Phenylalanine and Tyrosine Metabolism

Metabolites

2-Oxoglutarate

Formula: C5H6O5 (146.0215226)

CAS ID: 328-50-7

3-(4-Hydroxyphenyl)pyruvate

Formula: C9H8O4 (180.0422568)

CAS ID: 156-39-8

4-Fumarylacetoacetate

Formula: C8H8O6 (200.0320868)

CAS ID: 28613-33-4

4-Maleylacetoacetate

Formula: C8H8O6 (200.0320868)

CAS ID: 5698-52-2

Acetoacetate

Formula: C4H6O3 (102.0316926)

CAS ID: 541-50-4

Ammonia

Formula: NH3 (17.0265478)

CAS ID: 7664-41-7

AMP

Formula: C10H14N5O7P (347.06308240000004)

CAS ID: 61-19-8

ATP

Formula: C10H16N5O13P3 (506.9957476)

CAS ID: 56-65-5

CO2

Formula: CO2 (43.98983)

CAS ID: 124-38-9

H2O

Formula: H2O (18.0105642)

CAS ID: 7732-18-5

Homogentisate

Formula: C8H8O4 (168.0422568)

CAS ID: 451-13-8

Hydrogen peroxide

Formula: H2O2 (34.0054792)

CAS ID: 7722-84-1

L-Glutamate

Formula: C5H9NO4 (147.0531554)

CAS ID: 56-86-0

L-Phenylalanine

Formula: C9H11NO2 (165.0789746)

CAS ID: 63-91-2

L-Tyrosine

Formula: C9H11NO3 (181.0738896)

CAS ID: 60-18-4

Oxygen

Formula: O2 (31.98983)

CAS ID: 7782-44-7

Phenylpyruvate

Formula: C9H8O3 (164.0473418)

CAS ID: 156-06-9

Tetrahydrobiopterin

Formula: C9H15N5O3 (241.11748400000002)

CAS ID: 17528-72-2

diphosphate

Formula: O7P2 (173.911931)

CAS ID: 14000-31-8



Enzyme

EC Number name full name note
1.13.11.27 4-hydroxyphenylpyruvate dioxygenase 4-hydroxyphenylpyruvate:oxygen oxidoreductase (hydroxylating, decarboxylating)
2.6.1.5 tyrosine transaminase L-tyrosine:2-oxoglutarate aminotransferase


Proteins

Protein ID name full name