivative metabolism
Reactome:R-CEL-77286 mitochondrial fatty acid beta-oxidation of saturated fatty acids
Reactome:R-CEL-77346 Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA
Reactome:R-CEL-70895 Branched-chain amino acid catabolism
Reactome:R-DRE-8978868 Fatty acid metabolism
Reactome:R-DDI-77289 Mitochondrial Fatty Acid Beta-Oxidation
Reactome:R-DDI-77348 Beta oxidation of octanoyl-CoA to hexanoyl-CoA
Reactome:R-HSA-77286 mitochondrial fatty acid beta-oxidation of saturated fatty acids
Reactome:R-HSA-77346 Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA
Reactome:R-HSA-77288 mitochondrial fatty acid beta-oxidation of unsaturated fatty acids
Reactome:R-HSA-70895 Branched-chain amino acid catabolism
Reactome:R-MMU-1430728 Metabolism
Reactome:R-MMU-556833 Metabolism of lipids
Reactome:R-MMU-77286 mitochondrial fatty acid beta-oxidation of saturated fatty acids
Reactome:R-MMU-77346 Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA
Reactome:R-MMU-70895 Branched-chain amino acid catabolism
Reactome:R-RNO-8978868 Fatty acid metabolism
Reactome:R-RNO-77289 Mitochondrial Fatty Acid Beta-Oxidation
Reactome:R-RNO-77310 Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA
Reactome:R-RNO-77352 Beta oxidation of butanoyl-CoA to acetyl-CoA
Reactome:R-RNO-1482798 Acyl chain remodeling of CL
Reactome:R-RNO-70895 Branched-chain amino acid catabolism
Reactome:R-SSC-77285 Beta oxidation of myristoyl-CoA to lauroyl-CoA
Reactome:R-SSC-77350 Beta oxidation of hexanoyl-CoA to butanoyl-CoA
Reactome:R-SSC-1483206 Glycerophospholipid biosynthesis
Reactome:R-SSC-1482798 Acyl chain remodeling of CL
Reactome:R-BTA-8978868 Fatty acid metabolism
Reactome:R-BTA-77289 Mitochondrial Fatty Acid Beta-Oxidation
Reactome:R-BTA-77310 Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA
Reactome:R-BTA-77352 Beta oxidation of butanoyl-CoA to acetyl-CoA
Reactome:R-BTA-70895 Branched-chain amino acid catabolism
Reactome:R-CEL-556833 Metabolism of lipids
Reactome:R-CEL-77289 Mitochondrial Fatty Acid Beta-Oxidation
Reactome:R-CEL-77310 Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA
Reactome:R-CEL-77352 Beta oxidation of butanoyl-CoA to acetyl-CoA
Reactome:R-DRE-390918 Peroxisomal lipid metabolism
Reactome:R-DDI-8978868 Fatty acid metabolism
Reactome:R-DDI-77346 Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA
Reactome:R-DDI-71291 Amino acid and derivative metabolism
Reactome:R-HSA-556833 Metabolism of lipids
Reactome:R-HSA-8978868 Fatty acid metabolism
Reactome:R-HSA-77289 Mitochondrial Fatty Acid Beta-Oxidation
Reactome:R-HSA-77310 Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA
Reactome:R-HSA-77352 Beta oxidation of butanoyl-CoA to acetyl-CoA
Reactome:R-HSA-1482798 Acyl chain remodeling of CL
Reactome:R-MMU-8978868 Fatty acid metabolism
Reactome:R-MMU-77289 Mitochondrial Fatty Acid Beta-Oxidation
Reactome:R-MMU-77310 Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA
Reactome:R-MMU-77352 Beta oxidation of butanoyl-CoA to acetyl-CoA
Reactome:R-MMU-1482798 Acyl chain remodeling of CL
Reactome:R-RNO-77285 Beta oxidation of myristoyl-CoA to lauroyl-CoA
Reactome:R-RNO-77350 Beta oxidation of hexanoyl-CoA to butanoyl-CoA
