EC: 4.3.2.1

argininosuccinate lyase (2-(Nomega-L-arginino)succinate arginine-lyase (fumarate-forming))

enzyme lambda metabolic reaction experiment
uniprot:P24058 [argininosuccinate lyase(Enzyme) wildtype]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (Vmax * S) ) / (Km + S)) buffer: 60 mM Tris-HCl
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) mutant S29A]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (Vmax * S) ) / (Km + S)) buffer: 60 mM Tris-HCl
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) mutant T161S]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (Vmax * S) ) / (Km + S)) buffer: 60 mM Tris-HCl
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) mutant N116D]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (Vmax * S) ) / (Km + S)) buffer: 60 mM Tris-HCl
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) mutant D33N]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (Vmax * S) ) / (Km + S)) buffer: 60 mM Tris-HCl
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) mutant T281V]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (Vmax * S) ) / (Km + S)) buffer: 60 mM Tris-HCl
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) mutant D293N]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (Vmax * S) ) / (Km + S)) buffer: 60 mM Tris-HCl
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) mutant K325N]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (Vmax * S) ) / (Km + S)) buffer: 60 mM Tris-HCl
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) wildtype delta-Crystallin IIa]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 50 mM Tris-Cl
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) wildtype delta-Crystallin IIb]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 50 mM Tris-Cl
PH: 7.5
Temperature: 25
uniprot:P24057 [argininosuccinate lyase(Enzyme) wildtype delta-Crystallin Ia]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 50 mM Tris-Cl
PH: 7.5
Temperature: 25
- [argininosuccinate lyase(Enzyme) wildtype delta-Crystallin IIIa]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 50 mM Tris-Cl
PH: 7.5
Temperature: 25
- [argininosuccinate lyase(Enzyme) wildtype delta-Crystallin IVa]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 50 mM Tris-Cl
PH: 7.5
Temperature: 25
uniprot:P22675 [argininosuccinate lyase(Enzyme) wildtype]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 1 M potassium phosphate
PH: 7.5
Temperature: 37
uniprot:P24057 [argininosuccinate lyase(Enzyme) wildtype]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (Vmax * A) ) / (Km + A)) buffer: 0.1 M potassium phosphate
PH: 7.5
Temperature: 36
uniprot:P04424 [argininosuccinate lyase(Enzyme) wildtype]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (V * S) ) / (Km + S)) buffer: 0.1 M Tris/HCl, 420 U/ml Arginase
PH: 7.5
Temperature: 37
uniprot:P20673 [argininosuccinate lyase(Enzyme) wildtype]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (V * S) ) / (Km + S)) buffer: 0.1 M Tris/HCl, 420 U/ml Arginase
PH: 7.5
Temperature: 37
uniprot:P04424 [argininosuccinate lyase(Enzyme) wildtype]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (V * S) ) / (Km + S)) buffer: 0.1 M Tris/HCl, 420 U/ml Arginase
PH: 7.5
Temperature: 37
- [argininosuccinate lyase(Enzyme) wildtype delta-Crystallin IIIb]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 50 mM Tris-Cl
PH: 7.5
Temperature: 25
- [argininosuccinate lyase(Enzyme) wildtype delta-Crystallin VIIb]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 50 mM Tris-Cl
PH: 7.5
Temperature: 25
- [argininosuccinate lyase(Enzyme) wildtype delta-Crystallin Vb]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 50 mM Tris-Cl
PH: 7.5
Temperature: 25
- [argininosuccinate lyase(Enzyme) wildtype delta-Crystallin IVb]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 50 mM Tris-Cl
PH: 7.5
Temperature: 25
- [argininosuccinate lyase(Enzyme) wildtype delta-Crystallin VIb]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (( (E * kcat) ) * A) ) / (Km + A)) buffer: 50 mM Tris-Cl
PH: 7.5
Temperature: 25
uniprot:P04424 [argininosuccinate lyase(Enzyme) wildtype]

L_Arginine + Fumarate -> N(omega)_(L_Arginino)succinate
(( (Vmax * A) ) / (Km + A)) buffer: 0.1 M potassium phosphate
PH: 6.8
Temperature: 37
uniprot:P04424 [argininosuccinate lyase(Enzyme) wildtype]

