EC: 4.2.1.17
enoyl-CoA hydratase ((3S)-3-hydroxyacyl-CoA hydro-lyase)
Pathways
| pathway id | name |
|---|---|
| BioCyc:HUMAN_PWY-5177 | glutaryl-CoA degradation |
| BioCyc:HUMAN_ILEUDEG-PWY | isoleucine degradation |
| BioCyc:HUMAN_TRYPTOPHAN-DEGRADATION-1 | tryptophan degradation |
| BioCyc:HUMAN_PWY66-401 | superpathway of tryptophan utilization |
| BioCyc:META_FAO-PWY | fatty acid β-oxidation I |
| BioCyc:META_PWY-5137 | fatty acid β-oxidation III (unsaturated, odd number) |
| BioCyc:META_ILEUDEG-PWY | L-isoleucine degradation I |
| BioCyc:ECO_FAO-PWY | fatty acid β-oxidation I |
| BioCyc:ECO_PWY0-1337 | oleate β-oxidation |
| BioCyc:ECO_PWY0-321 | phenylacetate degradation I (aerobic) |
| BioCyc:ARA_LYSINE-DEG2-PWY | lysine degradation II |
| BioCyc:MTBCDC1551_ILEUDEG-PWY | L-isoleucine degradation I |
| BioCyc:ECOO157_VALDEG-PWY | valine degradation I |
| BioCyc:ECOL199310_PWY-5137 | fatty acid β-oxidation III (unsaturated, odd number) |
| BioCyc:MOUSE_PWY-5137 | fatty acid β-oxidation III (unsaturated, odd number) |
| BioCyc:MOUSE_PWY-5138 | fatty acid β-oxidation IV (unsaturated, even number) |
| BioCyc:BSUB_FAO-PWY | fatty acid β-oxidation I |
| BioCyc:ECOL316407_PWY0-321 | phenylacetate degradation I (aerobic) |
| BioCyc:ECOL316407_FAO-PWY | fatty acid β-oxidation I |
| BioCyc:META_PWY-7726 | (4Z,7Z,10Z,13Z,16Z)-docosapentaenoate biosynthesis (6-desaturase) |
| BioCyc:META_PWY-5138 | unsaturated, even numbered fatty acid β-oxidation |
| BioCyc:META_VALDEG-PWY | L-valine degradation I |
| BioCyc:ARA_PWY-5138 | unsaturated, even numbered fatty acid β-oxidation |
| BioCyc:VCHO_FAO-PWY | fatty acid β-oxidation I |
| BioCyc:VCHO_PWY-5137 | fatty acid β-oxidation III (unsaturated, odd number) |
| BioCyc:MTBH37RV_FAO-PWY | fatty acid β-oxidation I |
| BioCyc:MTBCDC1551_PWY0-321 | phenylacetate degradation I (aerobic) |
| BioCyc:ECOO157_PWY-5137 | fatty acid β-oxidation III (unsaturated, odd number) |
| BioCyc:MOUSE_PWY3DJ-0 | isoleucine degradation |
| BioCyc:BSUB_VALDEG-PWY | L-valine degradation I |
| BioCyc:HUMAN_VALDEG-PWY | valine degradation |
| BioCyc:HUMAN_PWY-5137 | fatty acid β-oxidation (unsaturated, odd number) |
| BioCyc:META_PWY-7007 | methyl ketone biosynthesis (engineered) |
| BioCyc:META_PWY-7948 | 4-oxopentanoate degradation |
| BioCyc:META_PWY-7571 | ferrichrome A biosynthesis |
| BioCyc:META_PWY-735 | jasmonic acid biosynthesis |
| BioCyc:ECO_PWY-6071 | superpathway of phenylethylamine degradation |
| BioCyc:ARA_PWY-5136 | fatty acid β-oxidation II (peroxisome) |
| BioCyc:VCHO_VALDEG-PWY | L-valine degradation I |
| BioCyc:MTBH37RV_PWY-6947 | superpathway of cholesterol degradation II (cholesterol dehydrogenase) |
| BioCyc:MTBCDC1551_VALDEG-PWY | L-valine degradation I |
| BioCyc:ECOO157_GLUCONEO-PWY | gluconeogenesis I |
| BioCyc:ECOO157_FAO-PWY | fatty acid β-oxidation I |
| BioCyc:ECOL199310_FAO-PWY | fatty acid β-oxidation I |
