| BioCyc:HUMAN_MALATE-ASPARTATE-SHUTTLE-PWY |
malate-aspartate shuttle |
| BioCyc:HUMAN_ASPARAGINE-DEG1-PWY-1 |
asparagine degradation |
| BioCyc:HUMAN_PWY-5328 |
superpathway of methionine degradation |
| BioCyc:META_ASPARAGINE-DEG1-PWY-1 |
L-asparagine degradation III (mammalian) |
| BioCyc:META_ASPARTATE-DEG1-PWY |
L-aspartate degradation I |
| BioCyc:META_CYSTEINE-DEG-PWY |
L-cysteine degradation I |
| BioCyc:META_PWY-5328 |
superpathway of L-methionine salvage and degradation |
| BioCyc:MOUSE_HYDROXYPRODEG-PWY |
4-hydroxyproline degradation I |
| BioCyc:MOUSE_CYSTEINE-DEG-PWY |
L-cysteine degradation I |
| BioCyc:MOUSE_PWY-5328 |
superpathway of methionine degradation |
| BioCyc:HUMAN_PWY-5329 |
L-cysteine degradation II |
| BioCyc:META_ASPARTATESYN-PWY |
L-aspartate biosynthesis |
| BioCyc:META_MALATE-ASPARTATE-SHUTTLE-PWY |
L-aspartate degradation II |
| BioCyc:META_PWY-5329 |
L-cysteine degradation III |
| BioCyc:HUMAN_ASPARTATESYN-PWY |
aspartate biosynthesis |
| BioCyc:HUMAN_CYSTEINE-DEG-PWY |
L-cysteine degradation I |
| Reactome:R-BTA-8963693 |
Aspartate and asparagine metabolism |
| Reactome:R-SSC-8963693 |
Aspartate and asparagine metabolism |
| Reactome:R-GGA-8963693 |
Aspartate and asparagine metabolism |
| Reactome:R-RNO-8963693 |
Aspartate and asparagine metabolism |
| Reactome:R-MMU-8963693 |
Aspartate and asparagine metabolism |
| Reactome:R-HSA-8963693 |
Aspartate and asparagine metabolism |
| Reactome:R-SSC-9856872 |
Malate-aspartate shuttle |
| Reactome:R-HSA-9856872 |
Malate-aspartate shuttle |
| Reactome:R-GGA-9856872 |
Malate-aspartate shuttle |
| Reactome:R-MMU-9856872 |
Malate-aspartate shuttle |
| Reactome:R-RNO-9856872 |
Malate-aspartate shuttle |
| Reactome:R-BTA-9856872 |
Malate-aspartate shuttle |
| Reactome:R-BTA-1430728 |
Metabolism |
| Reactome:R-BTA-1428517 |
Aerobic respiration and respiratory electron transport |
| Reactome:R-BTA-71291 |
Amino acid and derivative metabolism |
| Reactome:R-GGA-1660598 |
Metabolism |
| Reactome:R-GGA-352875 |
Gluconeogenesis |
| Reactome:R-HSA-611105 |
Respiratory electron transport |
| Reactome:R-MMU-1430728 |
Metabolism |
| Reactome:R-MMU-611105 |
Respiratory electron transport |
| Reactome:R-RNO-611105 |
Respiratory electron transport |
| Reactome:R-BTA-611105 |
Respiratory electron transport |
| Reactome:R-GGA-1428517 |
Aerobic respiration and respiratory electron transport |
| Reactome:R-GGA-71291 |
Amino acid and derivative metabolism |
| Reactome:R-HSA-1237112 |
Methionine salvage pathway |
| Reactome:R-SSC-1430728 |
Metabolism |
| Reactome:R-GGA-1430728 |
Metabolism |
| Reactome:R-GGA-353098 |
Carbohydrate metabolism |
| Reactome:R-GGA-372568 |
Amino acid metabolism |
| Reactome:R-HSA-1428517 |
Aerobic respiration and respiratory electron transport |
| Reactome:R-HSA-71291 |
Amino acid and derivative metabolism |
| Reactome:R-MMU-1428517 |
Aerobic respiration and respiratory electron transport |
| Reactome:R-MMU-71291 |
Amino acid and derivative metabolism |
| Reactome:R-RNO-1430728 |
Metabolism |
| Reactome:R-RNO-1428517 |
Aerobic respiration and respiratory electron transport |
| Reactome:R-RNO-71291 |
Amino acid and derivative metabolism |
| Reactome:R-SSC-611105 |
Respiratory electron transport |
| Reactome:R-SSC-71291 |
Amino acid and derivative metabolism |
| Reactome:R-GGA-611105 |
Respiratory electron transport |
| Reactome:R-HSA-1430728 |
Metabolism |
| Reactome:R-HSA-1614635 |
Sulfur amino acid metabolism |
| Reactome:R-SSC-1428517 |
Aerobic respiration and respiratory electron transport |
| WikiPathways:WP4595 |
Urea cycle and associated pathways |
| WikiPathways:WP4583 |
Biomarkers for urea cycle disorders |
| WikiPathways:WP5220 |
Metabolic reprogramming in pancreatic cancer |
| WikiPathways:WP4504 |
Cysteine and methionine catabolism |
| PathBank:SMP0120654 |
Cystinosis, Ocular Nonnephropathic |
| PathBank:SMP0120666 |
4-Hydroxybutyric Aciduria/Succinic Semialdehyde Dehydrogenase Deficiency |