Reactome:R-RNO-390918 Peroxisomal lipid metabolism
Reactome:R-RNO-1483206 Glycerophospholipid biosynthesis
Reactome:R-SSC-1430728 Metabolism
Reactome:R-SSC-556833 Metabolism of lipids
Reactome:R-SSC-77305 Beta oxidation of palmitoyl-CoA to myristoyl-CoA
Reactome:R-SSC-77348 Beta oxidation of octanoyl-CoA to hexanoyl-CoA
Reactome:R-SSC-1483257 Phospholipid metabolism
Reactome:R-BTA-77348 Beta oxidation of octanoyl-CoA to hexanoyl-CoA
Reactome:R-CEL-8978868 Fatty acid metabolism
Reactome:R-CEL-77348 Beta oxidation of octanoyl-CoA to hexanoyl-CoA
Reactome:R-CEL-71291 Amino acid and derivative metabolism
Reactome:R-DRE-1430728 Metabolism
Reactome:R-DRE-556833 Metabolism of lipids
Reactome:R-DDI-77286 mitochondrial fatty acid beta-oxidation of saturated fatty acids
Reactome:R-DDI-77350 Beta oxidation of hexanoyl-CoA to butanoyl-CoA
Reactome:R-HSA-77305 Beta oxidation of palmitoyl-CoA to myristoyl-CoA
Reactome:R-HSA-77348 Beta oxidation of octanoyl-CoA to hexanoyl-CoA
Reactome:R-HSA-390247 Beta-oxidation of very long chain fatty acids
Reactome:R-HSA-1483257 Phospholipid metabolism
Reactome:R-HSA-71291 Amino acid and derivative metabolism
Reactome:R-MMU-77305 Beta oxidation of palmitoyl-CoA to myristoyl-CoA
Reactome:R-MMU-77348 Beta oxidation of octanoyl-CoA to hexanoyl-CoA
Reactome:R-MMU-390247 Beta-oxidation of very long chain fatty acids
Reactome:R-MMU-1483257 Phospholipid metabolism
Reactome:R-MMU-71291 Amino acid and derivative metabolism
Reactome:R-RNO-1430728 Metabolism
Reactome:R-RNO-556833 Metabolism of lipids
Reactome:R-RNO-77286 mitochondrial fatty acid beta-oxidation of saturated fatty acids
Reactome:R-RNO-77346 Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA
Reactome:R-RNO-71291 Amino acid and derivative metabolism
Reactome:R-SSC-77289 Mitochondrial Fatty Acid Beta-Oxidation
Reactome:R-SSC-77310 Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA
Reactome:R-BTA-77350 Beta oxidation of hexanoyl-CoA to butanoyl-CoA
Reactome:R-CEL-1430728 Metabolism
Reactome:R-CEL-77350 Beta oxidation of hexanoyl-CoA to butanoyl-CoA
Reactome:R-DRE-390247 Beta-oxidation of very long chain fatty acids
Reactome:R-DDI-1430728 Metabolism
Reactome:R-DDI-556833 Metabolism of lipids
Reactome:R-DDI-77310 Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA
Reactome:R-DDI-77352 Beta oxidation of butanoyl-CoA to acetyl-CoA
Reactome:R-DDI-70895 Branched-chain amino acid catabolism
Reactome:R-HSA-1430728 Metabolism
Reactome:R-HSA-77285 Beta oxidation of myristoyl-CoA to lauroyl-CoA
Reactome:R-HSA-77350 Beta oxidation of hexanoyl-CoA to butanoyl-CoA
Reactome:R-HSA-390918 Peroxisomal lipid metabolism
Reactome:R-HSA-1483206 Glycerophospholipid biosynthesis
Reactome:R-MMU-77285 Beta oxidation of myristoyl-CoA to lauroyl-CoA
Reactome:R-MMU-77350 Beta oxidation of hexanoyl-CoA to butanoyl-CoA
Reactome:R-MMU-390918 Peroxisomal lipid metabolism
Reactome:R-MMU-1483206 Glycerophospholipid biosynthesis
Reactome:R-RNO-77305 Beta oxidation of palmitoyl-CoA to myristoyl-CoA
Reactome:R-RNO-77348 Beta oxidation of octanoyl-CoA to hexanoyl-CoA
Reactome:R-RNO-390247 Beta-oxidation of very long chain fatty acids
Reactome:R-RNO-1483257 Phospholipid metabolism