| BioCyc:MOUSE_PWY-5109 | 2-methylbutyrate biosynthesis |
| BioCyc:MOUSE_VALDEG-PWY | valine degradation I |
| BioCyc:BSUB_ILEUDEG-PWY | L-isoleucine degradation I |
| BioCyc:HUMAN_FAO-PWY | fatty acid β-oxidation |
| BioCyc:HUMAN_PWY66-391 | fatty acid β-oxidation (peroxisome) |
| BioCyc:META_PWY-561 | superpathway of glyoxylate cycle and fatty acid degradation |
| BioCyc:META_PWY-5136 | fatty acid β-oxidation II (peroxisome) |
| BioCyc:META_PWY66-391 | fatty acid β-oxidation VI (peroxisome) |
| BioCyc:META_PWY0-1337 | oleate β-oxidation |
| BioCyc:META_PWY-7606 | docosahexaenoate biosynthesis III (6-desaturase, mammals) |
| BioCyc:MTBH37RV_VALDEG-PWY | L-valine degradation I |
| BioCyc:MTBH37RV_PWY-6944 | androstenedione degradation |
| BioCyc:MTBCDC1551_FAO-PWY | fatty acid β-oxidation I |
| BioCyc:MOUSE_FAO-PWY | fatty acid β-oxidation I |
| BioCyc:MOUSE_PWY-2361 | 3-oxoadipate degradation |
| BioCyc:MOUSE_PWY-5136 | fatty acid β-oxidation II (core pathway) |
| BioCyc:MOUSE_PWY3DJ-86 | valine degradation |
| BioCyc:ECOL316407_PWY-6071 | superpathway of phenylethylamine degradation |
| WikiPathways:WP2472 | Escherichia coli K-12 peripherome |
| PathBank:SMP0000781 | Fatty Acid Oxidation |
| PathBank:SMP0001033 | fatty acid oxidation (Butanoate) |
| PathBank:SMP0001034 | fatty acid oxidation (Decanoate) |
| PathBank:SMP0001035 | fatty acid oxidation (hexanoate) |
| PathBank:SMP0001036 | Fatty Acid Oxidation (Laurate) |
| PathBank:SMP0001037 | fatty acid oxidation (myristate) |
| PathBank:SMP0001038 | fatty acid oxidation (octanoate) |
| PathBank:SMP0001039 | fatty acid oxidation (palmitate) |
| PathBank:SMP0001040 | fatty acid oxidation (steareate) |
| PathBank:SMP0002039 | Oleic Acid Oxidation |
| PathBank:SMP0002041 | Phenylethylamine Metabolism |
| Plant Reactome:R-OSA-2744345 | Metabolism and regulation |
| Plant Reactome:R-OSA-2744343 | Amino acid metabolism |
| Plant Reactome:R-OSA-5655122 | Amino acid biosynthesis |
| Plant Reactome:R-OSA-1119445 | Beta-alanine biosynthesis II |
| PlantCyc:ARA_LYSINE-DEG2-PWY | lysine degradation II |
| PlantCyc:PLANT_PWY-5136 | fatty acid β-oxidation II (peroxisome) |
| PlantCyc:PLANT_PWY-5138 | unsaturated, even numbered fatty acid β-oxidation |
| PlantCyc:ARA_PWY-5138 | unsaturated, even numbered fatty acid β-oxidation |
| PlantCyc:ARA_PWY-561 | superpathway of glyoxylate cycle and fatty acid degradation |
| PlantCyc:ARA_PWY-5136 | fatty acid β-oxidation II (peroxisome) |
| PlantCyc:PLANT_LYSINE-DEG2-PWY | lysine degradation II |
| PlantCyc:PLANT_PWY-561 | superpathway of glyoxylate cycle and fatty acid degradation |
| Reactome:R-BTA-1430728 | Metabolism |
| Reactome:R-BTA-556833 | Metabolism of lipids |
| Reactome:R-BTA-77286 | mitochondrial fatty acid beta-oxidation of saturated fatty acids |
| Reactome:R-BTA-77346 | Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA |
| Reactome:R-BTA-71291 | Amino acid and derivative metabolism |
| Reactome:R-CEL-77286 | mitochondrial fatty acid beta-oxidation of saturated fatty acids |
| Reactome:R-CEL-77346 | Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA |
| Reactome:R-CEL-70895 | Branched-chain amino acid catabolism |
| Reactome:R-DRE-8978868 | Fatty acid metabolism |
| Reactome:R-DDI-77289 | Mitochondrial Fatty Acid Beta-Oxidation |
| Reactome:R-DDI-77348 | Beta oxidation of octanoyl-CoA to hexanoyl-CoA |
| Reactome:R-HSA-77286 | mitochondrial fatty acid beta-oxidation of saturated fatty acids |
| Reactome:R-HSA-77346 | Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA |
| Reactome:R-HSA-77288 | mitochondrial fatty acid beta-oxidation of unsaturated fatty acids |
| Reactome:R-HSA-70895 | Branched-chain amino acid catabolism |
| Reactome:R-MMU-1430728 | Metabolism |
| Reactome:R-MMU-556833 | Metabolism of lipids |
| Reactome:R-MMU-77286 | mitochondrial fatty acid beta-oxidation of saturated fatty acids |
| Reactome:R-MMU-77346 | Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA |
| Reactome:R-MMU-70895 | Branched-chain amino acid catabolism |
| Reactome:R-RNO-8978868 | Fatty acid metabolism |
| Reactome:R-RNO-77289 | Mitochondrial Fatty Acid Beta-Oxidation |
| Reactome:R-RNO-77310 | Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA |
| Reactome:R-RNO-77352 | Beta oxidation of butanoyl-CoA to acetyl-CoA |
| Reactome:R-RNO-1482798 | Acyl chain remodeling of CL |
| Reactome:R-RNO-70895 | Branched-chain amino acid catabolism |
| Reactome:R-SSC-77285 | Beta oxidation of myristoyl-CoA to lauroyl-CoA |
| Reactome:R-SSC-77350 | Beta oxidation of hexanoyl-CoA to butanoyl-CoA |
| Reactome:R-SSC-1483206 | Glycerophospholipid biosynthesis |
| Reactome:R-SSC-1482798 | Acyl chain remodeling of CL |
| Reactome:R-BTA-8978868 | Fatty acid metabolism |
| Reactome:R-BTA-77289 | Mitochondrial Fatty Acid Beta-Oxidation |
| Reactome:R-BTA-77310 | Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA |
| Reactome:R-BTA-77352 | Beta oxidation of butanoyl-CoA to acetyl-CoA |
| Reactome:R-BTA-70895 | Branched-chain amino acid catabolism |
| Reactome:R-CEL-556833 | Metabolism of lipids |
| Reactome:R-CEL-77289 | Mitochondrial Fatty Acid Beta-Oxidation |
| Reactome:R-CEL-77310 | Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA |
| Reactome:R-CEL-77352 | Beta oxidation of butanoyl-CoA to acetyl-CoA |
| Reactome:R-DRE-390918 | Peroxisomal lipid metabolism |
| Reactome:R-DDI-8978868 | Fatty acid metabolism |
| Reactome:R-DDI-77346 | Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA |
| Reactome:R-DDI-71291 | Amino acid and derivative metabolism |
| Reactome:R-HSA-556833 | Metabolism of lipids |
| Reactome:R-HSA-8978868 | Fatty acid metabolism |
| Reactome:R-HSA-77289 | Mitochondrial Fatty Acid Beta-Oxidation |
| Reactome:R-HSA-77310 | Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA |
| Reactome:R-HSA-77352 | Beta oxidation of butanoyl-CoA to acetyl-CoA |
| Reactome:R-HSA-1482798 | Acyl chain remodeling of CL |
| Reactome:R-MMU-8978868 | Fatty acid metabolism |
| Reactome:R-MMU-77289 | Mitochondrial Fatty Acid Beta-Oxidation |
| Reactome:R-MMU-77310 | Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA |
| Reactome:R-MMU-77352 | Beta oxidation of butanoyl-CoA to acetyl-CoA |
| Reactome:R-MMU-1482798 | Acyl chain remodeling of CL |
| Reactome:R-RNO-77285 | Beta oxidation of myristoyl-CoA to lauroyl-CoA |
| Reactome:R-RNO-77350 | Beta oxidation of hexanoyl-CoA to butanoyl-CoA |
| Reactome:R-RNO-390918 | Peroxisomal lipid metabolism |
| Reactome:R-RNO-1483206 | Glycerophospholipid biosynthesis |
| Reactome:R-SSC-1430728 | Metabolism |
| Reactome:R-SSC-556833 | Metabolism of lipids |
| Reactome:R-SSC-77305 | Beta oxidation of palmitoyl-CoA to myristoyl-CoA |
| Reactome:R-SSC-77348 | Beta oxidation of octanoyl-CoA to hexanoyl-CoA |
| Reactome:R-SSC-1483257 | Phospholipid metabolism |
| Reactome:R-BTA-77348 | Beta oxidation of octanoyl-CoA to hexanoyl-CoA |
| Reactome:R-CEL-8978868 | Fatty acid metabolism |
| Reactome:R-CEL-77348 | Beta oxidation of octanoyl-CoA to hexanoyl-CoA |
| Reactome:R-CEL-71291 | Amino acid and derivative metabolism |
| Reactome:R-DRE-1430728 | Metabolism |
| Reactome:R-DRE-556833 | Metabolism of lipids |
| Reactome:R-DDI-77286 | mitochondrial fatty acid beta-oxidation of saturated fatty acids |
| Reactome:R-DDI-77350 | Beta oxidation of hexanoyl-CoA to butanoyl-CoA |
| Reactome:R-HSA-77305 | Beta oxidation of palmitoyl-CoA to myristoyl-CoA |
| Reactome:R-HSA-77348 | Beta oxidation of octanoyl-CoA to hexanoyl-CoA |
| Reactome:R-HSA-390247 | Beta-oxidation of very long chain fatty acids |
| Reactome:R-HSA-1483257 | Phospholipid metabolism |
| Reactome:R-HSA-71291 | Amino acid and derivative metabolism |
| Reactome:R-MMU-77305 | Beta oxidation of palmitoyl-CoA to myristoyl-CoA |
| Reactome:R-MMU-77348 | Beta oxidation of octanoyl-CoA to hexanoyl-CoA |
| Reactome:R-MMU-390247 | Beta-oxidation of very long chain fatty acids |
| Reactome:R-MMU-1483257 | Phospholipid metabolism |
| Reactome:R-MMU-71291 | Amino acid and derivative metabolism |
| Reactome:R-RNO-1430728 | Metabolism |
| Reactome:R-RNO-556833 | Metabolism of lipids |
| Reactome:R-RNO-77286 | mitochondrial fatty acid beta-oxidation of saturated fatty acids |
| Reactome:R-RNO-77346 | Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA |
| Reactome:R-RNO-71291 | Amino acid and derivative metabolism |
| Reactome:R-SSC-77289 | Mitochondrial Fatty Acid Beta-Oxidation |
| Reactome:R-SSC-77310 | Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA |
| Reactome:R-BTA-77350 | Beta oxidation of hexanoyl-CoA to butanoyl-CoA |
| Reactome:R-CEL-1430728 | Metabolism |
| Reactome:R-CEL-77350 | Beta oxidation of hexanoyl-CoA to butanoyl-CoA |
| Reactome:R-DRE-390247 | Beta-oxidation of very long chain fatty acids |