Fumarate + L_Arginine -> N(omega)_(L_Arginino)succinate
(( (Vmax * A) ) / (Km + A)) buffer: 0.1 M potassium phosphate
PH: 6.8
Temperature: 37
uniprot:P04424 [argininosuccinate lyase(Enzyme) wildtype]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (Vmax * A) ) / (Km + A)) buffer: 0.1 M potassium phosphate
PH: 7.5
Temperature: 37
uniprot:P24058 [argininosuccinate lyase(Enzyme) wildtype]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (Vmax * A) ) / (Km + A)) buffer: 50 mM Tris-HCl
PH: 7.5
Temperature: 22
uniprot:P24058 [argininosuccinate lyase(Enzyme) mutant H91N]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (Vmax * A) ) / (Km + A)) buffer: 50 mM Tris-HCl
PH: 7.5
Temperature: 22
uniprot:P24058 [Citrulline]

L_Arginine + Fumarate -> N(omega)_(L_Arginino)succinate
(( (Vmax * Q) ) / (( (Km_Q * (1 + (I / Kis))) ) + (Q * (1 + (I / Kii))))) buffer: 50 mM Tris/HCl
PH: 7.5
Temperature: 25
uniprot:P24058 [Citrulline]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (Vmax * A) ) / (( (Km_A * (1 + (I / Kis))) ) + (A * (1 + (I / Kii))))) buffer: 50 mM Tris/HCl
PH: 7.5
Temperature: 25
uniprot:P24058 [Citrulline]

L_Arginine + Fumarate -> N(omega)_(L_Arginino)succinate
(( (Vmax * P) ) / (( (Km_P * (1 + (I / Kis))) ) + P)) buffer: 50 mM Tris/HCl
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) wildtype]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (Vmax * A) ) / (( (Km_A * (1 + (I / Kis))) ) + (A * (1 + (I / Kii))))) buffer: 50 mM Tris/HCl
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) wildtype]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (Vmax * A) ) / (( (Km_A * (1 + (I / Kis))) ) + (A * (1 + (I / Kii))))) buffer: 50 mM Tris/HCl
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) wildtype]

L_Arginine + Fumarate -> N(omega)_(L_Arginino)succinate
(( (( (Vmax * P) ) * Q) ) / (( (( (( (Kip * Kiq_EP) ) + (Kip_EQ * Q)) ) + (Kiq_EP * P)) ) + (P * Q))) buffer: 50 mM Tris/HCl
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) wildtype]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (Vmax * A) ) / (Km_A + A)) buffer: 50 mM Tris/HCl
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) wildtype]

Fumarate + L_Arginine -> N(omega)_(L_Arginino)succinate
(( (Vmax * P) ) / (Km_P + P)) buffer: 50 mM Tris/HCl
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) wildtype]

