EC: 3.1.3.52
[3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)]-phosphatase ([3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)]-phosphate phosphohydrolase)
| enzyme | lambda | metabolic reaction | experiment |
|---|
Pathways
| pathway id | name |
|---|---|
| Reactome:R-HSA-9865118 | Diseases of branched-chain amino acid catabolism |
| Reactome:R-HSA-9865114 | Maple Syrup Urine Disease |
| Reactome:R-HSA-9912529 | H139Hfs13* PPM1K causes a mild variant of MSUD |
| Reactome:R-BTA-1430728 | Metabolism |
| Reactome:R-BTA-71291 | Amino acid and derivative metabolism |
| Reactome:R-HSA-70895 | Branched-chain amino acid catabolism |
| Reactome:R-HSA-1643685 | Disease |
| Reactome:R-MMU-1430728 | Metabolism |
| Reactome:R-MMU-70895 | Branched-chain amino acid catabolism |
| Reactome:R-BTA-70895 | Branched-chain amino acid catabolism |
| Reactome:R-HSA-71291 | Amino acid and derivative metabolism |
| Reactome:R-HSA-5668914 | Diseases of metabolism |
| Reactome:R-MMU-71291 | Amino acid and derivative metabolism |
| Reactome:R-HSA-1430728 | Metabolism |