| Reactome:R-DDI-1430728 | Metabolism |
| Reactome:R-DDI-556833 | Metabolism of lipids |
| Reactome:R-DDI-77310 | Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA |
| Reactome:R-DDI-77352 | Beta oxidation of butanoyl-CoA to acetyl-CoA |
| Reactome:R-DDI-70895 | Branched-chain amino acid catabolism |
| Reactome:R-HSA-1430728 | Metabolism |
| Reactome:R-HSA-77285 | Beta oxidation of myristoyl-CoA to lauroyl-CoA |
| Reactome:R-HSA-77350 | Beta oxidation of hexanoyl-CoA to butanoyl-CoA |
| Reactome:R-HSA-390918 | Peroxisomal lipid metabolism |
| Reactome:R-HSA-1483206 | Glycerophospholipid biosynthesis |
| Reactome:R-MMU-77285 | Beta oxidation of myristoyl-CoA to lauroyl-CoA |
| Reactome:R-MMU-77350 | Beta oxidation of hexanoyl-CoA to butanoyl-CoA |
| Reactome:R-MMU-390918 | Peroxisomal lipid metabolism |
| Reactome:R-MMU-1483206 | Glycerophospholipid biosynthesis |
| Reactome:R-RNO-77305 | Beta oxidation of palmitoyl-CoA to myristoyl-CoA |
| Reactome:R-RNO-77348 | Beta oxidation of octanoyl-CoA to hexanoyl-CoA |
| Reactome:R-RNO-390247 | Beta-oxidation of very long chain fatty acids |
| Reactome:R-RNO-1483257 | Phospholipid metabolism |
| Reactome:R-SSC-8978868 | Fatty acid metabolism |
| Reactome:R-SSC-77286 | mitochondrial fatty acid beta-oxidation of saturated fatty acids |
| Reactome:R-SSC-77346 | Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA |
| WikiPathways:WP5123 | Mitochondrial fatty acid oxidation disorders |
| WikiPathways:WP5355 | Metabolic Epileptic Disorders |
| WikiPathways:WP4686 | Leucine, isoleucine and valine metabolism |
| WikiPathways:WP2318 | Fatty acid oxidation |
| PathBank:SMP0120662 | 3-Methylcrotonyl-CoA Carboxylase Deficiency Type I |
| PathBank:SMP0120734 | Malonic Aciduria |
| PathBank:SMP0120746 | Saccharopinuria/Hyperlysinemia II |
| PathBank:SMP0120786 | Malonyl-CoA Decarboxylase Deficiency |
| PathBank:SMP0120806 | 3-Hydroxyisobutyric Aciduria |
| PathBank:SMP0120822 | Carnitine Palmitoyl Transferase Deficiency I |
| PathBank:SMP0120826 | Medium Chain Acyl-CoA Dehydrogenase Deficiency (MCAD) |
| PathBank:SMP0120854 | Pyridoxine Dependency with Seizures |
| PathBank:SMP0120870 | 2-Aminoadipic 2-Oxoadipic Aciduria |
| PathBank:SMP0120440 | 3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency |
| PathBank:SMP0120444 | 3-Methylglutaconic Aciduria Type IV |
| PathBank:SMP0120476 | Ethylmalonic Encephalopathy |
| PathBank:SMP0120484 | Glutaric Aciduria Type I |
| PathBank:SMP0120516 | Maple Syrup Urine Disease |
| PathBank:SMP0120520 | Short-Chain Acyl-CoA Dehydrogenase Deficiency (SCAD Deficiency) |
| PathBank:SMP0120528 | Methylmalonic Aciduria Due to Cobalamin-Related Disorders |
| PathBank:SMP0120589 | Isovaleric Acidemia |
| PathBank:SMP0120593 | Hyperlysinemia II or Saccharopinuria |
| PathBank:SMP0120605 | Very-Long-Chain Acyl-CoA Dehydrogenase Deficiency (VLCAD) |