L_Arginine + Fumarate -> N(omega)_(L_Arginino)succinate
(( (Vmax * Q) ) / (Km_Q + Q)) buffer: 50 mM Tris/HCl
PH: 7.5
Temperature: 25
- [argininosuccinate lyase(Enzyme) wildtype delta-B crystallin]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (Vmax * A) ) / (Km + A)) buffer: 20 mM phosphate
PH: 7
Temperature: 40
uniprot:P24058 [argininosuccinate lyase(Enzyme) wildtype delta-E crystallin]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (Vmax * A) ) / (Km + A)) buffer: 20 mM phosphate
PH: 7
Temperature: 40
- [argininosuccinate lyase(Enzyme) wildtype delta-D crystallin]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (Vmax * A) ) / (Km + A)) buffer: 20 mM phosphate
PH: 7
Temperature: 40
- [argininosuccinate lyase(Enzyme) wildtype delta-C crystallin]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (Vmax * A) ) / (Km + A)) buffer: 20 mM phosphate
PH: 7
Temperature: 40
uniprot:P24058 [H+]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (( (( (E * kcat0) ) / (( (1 + (( (10 ^ (0 - pH)) ) / (10 ^ (0 - pK1_a)))) ) + (( (10 ^ (0 - pK2_a)) ) / (10 ^ (0 - pH))))) ) * S) ) / (( (( (kcat0 / (( (1 + (( (10 ^ (0 - pH)) ) / (10 ^ (0 - pK1_a)))) ) + (( (10 ^ (0 - pK2_a)) ) / (10 ^ (0 - pH))))) ) / (kcat_Km0 / (( (1 + (( (10 ^ (0 - pH)) ) / (10 ^ (0 - pK1_b)))) ) + (( (10 ^ (0 - pK2_b)) ) / (10 ^ (0 - pH)))))) ) + S)) buffer: KH2PO4 / K2HPO4
PH: 5.5
Temperature: 25
uniprot:P24058 [H+]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (( (( (E * kcat0) ) / (( (1 + (( (10 ^ (0 - pH)) ) / (10 ^ (0 - pK1_a)))) ) + (( (10 ^ (0 - pK2_a)) ) / (10 ^ (0 - pH))))) ) * S) ) / (( (( (kcat0 / (( (1 + (( (10 ^ (0 - pH)) ) / (10 ^ (0 - pK1_a)))) ) + (( (10 ^ (0 - pK2_a)) ) / (10 ^ (0 - pH))))) ) / (kcat_Km0 / (( (1 + (( (10 ^ (0 - pH)) ) / (10 ^ (0 - pK1_b)))) ) + (( (10 ^ (0 - pK2_b)) ) / (10 ^ (0 - pH)))))) ) + S)) buffer: KH2PO4 / K2HPO4
PH: 5.5
Temperature: 25
uniprot:P22675 [argininosuccinate lyase(Enzyme) wildtype]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (Vmax * A) ) / (Km + A)) buffer: 0.1 M sodium phosphate
PH: 7.5
Temperature: 37
uniprot:P22675 [argininosuccinate lyase(Enzyme) mutant arg-7-1]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (Vmax * A) ) / (Km + A)) buffer: 0.1 M sodium phosphate
PH: 7.5
Temperature: 37
uniprot:P22675 [argininosuccinate lyase(Enzyme) mutant arg-7-6]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (Vmax * A) ) / (Km + A)) buffer: 0.1 M sodium phosphate
PH: 7.5
Temperature: 37
uniprot:P22675 [argininosuccinate lyase(Enzyme) mutant arg-7-5]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (Vmax * A) ) / (Km + A)) buffer: 0.1 M sodium phosphate
PH: 7.5
Temperature: 37
uniprot:P22675 [argininosuccinate lyase(Enzyme) mutant arg-7-7]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (Vmax * A) ) / (Km + A)) buffer: 0.1 M sodium phosphate
PH: 7.5
Temperature: 37
- [argininosuccinate lyase(Enzyme) wildtype 211-chimera (delta-2 crystallin domain 1 and delta-1 crystallin domain 2+3)]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (Vmax * A) ) / (Km + A)) buffer: 10 mM Tris-HCl, 1 mM EDTA
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) wildtype delta-2 crystallin]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (Vmax * A) ) / (Km + A)) buffer: 10 mM Tris-HCl, 1 mM EDTA
PH: 7.5
Temperature: 25
uniprot:P24057 [argininosuccinate lyase(Enzyme) mutant delta-1 crystallin-double loop[22-31,74-89]-M9W/V14S]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (Vmax * A) ) / (Km + A)) buffer: 10 mM Tris-HCl, 1 mM EDTA