Reactome:R-SSC-8978868 Fatty acid metabolism
Reactome:R-SSC-77286 mitochondrial fatty acid beta-oxidation of saturated fatty acids
Reactome:R-SSC-77346 Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA
WikiPathways:WP5123 Mitochondrial fatty acid oxidation disorders
WikiPathways:WP5355 Metabolic Epileptic Disorders
WikiPathways:WP4686 Leucine, isoleucine and valine metabolism
WikiPathways:WP2318 Fatty acid oxidation
PathBank:SMP0120662 3-Methylcrotonyl-CoA Carboxylase Deficiency Type I
PathBank:SMP0120734 Malonic Aciduria
PathBank:SMP0120746 Saccharopinuria/Hyperlysinemia II
PathBank:SMP0120786 Malonyl-CoA Decarboxylase Deficiency
PathBank:SMP0120806 3-Hydroxyisobutyric Aciduria
PathBank:SMP0120822 Carnitine Palmitoyl Transferase Deficiency I
PathBank:SMP0120826 Medium Chain Acyl-CoA Dehydrogenase Deficiency (MCAD)
PathBank:SMP0120854 Pyridoxine Dependency with Seizures
PathBank:SMP0120870 2-Aminoadipic 2-Oxoadipic Aciduria
PathBank:SMP0120440 3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency
PathBank:SMP0120444 3-Methylglutaconic Aciduria Type IV
PathBank:SMP0120476 Ethylmalonic Encephalopathy
PathBank:SMP0120484 Glutaric Aciduria Type I
PathBank:SMP0120516 Maple Syrup Urine Disease
PathBank:SMP0120520 Short-Chain Acyl-CoA Dehydrogenase Deficiency (SCAD Deficiency)
PathBank:SMP0120528 Methylmalonic Aciduria Due to Cobalamin-Related Disorders
PathBank:SMP0120589 Isovaleric Acidemia
PathBank:SMP0120593 Hyperlysinemia II or Saccharopinuria
PathBank:SMP0120605 Very-Long-Chain Acyl-CoA Dehydrogenase Deficiency (VLCAD)
PathBank:SMP0120609 Trifunctional Protein Deficiency
PathBank:SMP0121348 Fatty Acid Oxidation (Hexanoate)
PathBank:SMP0121352 Fatty Acid Oxidation (Palmitate)
PathBank:SMP0122220 Oleic Acid Oxidation
PathBank:SMP0000032 Valine, Leucine, and Isoleucine Degradation
PathBank:SMP0000051 Fatty Acid Metabolism
PathBank:SMP0000016 Propanoate Metabolism
PathBank:SMP0000173 beta-Ketothiolase Deficiency
PathBank:SMP0000199 Maple Syrup Urine Disease
PathBank:SMP0000384 Methylmalonate Semialdehyde Dehydrogenase Deficiency
PathBank:SMP0000235 Short-Chain Acyl-CoA Dehydrogenase Deficiency (SCAD Deficiency)
PathBank:SMP0000239 Saccharopinuria/Hyperlysinemia II
PathBank:SMP0000482 Mitochondrial Beta-Oxidation of Long Chain Saturated Fatty Acids
PathBank:SMP0000141 3-Methylglutaconic Aciduria Type IV
PathBank:SMP0000524 Isovaleric Acidemia
PathBank:SMP0000528 Hyperlysinemia II or Saccharopinuria
PathBank:SMP0000540 Very-Long-Chain Acyl-CoA Dehydrogenase Deficiency (VLCAD)
PathBank:SMP0000544 Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase Deficiency (LCHAD)
PathBank:SMP0000568 Short-Chain 3-Hydroxyacyl-CoA Dehydrogenase Deficiency (SCHAD)
PathBank:SMP0002433 Leucine Degradation
PathBank:SMP0087294 Fatty Acid Elongation in Mitochondria
PathBank:SMP0087358 Mitochondrial Beta-Oxidation of Short Chain Saturated Fatty Acids
PathBank:SMP0087430 Fatty Acid Metabolism
PathBank:SMP0063612 Fatty Acid Elongation In Mitochondria
PathBank:SMP0063656 Propanoate Metabolism
PathBank:SMP0120661 3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency
PathBank:SMP0120665 3-Methylglutaconic Aciduria Type IV
