EC: 2.1.4.1

glycine amidinotransferase (L-arginine:glycine amidinotransferase)

enzyme lambda metabolic reaction experiment
uniprot:Q6ITZ7 [glycine amidinotransferase(Enzyme) wildtype]

L_Arginine + Glycine -> L_Ornithine + Guanidinoacetate		 (( (Vmax * A) ) / (Km + A)) buffer: 0.1 M sodium phosphate
PH: 7.5
Temperature: 37

Pathways

pathway id name
BioCyc:META_GLYCGREAT-PWY creatine biosynthesis
BioCyc:MOUSE_PWY3DJ-35588 creatine biosynthesis
BioCyc:MOUSE_GLYCGREAT-PWY glycine degradation (creatine biosynthesis)
BioCyc:HUMAN_GLYCGREAT-PWY creatine biosynthesis
Reactome:R-BTA-1430728 Metabolism
Reactome:R-BTA-71291 Amino acid and derivative metabolism
Reactome:R-DRE-71291 Amino acid and derivative metabolism
Reactome:R-HSA-71288 Creatine metabolism
Reactome:R-MMU-1430728 Metabolism
Reactome:R-MMU-71288 Creatine metabolism
Reactome:R-RNO-71288 Creatine metabolism
Reactome:R-SSC-71288 Creatine metabolism
Reactome:R-BTA-71288 Creatine metabolism
Reactome:R-DRE-71288 Creatine metabolism
Reactome:R-SSC-1430728 Metabolism
Reactome:R-XTR-71291 Amino acid and derivative metabolism
Reactome:R-DRE-1430728 Metabolism
Reactome:R-HSA-71291 Amino acid and derivative metabolism
Reactome:R-MMU-71291 Amino acid and derivative metabolism
Reactome:R-RNO-1430728 Metabolism
Reactome:R-RNO-71291 Amino acid and derivative metabolism
Reactome:R-SSC-71291 Amino acid and derivative metabolism
Reactome:R-XTR-1430728 Metabolism
Reactome:R-HSA-1430728 Metabolism
Reactome:R-XTR-71288 Creatine metabolism
WikiPathways:WP497 Urea cycle and metabolism of amino groups
WikiPathways:WP4583 Biomarkers for urea cycle disorders
WikiPathways:WP5355 Metabolic Epileptic Disorders
PathBank:SMP0120569 Creatine Deficiency, Guanidinoacetate Methyltransferase Deficiency
PathBank:SMP0000020 Arginine and Proline Metabolism
PathBank:SMP0000362 Arginine: Glycine Amidinotransferase Deficiency (AGAT Deficiency)
PathBank:SMP0000188 Guanidinoacetate Methyltransferase Deficiency (GAMT Deficiency)
PathBank:SMP0000242 Dimethylglycine Dehydrogenase Deficiency
PathBank:SMP0000223 Non-Ketotic Hyperglycinemia
PathBank:SMP0000484 Dimethylglycine Dehydrogenase Deficiency
PathBank:SMP0000504 Creatine Deficiency, Guanidinoacetate Methyltransferase Deficiency
PathBank:SMP0063596 Arginine and Proline Metabolism
PathBank:SMP0120653 3-Phosphoglycerate Dehydrogenase Deficiency
PathBank:SMP0120475 Dimethylglycine Dehydrogenase Deficiency
PathBank:SMP0120499 Hyperprolinemia Type I
PathBank:SMP0120539 Prolinemia Type II
PathBank:SMP0120572 L-Arginine:Glycine Amidinotransferase Deficiency
PathBank:SMP0000004 Glycine and Serine Metabolism
PathBank:SMP0000207 Prolidase Deficiency (PD)
PathBank:SMP0000208 Prolinemia Type II
PathBank:SMP0000507 L-Arginine:Glycine Amidinotransferase Deficiency
PathBank:SMP0000721 3-Phosphoglycerate Dehydrogenase Deficiency
PathBank:SMP0087245 Glycine and Serine Metabolism
PathBank:SMP0120501 Hyperprolinemia Type II
PathBank:SMP0120521 Sarcosinemia
PathBank:SMP0120541 Prolidase Deficiency (PD)
PathBank:SMP0120570 Hyperornithinemia with Gyrate Atrophy (HOGA)
PathBank:SMP0000360 Hyperprolinemia Type II
PathBank:SMP0000363 Ornithine Aminotransferase Deficiency (OAT Deficiency)
PathBank:SMP0000179 Dihydropyrimidine Dehydrogenase Deficiency (DHPD)
PathBank:SMP0000485 Hyperglycinemia, Non-Ketotic
PathBank:SMP0000505 Hyperornithinemia with Gyrate Atrophy (HOGA)
PathBank:SMP0120454 Arginine: Glycine Amidinotransferase Deficiency (AGAT Deficiency)
PathBank:SMP0120474 Dihydropyrimidine Dehydrogenase Deficiency (DHPD)
PathBank:SMP0120490 Guanidinoacetate Methyltransferase Deficiency (GAMT Deficiency)
PathBank:SMP0120534 Non-Ketotic Hyperglycinemia
PathBank:SMP0120538 Ornithine Aminotransferase Deficiency (OAT Deficiency)
PathBank:SMP0120550 Hyperglycinemia, Non-Ketotic
PathBank:SMP0120571 Hyperornithinemia-Hyperammonemia-Homocitrullinuria [HHH-syndrome]
PathBank:SMP0000361 Hyperprolinemia Type I
PathBank:SMP0000244 Sarcosinemia
PathBank:SMP0000506 Hyperornithinemia-Hyperammonemia-Homocitrullinuria [HHH-syndrome]
PathBank:SMP0087178 Arginine and Proline Metabolism
PathBank:SMP0063626 Glycine and Serine Metabolism