| PathBank:SMP0120609 | Trifunctional Protein Deficiency |
| PathBank:SMP0121348 | Fatty Acid Oxidation (Hexanoate) |
| PathBank:SMP0121352 | Fatty Acid Oxidation (Palmitate) |
| PathBank:SMP0122220 | Oleic Acid Oxidation |
| PathBank:SMP0000032 | Valine, Leucine, and Isoleucine Degradation |
| PathBank:SMP0000051 | Fatty Acid Metabolism |
| PathBank:SMP0000016 | Propanoate Metabolism |
| PathBank:SMP0000173 | beta-Ketothiolase Deficiency |
| PathBank:SMP0000199 | Maple Syrup Urine Disease |
| PathBank:SMP0000384 | Methylmalonate Semialdehyde Dehydrogenase Deficiency |
| PathBank:SMP0000235 | Short-Chain Acyl-CoA Dehydrogenase Deficiency (SCAD Deficiency) |
| PathBank:SMP0000239 | Saccharopinuria/Hyperlysinemia II |
| PathBank:SMP0000482 | Mitochondrial Beta-Oxidation of Long Chain Saturated Fatty Acids |
| PathBank:SMP0000141 | 3-Methylglutaconic Aciduria Type IV |
| PathBank:SMP0000524 | Isovaleric Acidemia |
| PathBank:SMP0000528 | Hyperlysinemia II or Saccharopinuria |
| PathBank:SMP0000540 | Very-Long-Chain Acyl-CoA Dehydrogenase Deficiency (VLCAD) |
| PathBank:SMP0000544 | Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase Deficiency (LCHAD) |
| PathBank:SMP0000568 | Short-Chain 3-Hydroxyacyl-CoA Dehydrogenase Deficiency (SCHAD) |
| PathBank:SMP0002433 | Leucine Degradation |
| PathBank:SMP0087294 | Fatty Acid Elongation in Mitochondria |
| PathBank:SMP0087358 | Mitochondrial Beta-Oxidation of Short Chain Saturated Fatty Acids |
| PathBank:SMP0087430 | Fatty Acid Metabolism |
| PathBank:SMP0063612 | Fatty Acid Elongation In Mitochondria |
| PathBank:SMP0063656 | Propanoate Metabolism |
| PathBank:SMP0120661 | 3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency |
| PathBank:SMP0120665 | 3-Methylglutaconic Aciduria Type IV |
| PathBank:SMP0120745 | Methylmalonic Aciduria |
| PathBank:SMP0120757 | Propionic Acidemia |
| PathBank:SMP0120805 | 3-Hydroxyisobutyric Acid Dehydrogenase Deficiency |
| PathBank:SMP0120825 | Carnitine Palmitoyl Transferase Deficiency II |
| PathBank:SMP0120439 | 2-Methyl-3-hydroxybutryl-CoA Dehydrogenase Deficiency |
| PathBank:SMP0120443 | 3-Methylglutaconic Aciduria Type III |
| PathBank:SMP0120459 | beta-Ketothiolase Deficiency |
| PathBank:SMP0120503 | Isovaleric Aciduria |
| PathBank:SMP0120523 | Methylmalonate Semialdehyde Dehydrogenase Deficiency |
| PathBank:SMP0120588 | Isobutyryl-CoA Dehydrogenase Deficiency |
| PathBank:SMP0120592 | Hyperlysinemia I, Familial |
| PathBank:SMP0120604 | Long Chain Acyl-CoA Dehydrogenase Deficiency (LCAD) |
| PathBank:SMP0120608 | Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase Deficiency (LCHAD) |
| PathBank:SMP0120632 | Short-Chain 3-Hydroxyacyl-CoA Dehydrogenase Deficiency (SCHAD) |
| PathBank:SMP0121206 | Jasmonic Acid Biosynthesis |
| PathBank:SMP0121347 | Fatty Acid Oxidation (Decanoate) |
| PathBank:SMP0121351 | Fatty Acid Oxidation (Octanoate) |