PathBank:SMP0120745 Methylmalonic Aciduria
PathBank:SMP0120757 Propionic Acidemia
PathBank:SMP0120805 3-Hydroxyisobutyric Acid Dehydrogenase Deficiency
PathBank:SMP0120825 Carnitine Palmitoyl Transferase Deficiency II
PathBank:SMP0120439 2-Methyl-3-hydroxybutryl-CoA Dehydrogenase Deficiency
PathBank:SMP0120443 3-Methylglutaconic Aciduria Type III
PathBank:SMP0120459 beta-Ketothiolase Deficiency
PathBank:SMP0120503 Isovaleric Aciduria
PathBank:SMP0120523 Methylmalonate Semialdehyde Dehydrogenase Deficiency
PathBank:SMP0120588 Isobutyryl-CoA Dehydrogenase Deficiency
PathBank:SMP0120592 Hyperlysinemia I, Familial
PathBank:SMP0120604 Long Chain Acyl-CoA Dehydrogenase Deficiency (LCAD)
PathBank:SMP0120608 Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase Deficiency (LCHAD)
PathBank:SMP0120632 Short-Chain 3-Hydroxyacyl-CoA Dehydrogenase Deficiency (SCHAD)
PathBank:SMP0121206 Jasmonic Acid Biosynthesis
PathBank:SMP0121347 Fatty Acid Oxidation (Decanoate)
PathBank:SMP0121351 Fatty Acid Oxidation (Octanoate)
PathBank:SMP0000073 Butyrate Metabolism
PathBank:SMP0000054 Fatty Acid Elongation in Mitochondria
PathBank:SMP0000138 3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency
PathBank:SMP0000140 3-Methylglutaconic Aciduria Type III
PathBank:SMP0000238 Isovaleric Aciduria
PathBank:SMP0000185 Glutaric Aciduria Type I
PathBank:SMP0000186 Glutaric Aciduria Type I
PathBank:SMP0000481 Mitochondrial Beta-Oxidation of Medium Chain Saturated Fatty Acids
PathBank:SMP0000201 Methylmalonic Aciduria Due to Cobalamin-Related Disorders
PathBank:SMP0000523 Isobutyryl-CoA Dehydrogenase Deficiency
PathBank:SMP0000527 Hyperlysinemia I, Familial
PathBank:SMP0000539 Long Chain Acyl-CoA Dehydrogenase Deficiency (LCAD)
PathBank:SMP0000571 Pyridoxine Dependency with Seizures
PathBank:SMP0087341 Propanoate Metabolism
PathBank:SMP0087521 Mitochondrial Beta-Oxidation of Medium Chain Saturated Fatty Acids
PathBank:SMP0063603 Butyrate Metabolism
PathBank:SMP0063641 Mitochondrial Beta-Oxidation of Short Chain Saturated Fatty Acids
PathBank:SMP0063689 Valine, Leucine, and Isoleucine Degradation
PathBank:SMP0120660 2-Methyl-3-hydroxybutryl-CoA Dehydrogenase Deficiency
PathBank:SMP0120664 3-Methylglutaconic Aciduria Type III
PathBank:SMP0120696 Ethylmalonic Encephalopathy
PathBank:SMP0120704 Glutaric Aciduria Type I
PathBank:SMP0120736 Maple Syrup Urine Disease
PathBank:SMP0120740 Short-Chain Acyl-CoA Dehydrogenase Deficiency (SCAD Deficiency)
PathBank:SMP0120748 Methylmalonic Aciduria Due to Cobalamin-Related Disorders
PathBank:SMP0120808 Isovaleric Acidemia
PathBank:SMP0120812 Hyperlysinemia II or Saccharopinuria
PathBank:SMP0120824 Very-Long-Chain Acyl-CoA Dehydrogenase Deficiency (VLCAD)
PathBank:SMP0120828 Trifunctional Protein Deficiency
PathBank:SMP0120441 3-Methylcrotonyl-CoA Carboxylase Deficiency Type I
PathBank:SMP0120525 Methylmalonic Aciduria
PathBank:SMP0120537 Propionic Acidemia
PathBank:SMP0120586 3-Hydroxyisobutyric Acid Dehydrogenase Deficiency
PathBank:SMP0120606 Carnitine Palmitoyl Transferase Deficiency II
PathBank:SMP0121261 Fatty Acid Oxidation
PathBank:SMP0121349 Fatty Acid Oxidation (Laurate)