PH: 7.5
Temperature: 25
uniprot:P24057 [argininosuccinate lyase(Enzyme) mutant delta-1 crystallin-double loop[22-31,74-89]-M9W]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (Vmax * A) ) / (Km + A)) buffer: 10 mM Tris-HCl, 1 mM EDTA
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) mutant delta-2 crystallin-D115A]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (Vmax * A) ) / (Km + A)) buffer: 10 mM Tris-HCl, 1 mM EDTA
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) mutant delta-2 crystallin-W9Y]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (Vmax * A) ) / (Km + A)) buffer: 10 mM Tris-HCl, 1 mM EDTA
PH: 7.5
Temperature: 25
uniprot:P24057 [argininosuccinate lyase(Enzyme) mutant delta-1 crystallin-double loop[22-31,74-89]-M9W/E115D]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (Vmax * A) ) / (Km + A)) buffer: 10 mM Tris-HCl, 1 mM EDTA
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) mutant delta-2 crystallin-W9M]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (Vmax * A) ) / (Km + A)) buffer: 10 mM Tris-HCl, 1 mM EDTA
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) mutant delta-2 crystallin-W9R]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (Vmax * A) ) / (Km + A)) buffer: 10 mM Tris-HCl, 1 mM EDTA
PH: 7.5
Temperature: 25
uniprot:P24057 [argininosuccinate lyase(Enzyme) mutant delta-1 crystallin-double loop[22-31,74-89]-M9Y/E115D]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (Vmax * A) ) / (Km + A)) buffer: 10 mM Tris-HCl, 1 mM EDTA
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) mutant delta-2 crystallin-W9A]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (Vmax * A) ) / (Km + A)) buffer: 10 mM Tris-HCl, 1 mM EDTA
PH: 7.5
Temperature: 25
uniprot:P24057 [argininosuccinate lyase(Enzyme) mutant delta-1 crystallin-double loop[22-31,74-89]-M9F/E115D]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (Vmax * A) ) / (Km + A)) buffer: 10 mM Tris-HCl, 1 mM EDTA
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) mutant delta-2 crystallin-W9F]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (Vmax * A) ) / (Km + A)) buffer: 10 mM Tris-HCl, 1 mM EDTA
PH: 7.5
Temperature: 25
- [argininosuccinate lyase(Enzyme) wildtype 221-chimera (delta-2 crystallin domain 1+2 and delta-1 crystallin domain 3)]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (Vmax * A) ) / (Km + A)) buffer: 60 mM Tris-HCl
PH: 7.5
Temperature: 25
- [argininosuccinate lyase(Enzyme) wildtype 211-chimera (delta-2 crystallin domain 1 and delta-1 crystallin domain 2+3)]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (Vmax * A) ) / (Km + A)) buffer: 60 mM Tris-HCl
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) wildtype delta-2 crystallin]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (Vmax * A) ) / (Km + A)) buffer: 60 mM Tris-HCl
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) mutant delta-2 crystallin-truncated[1-9]]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (Vmax * A) ) / (Km + A)) buffer: 10 mM Tris-HCl, 1 mM EDTA
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) mutant delta-2 crystallin-D115E]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (Vmax * A) ) / (Km + A)) buffer: 10 mM Tris-HCl, 1 mM EDTA
PH: 7.5
Temperature: 25
uniprot:P24058 [argininosuccinate lyase(Enzyme) mutant delta-2 crystallin-truncated[1-8]]