| PathBank:SMP0000073 | Butyrate Metabolism |
| PathBank:SMP0000054 | Fatty Acid Elongation in Mitochondria |
| PathBank:SMP0000138 | 3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency |
| PathBank:SMP0000140 | 3-Methylglutaconic Aciduria Type III |
| PathBank:SMP0000238 | Isovaleric Aciduria |
| PathBank:SMP0000185 | Glutaric Aciduria Type I |
| PathBank:SMP0000186 | Glutaric Aciduria Type I |
| PathBank:SMP0000481 | Mitochondrial Beta-Oxidation of Medium Chain Saturated Fatty Acids |
| PathBank:SMP0000201 | Methylmalonic Aciduria Due to Cobalamin-Related Disorders |
| PathBank:SMP0000523 | Isobutyryl-CoA Dehydrogenase Deficiency |
| PathBank:SMP0000527 | Hyperlysinemia I, Familial |
| PathBank:SMP0000539 | Long Chain Acyl-CoA Dehydrogenase Deficiency (LCAD) |
| PathBank:SMP0000571 | Pyridoxine Dependency with Seizures |
| PathBank:SMP0087341 | Propanoate Metabolism |
| PathBank:SMP0087521 | Mitochondrial Beta-Oxidation of Medium Chain Saturated Fatty Acids |
| PathBank:SMP0063603 | Butyrate Metabolism |
| PathBank:SMP0063641 | Mitochondrial Beta-Oxidation of Short Chain Saturated Fatty Acids |
| PathBank:SMP0063689 | Valine, Leucine, and Isoleucine Degradation |
| PathBank:SMP0120660 | 2-Methyl-3-hydroxybutryl-CoA Dehydrogenase Deficiency |
| PathBank:SMP0120664 | 3-Methylglutaconic Aciduria Type III |
| PathBank:SMP0120696 | Ethylmalonic Encephalopathy |
| PathBank:SMP0120704 | Glutaric Aciduria Type I |
| PathBank:SMP0120736 | Maple Syrup Urine Disease |
| PathBank:SMP0120740 | Short-Chain Acyl-CoA Dehydrogenase Deficiency (SCAD Deficiency) |
| PathBank:SMP0120748 | Methylmalonic Aciduria Due to Cobalamin-Related Disorders |
| PathBank:SMP0120808 | Isovaleric Acidemia |
| PathBank:SMP0120812 | Hyperlysinemia II or Saccharopinuria |
| PathBank:SMP0120824 | Very-Long-Chain Acyl-CoA Dehydrogenase Deficiency (VLCAD) |
| PathBank:SMP0120828 | Trifunctional Protein Deficiency |
| PathBank:SMP0120441 | 3-Methylcrotonyl-CoA Carboxylase Deficiency Type I |
| PathBank:SMP0120525 | Methylmalonic Aciduria |
| PathBank:SMP0120537 | Propionic Acidemia |
| PathBank:SMP0120586 | 3-Hydroxyisobutyric Acid Dehydrogenase Deficiency |
| PathBank:SMP0120606 | Carnitine Palmitoyl Transferase Deficiency II |
| PathBank:SMP0121261 | Fatty Acid Oxidation |
| PathBank:SMP0121349 | Fatty Acid Oxidation (Laurate) |
| PathBank:SMP0121353 | Fatty Acid Oxidation (Steareate) |
| PathBank:SMP0000137 | 2-Methyl-3-hydroxybutyryl-CoA Dehydrogenase Deficiency |
| PathBank:SMP0000237 | 3-Methylcrotonyl-CoA Carboxylase Deficiency Type I |
| PathBank:SMP0000200 | Methylmalonic Aciduria |
| PathBank:SMP0000521 | 3-Hydroxyisobutyric Acid Dehydrogenase Deficiency |
| PathBank:SMP0000541 | Carnitine Palmitoyl Transferase Deficiency II |
| PathBank:SMP0000545 | Trifunctional Protein Deficiency |
| PathBank:SMP0000719 | 2-Aminoadipic 2-Oxoadipic Aciduria |
| PathBank:SMP0002434 | Lysine Metabolism |