| PathBank:SMP0120682 |
Carbamoyl Phosphate Synthetase Deficiency |
| PathBank:SMP0120686 |
Citrullinemia Type I |
| PathBank:SMP0120714 |
Homocarnosinosis |
| PathBank:SMP0120762 |
Ornithine Transcarbamylase Deficiency (OTC Deficiency) |
| PathBank:SMP0120850 |
Succinic Semialdehyde Dehydrogenase Deficiency |
| PathBank:SMP0120540 |
Phenylketonuria |
| PathBank:SMP0120569 |
Creatine Deficiency, Guanidinoacetate Methyltransferase Deficiency |
| PathBank:SMP0000020 |
Arginine and Proline Metabolism |
| PathBank:SMP0000362 |
Arginine: Glycine Amidinotransferase Deficiency (AGAT Deficiency) |
| PathBank:SMP0000188 |
Guanidinoacetate Methyltransferase Deficiency (GAMT Deficiency) |
| PathBank:SMP0000369 |
Tyrosinemia Type 2 (or Richner-Hanhart Syndrome) |
| PathBank:SMP0000190 |
Hawkinsinuria |
| PathBank:SMP0000504 |
Creatine Deficiency, Guanidinoacetate Methyltransferase Deficiency |
| PathBank:SMP0000722 |
Cystinosis, Ocular Nonnephropathic |
| PathBank:SMP0087278 |
Glutamate Metabolism |
| PathBank:SMP0063596 |
Arginine and Proline Metabolism |
| PathBank:SMP0120677 |
Argininosuccinic Aciduria |
| PathBank:SMP0120491 |
Hawkinsinuria |
| PathBank:SMP0120499 |
Hyperprolinemia Type I |
| PathBank:SMP0120511 |
Tyrosinemia Type 3 (TYRO3) |
| PathBank:SMP0120539 |
Prolinemia Type II |
| PathBank:SMP0120564 |
beta-Mercaptolactate-Cysteine Disulfiduria |
| PathBank:SMP0120572 |
L-Arginine:Glycine Amidinotransferase Deficiency |
| PathBank:SMP0000207 |
Prolidase Deficiency (PD) |
| PathBank:SMP0000208 |
Prolinemia Type II |
| PathBank:SMP0000206 |
Phenylketonuria |
| PathBank:SMP0000169 |
Alkaptonuria |
| PathBank:SMP0000429 |
Disulfiram Action Pathway |
| PathBank:SMP0000499 |
beta-Mercaptolactate-Cysteine Disulfiduria |
| PathBank:SMP0000507 |
L-Arginine:Glycine Amidinotransferase Deficiency |
| PathBank:SMP0087301 |
Malate-Aspartate Shuttle |
| PathBank:SMP0063607 |
Cysteine Metabolism |
| PathBank:SMP0063684 |
Tyrosine Metabolism |
| PathBank:SMP0120676 |
Argininemia |
| PathBank:SMP0120716 |
Hyperinsulinism-Hyperammonemia Syndrome |
| PathBank:SMP0108773 |
Glutaminolysis and Cancer |
| PathBank:SMP0120453 |
Alkaptonuria |
| PathBank:SMP0120501 |
Hyperprolinemia Type II |
| PathBank:SMP0120509 |
Tyrosinemia Type I |
| PathBank:SMP0120513 |
Tyrosinemia Type 2 (or Richner-Hanhart Syndrome) |
| PathBank:SMP0120541 |
Prolidase Deficiency (PD) |
| PathBank:SMP0120570 |
Hyperornithinemia with Gyrate Atrophy (HOGA) |
| PathBank:SMP0120598 |
Monoamine Oxidase-A Deficiency (MAO-A) |
| PathBank:SMP0000013 |
Cysteine Metabolism |
| PathBank:SMP0000360 |
Hyperprolinemia Type II |
| PathBank:SMP0000363 |
Ornithine Aminotransferase Deficiency (OAT Deficiency) |
| PathBank:SMP0000370 |
Tyrosinemia Type 3 (TYRO3) |
| PathBank:SMP0000218 |
Tyrosinemia Type I |
| PathBank:SMP0000505 |
Hyperornithinemia with Gyrate Atrophy (HOGA) |
| PathBank:SMP0000533 |
Monoamine Oxidase-A Deficiency (MAO-A) |
| PathBank:SMP0120659 |
2-Hydroxyglutric Aciduria (D and L Form) |
| PathBank:SMP0120454 |
Arginine: Glycine Amidinotransferase Deficiency (AGAT Deficiency) |
| PathBank:SMP0120490 |
Guanidinoacetate Methyltransferase Deficiency (GAMT Deficiency) |
| PathBank:SMP0120538 |
Ornithine Aminotransferase Deficiency (OAT Deficiency) |
| PathBank:SMP0120559 |
Tyrosinemia, Transient, of the Newborn |
| PathBank:SMP0120563 |
Dopamine beta-Hydroxylase Deficiency |
| PathBank:SMP0120571 |
Hyperornithinemia-Hyperammonemia-Homocitrullinuria [HHH-syndrome] |
| PathBank:SMP0000006 |
Tyrosine Metabolism |
| PathBank:SMP0000008 |
Phenylalanine and Tyrosine Metabolism |
| PathBank:SMP0000361 |
Hyperprolinemia Type I |
| PathBank:SMP0000494 |
Tyrosinemia, Transient, of the Newborn |
| PathBank:SMP0000498 |
Dopamine beta-Hydroxylase Deficiency |
| PathBank:SMP0000506 |
Hyperornithinemia-Hyperammonemia-Homocitrullinuria [HHH-syndrome] |
| PathBank:SMP0087319 |
Urea Cycle |
| PathBank:SMP0063649 |
Phenylalanine and Tyrosine Metabolism |