N(omega)_(L_Arginino)succinate -> L_Arginine + Fumarate
(( (Vmax * A) ) / (Km + A)) buffer: 10 mM Tris-HCl, 1 mM EDTA
PH: 7.5
Temperature: 25
uniprot:P04424 [argininosuccinate lyase(Enzyme) wildtype]

N(omega)_(L_Arginino)succinate -> Fumarate + L_Arginine
(( (Vmax * S) ) / (Km + S)) buffer: 100 mM Potassium Phosphate
PH: 6.8
Temperature: 37
uniprot:P04424 [argininosuccinate lyase(Enzyme) wildtype]

L_Arginine + Fumarate -> N(omega)_(L_Arginino)succinate
(( (Vmax * S) ) / (Km + S)) buffer: 100 mM Potassium Phosphate
PH: 6.8
Temperature: 37
uniprot:P04424 [argininosuccinate lyase(Enzyme) wildtype]

L_Arginine + Fumarate -> N(omega)_(L_Arginino)succinate
(( (Vmax * S) ) / (Km + S)) buffer: 100 mM Potassium Phosphate
PH: 6.8
Temperature: 37

Pathways

pathway id name
BioCyc:HUMAN_PWY-4984 urea cycle
BioCyc:META_PWY-5004 superpathway of L-citrulline metabolism
BioCyc:ARA_PWY-4983 L-citrulline-nitric oxide cycle
BioCyc:VCHO_PWY-4984 urea cycle
BioCyc:VCHO_ARGSYN-PWY L-arginine biosynthesis I (via L-ornithine)
BioCyc:MTBCDC1551_PWY-7400 L-arginine biosynthesis IV (archaebacteria)
BioCyc:ANTHRA_ARGSYN-PWY L-arginine biosynthesis I (via L-ornithine)
BioCyc:ANTHRA_PWY-4984 urea cycle
BioCyc:MOUSE_PWY-4984 urea cycle
BioCyc:ECOL316407_ARG+POLYAMINE-SYN superpathway of arginine and polyamine biosynthesis
BioCyc:PDIF272563_ARGSYNBSUB-PWY L-arginine biosynthesis II (acetyl cycle)
BioCyc:HUMAN_PWY-4983 citrulline-nitric oxide cycle
BioCyc:META_PWY-4984 urea cycle
BioCyc:ECO_ARG+POLYAMINE-SYN superpathway of arginine and polyamine biosynthesis
BioCyc:ECO_ARGSYN-PWY L-arginine biosynthesis I (via L-ornithine)
BioCyc:ARA_PWY-4984 urea cycle
BioCyc:MTBH37RV_ARGSYNBSUB-PWY L-arginine biosynthesis II (acetyl cycle)
BioCyc:MTBCDC1551_ARGSYN-PWY L-arginine biosynthesis I (via L-ornithine)
BioCyc:ECOO157_PWY-7400 arginine biosynthesis IV (archaebacteria)
BioCyc:ECOL199310_PWY-7400 arginine biosynthesis IV (archaebacteria)
BioCyc:ECOL199310_ARGSYN-PWY arginine biosynthesis I (via L-ornithine)
BioCyc:ANTHRA_ARGSYNBSUB-PWY L-arginine biosynthesis II (acetyl cycle)
BioCyc:AGRO_ARGSYN-PWY L-arginine biosynthesis I (via L-ornithine)
BioCyc:MOUSE_PWY-5004 superpathway of citrulline metabolism
BioCyc:PDIF272563_ARGSYN-PWY L-arginine biosynthesis I (via L-ornithine)
BioCyc:CORYNE_ARGSYNBSUB-PWY L-arginine biosynthesis II (acetyl cycle)
BioCyc:META_ARGSYN-PWY L-arginine biosynthesis I (via L-ornithine)
BioCyc:META_PWY-4983 nitric oxide biosynthesis II (mammals)
BioCyc:YEAST_PWY-4984 urea cycle
BioCyc:ARA_ARGSYN-PWY L-arginine biosynthesis I (via L-ornithine)
BioCyc:ECOL199310_ARGSYNBSUB-PWY arginine biosynthesis II (acetyl cycle)
BioCyc:MOUSE_ARGININE-SYN4-PWY arginine biosynthesis IV
BioCyc:ECOL316407_ARGSYN-PWY arginine biosynthesis I (via L-ornithine)
BioCyc:BTHE_ARGSYN-PWY arginine biosynthesis I (via L-ornithine)
BioCyc:BTHE_PWY-4984 urea cycle
BioCyc:BTHE_PWY-7400 arginine biosynthesis IV (archaebacteria)
BioCyc:CORYNE_ARGSYN-PWY L-arginine biosynthesis I (via L-ornithine)
BioCyc:META_ARG+POLYAMINE-SYN superpathway of arginine and polyamine biosynthesis
BioCyc:YEAST_ARGSYNBSUB-PWY arginine biosynthesis
BioCyc:ARA_ARGSYNBSUB-PWY L-arginine biosynthesis II (acetyl cycle)
BioCyc:VCHO_ARGSYNBSUB-PWY L-arginine biosynthesis II (acetyl cycle)
BioCyc:MTBH37RV_ARGSYN-PWY L-arginine biosynthesis I (via L-ornithine)
BioCyc:MTBCDC1551_ARGSYNBSUB-PWY L-arginine biosynthesis II (acetyl cycle)
BioCyc:ECOO157_ARGSYN-PWY arginine biosynthesis I (via L-ornithine)
BioCyc:AGRO_PWY-4984 urea cycle
BioCyc:MOUSE_PWY-4983 citrulline-nitric oxide cycle
BioCyc:BSUB_ARGSYNBSUB-PWY L-arginine biosynthesis II (acetyl cycle)
BioCyc:SYNEL_PWY-4984 urea cycle
BioCyc:SYNEL_ARGSYNBSUB-PWY L-arginine biosynthesis II (acetyl cycle)
BioCyc:GCF_000013425_ARGSYNBSUB-PWY L-arginine biosynthesis II (acetyl cycle)
PathBank:SMP0000809 Aspartate Metabolism
PathBank:SMP0000812 Arginine Metabolism