| PathBank:SMP0087280 | Fatty Acid Metabolism |
| PathBank:SMP0087300 | Lysine Degradation |
| PathBank:SMP0087360 | Mitochondrial Beta-Oxidation of Long Chain Saturated Fatty Acids |
| PathBank:SMP0087480 | Propanoate Metabolism |
| PathBank:SMP0012062 | Fatty Acid Beta-Oxidation I |
| PathBank:SMP0063640 | Mitochondrial Beta-Oxidation of Medium Chain Saturated Fatty Acids |
| PathBank:SMP0120651 | 2-Aminoadipic 2-Oxoadipic Aciduria |
| PathBank:SMP0120663 | 3-Methylglutaconic Aciduria Type I |
| PathBank:SMP0120679 | beta-Ketothiolase Deficiency |
| PathBank:SMP0120723 | Isovaleric Aciduria |
| PathBank:SMP0120743 | Methylmalonate Semialdehyde Dehydrogenase Deficiency |
| PathBank:SMP0120807 | Isobutyryl-CoA Dehydrogenase Deficiency |
| PathBank:SMP0120811 | Hyperlysinemia I, Familial |
| PathBank:SMP0120823 | Long Chain Acyl-CoA Dehydrogenase Deficiency (LCAD) |
| PathBank:SMP0120827 | Long-Chain-3-Hydroxyacyl-CoA Dehydrogenase Deficiency (LCHAD) |
| PathBank:SMP0120851 | Short-Chain 3-Hydroxyacyl-CoA Dehydrogenase Deficiency (SCHAD) |
| PathBank:SMP0120442 | 3-Methylglutaconic Aciduria Type I |
| PathBank:SMP0120514 | Malonic Aciduria |
| PathBank:SMP0120526 | Saccharopinuria/Hyperlysinemia II |
| PathBank:SMP0120567 | Malonyl-CoA Decarboxylase Deficiency |
| PathBank:SMP0120587 | 3-Hydroxyisobutyric Aciduria |
| PathBank:SMP0120603 | Carnitine Palmitoyl Transferase Deficiency I |
| PathBank:SMP0120607 | Medium Chain Acyl-CoA Dehydrogenase Deficiency (MCAD) |
| PathBank:SMP0120635 | Pyridoxine Dependency with Seizures |
| PathBank:SMP0121350 | Fatty Acid Oxidation (Myristate) |
| PathBank:SMP0122226 | L-Carnitine Degradation I |
| PathBank:SMP0000037 | Lysine Degradation |
| PathBank:SMP0000236 | Propionic Acidemia |
| PathBank:SMP0000139 | 3-Methylglutaconic Aciduria Type I |
| PathBank:SMP0000181 | Ethylmalonic Encephalopathy |
| PathBank:SMP0000480 | Mitochondrial Beta-Oxidation of Short Chain Saturated Fatty Acids |
| PathBank:SMP0000198 | Malonic Aciduria |
| PathBank:SMP0000502 | Malonyl-CoA Decarboxylase Deficiency |
| PathBank:SMP0000522 | 3-Hydroxyisobutyric Aciduria |
| PathBank:SMP0000538 | Carnitine Palmitoyl Transferase Deficiency I |
| PathBank:SMP0000542 | Medium Chain Acyl-CoA Dehydrogenase Deficiency (MCAD) |
| PathBank:SMP0000635 | Valproic Acid Metabolism Pathway |
| PathBank:SMP0087287 | Butyrate Metabolism |
| PathBank:SMP0087327 | Valine, Leucine, and Isoleucine Degradation |
| PathBank:SMP0087359 | Mitochondrial Beta-Oxidation of Medium Chain Saturated Fatty Acids |
| PathBank:SMP0087519 | Mitochondrial Beta-Oxidation of Short Chain Saturated Fatty Acids |
| PathBank:SMP0087523 | Mitochondrial Beta-Oxidation of Long Chain Saturated Fatty Acids |
| PathBank:SMP0063589 | Fatty Acid Metabolism |
| PathBank:SMP0063635 | Lysine Degradation |
| PathBank:SMP0063639 | Mitochondrial Beta-Oxidation of Long Chain Saturated Fatty Acids |