PathBank:SMP0121353 Fatty Acid Oxidation (Steareate)
PathBank:SMP0000137 2-Methyl-3-hydroxybutyryl-CoA Dehydrogenase Deficiency
PathBank:SMP0000237 3-Methylcrotonyl-CoA Carboxylase Deficiency Type I
PathBank:SMP0000200 Methylmalonic Aciduria
PathBank:SMP0000521 3-Hydroxyisobutyric Acid Dehydrogenase Deficiency
PathBank:SMP0000541 Carnitine Palmitoyl Transferase Deficiency II
PathBank:SMP0000545 Trifunctional Protein Deficiency
PathBank:SMP0000719 2-Aminoadipic 2-Oxoadipic Aciduria
PathBank:SMP0002434 Lysine Metabolism
PathBank:SMP0087280 Fatty Acid Metabolism
PathBank:SMP0087300 Lysine Degradation
PathBank:SMP0087360 Mitochondrial Beta-Oxidation of Long Chain Saturated Fatty Acids
PathBank:SMP0087480 Propanoate Metabolism
PathBank:SMP0012062 Fatty Acid Beta-Oxidation I
PathBank:SMP0063640 Mitochondrial Beta-Oxidation of Medium Chain Saturated Fatty Acids
PathBank:SMP0120651 2-Aminoadipic 2-Oxoadipic Aciduria
PathBank:SMP0120663 3-Methylglutaconic Aciduria Type I
PathBank:SMP0120679 beta-Ketothiolase Deficiency
PathBank:SMP0120723 Isovaleric Aciduria
PathBank:SMP0120743 Methylmalonate Semialdehyde Dehydrogenase Deficiency
PathBank:SMP0120807 Isobutyryl-CoA Dehydrogenase Deficiency
PathBank:SMP0120811 Hyperlysinemia I, Familial
PathBank:SMP0120823 Long Chain Acyl-CoA Dehydrogenase Deficiency (LCAD)
PathBank:SMP0120827 Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase Deficiency (LCHAD)
PathBank:SMP0120851 Short-Chain 3-Hydroxyacyl-CoA Dehydrogenase Deficiency (SCHAD)
PathBank:SMP0120442 3-Methylglutaconic Aciduria Type I
PathBank:SMP0120514 Malonic Aciduria
PathBank:SMP0120526 Saccharopinuria/Hyperlysinemia II
PathBank:SMP0120567 Malonyl-CoA Decarboxylase Deficiency
PathBank:SMP0120587 3-Hydroxyisobutyric Aciduria
PathBank:SMP0120603 Carnitine Palmitoyl Transferase Deficiency I
PathBank:SMP0120607 Medium Chain Acyl-CoA Dehydrogenase Deficiency (MCAD)
PathBank:SMP0120635 Pyridoxine Dependency with Seizures
PathBank:SMP0121350 Fatty Acid Oxidation (Myristate)
PathBank:SMP0122226 L-Carnitine Degradation I
PathBank:SMP0000037 Lysine Degradation
PathBank:SMP0000236 Propionic Acidemia
PathBank:SMP0000139 3-Methylglutaconic Aciduria Type I
PathBank:SMP0000181 Ethylmalonic Encephalopathy
PathBank:SMP0000480 Mitochondrial Beta-Oxidation of Short Chain Saturated Fatty Acids
PathBank:SMP0000198 Malonic Aciduria
PathBank:SMP0000502 Malonyl-CoA Decarboxylase Deficiency
PathBank:SMP0000522 3-Hydroxyisobutyric Aciduria
PathBank:SMP0000538 Carnitine Palmitoyl Transferase Deficiency I
PathBank:SMP0000542 Medium Chain Acyl-CoA Dehydrogenase Deficiency (MCAD)
PathBank:SMP0000635 Valproic Acid Metabolism Pathway
PathBank:SMP0087287 Butyrate Metabolism
PathBank:SMP0087327 Valine, Leucine, and Isoleucine Degradation
PathBank:SMP0087359 Mitochondrial Beta-Oxidation of Medium Chain Saturated Fatty Acids
PathBank:SMP0087519 Mitochondrial Beta-Oxidation of Short Chain Saturated Fatty Acids
PathBank:SMP0087523 Mitochondrial Beta-Oxidation of Long Chain Saturated Fatty Acids
PathBank:SMP0063589 Fatty Acid Metabolism
PathBank:SMP0063635 Lysine Degradation
PathBank:SMP0063639 Mitochondrial Beta-Oxidation of Long Chain Saturated Fatty Acids