PlantCyc:ARA_ARGSYN-PWY L-arginine biosynthesis I (via L-ornithine)
PlantCyc:ARA_PWY-4983 nitric oxide biosynthesis II (mammals)
PlantCyc:ARA_PWY-4984 urea cycle
PlantCyc:ARA_ARGSYNBSUB-PWY L-arginine biosynthesis II (acetyl cycle)
PlantCyc:ARA_PWY-5004 superpathway of L-citrulline metabolism
Reactome:R-BTA-1430728 Metabolism
Reactome:R-BTA-71291 Amino acid and derivative metabolism
Reactome:R-MMU-1430728 Metabolism
Reactome:R-SCE-71291 Amino acid and derivative metabolism
Reactome:R-SPO-1430728 Metabolism
Reactome:R-SCE-1430728 Metabolism
Reactome:R-SPO-71291 Amino acid and derivative metabolism
Reactome:R-SPO-70635 Urea cycle
Reactome:R-BTA-70635 Urea cycle
Reactome:R-HSA-71291 Amino acid and derivative metabolism
Reactome:R-MMU-71291 Amino acid and derivative metabolism
Reactome:R-RNO-1430728 Metabolism
Reactome:R-RNO-71291 Amino acid and derivative metabolism
Reactome:R-HSA-1430728 Metabolism
Reactome:R-HSA-70635 Urea cycle
Reactome:R-MMU-70635 Urea cycle
Reactome:R-RNO-70635 Urea cycle
Reactome:R-SCE-70635 Urea cycle
WikiPathways:WP4595 Urea cycle and associated pathways
WikiPathways:WP497 Urea cycle and metabolism of amino groups
WikiPathways:WP4583 Biomarkers for urea cycle disorders
PathBank:SMP0120456 Argininosuccinic Aciduria
PathBank:SMP0120569 Creatine Deficiency, Guanidinoacetate Methyltransferase Deficiency
PathBank:SMP0000059 Urea Cycle
PathBank:SMP0000020 Arginine and Proline Metabolism
PathBank:SMP0000362 Arginine: Glycine Amidinotransferase Deficiency (AGAT Deficiency)
PathBank:SMP0000188 Guanidinoacetate Methyltransferase Deficiency (GAMT Deficiency)
PathBank:SMP0000001 Citrullinemia Type I
PathBank:SMP0000504 Creatine Deficiency, Guanidinoacetate Methyltransferase Deficiency
PathBank:SMP0002420 Proline Metabolism
PathBank:SMP0087165 Aspartate Metabolism
PathBank:SMP0063596 Arginine and Proline Metabolism
PathBank:SMP0120455 Argininemia
PathBank:SMP0120499 Hyperprolinemia Type I
PathBank:SMP0120539 Prolinemia Type II
PathBank:SMP0120572 L-Arginine:Glycine Amidinotransferase Deficiency
PathBank:SMP0121271 Aspartate Metabolism
PathBank:SMP0000207 Prolidase Deficiency (PD)
PathBank:SMP0000208 Prolinemia Type II
PathBank:SMP0000003 Argininosuccinic Aciduria
PathBank:SMP0000507 L-Arginine:Glycine Amidinotransferase Deficiency
PathBank:SMP0002416 Arginine Metabolism
PathBank:SMP0087224 Urea Cycle
PathBank:SMP0120461 Canavan Disease
PathBank:SMP0120501 Hyperprolinemia Type II
PathBank:SMP0120541 Prolidase Deficiency (PD)
PathBank:SMP0120570 Hyperornithinemia with Gyrate Atrophy (HOGA)
PathBank:SMP0000067 Aspartate Metabolism
PathBank:SMP0000360 Hyperprolinemia Type II
PathBank:SMP0000363 Ornithine Aminotransferase Deficiency (OAT Deficiency)
PathBank:SMP0000175 Canavan Disease
PathBank:SMP0000205 Ornithine Transcarbamylase Deficiency (OTC Deficiency)
PathBank:SMP0000505 Hyperornithinemia with Gyrate Atrophy (HOGA)
PathBank:SMP0012004 Arginine and Proline Metabolism
PathBank:SMP0120454 Arginine: Glycine Amidinotransferase Deficiency (AGAT Deficiency)
PathBank:SMP0120462 Carbamoyl Phosphate Synthetase Deficiency
PathBank:SMP0120466 Citrullinemia Type I
PathBank:SMP0120490 Guanidinoacetate Methyltransferase Deficiency (GAMT Deficiency)
PathBank:SMP0120502 Hypoacetylaspartia
PathBank:SMP0120538 Ornithine Aminotransferase Deficiency (OAT Deficiency)
PathBank:SMP0120542 Ornithine Transcarbamylase Deficiency (OTC Deficiency)
PathBank:SMP0120571 Hyperornithinemia-Hyperammonemia-Homocitrullinuria [HHH-syndrome]
PathBank:SMP0121274 Arginine Metabolism
PathBank:SMP0000361 Hyperprolinemia Type I
PathBank:SMP0000192 Hypoacetylaspartia
PathBank:SMP0000357 Argininemia
PathBank:SMP0000002 Carbamoyl Phosphate Synthetase Deficiency
PathBank:SMP0000506 Hyperornithinemia-Hyperammonemia-Homocitrullinuria [HHH-syndrome]
PathBank:SMP0087178 Arginine and Proline Metabolism
PathBank:SMP0063597 Aspartate Metabolism
PathBank:SMP0063686 Urea Cycle